The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses
Mucopolysaccharidoses (MPSs) are a group of rare, genetic lysosomal storage disorders. They are caused by deficiencies of the lysosomal enzymes involved in the degradation of glycosaminoglycans (GAGs). Pain is a common feature in mucopolysaccharidoses. However, the pathophysiology of pain in this gr...
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| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Wiley
2017-01-01
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| Series: | Case Reports in Pediatrics |
| Online Access: | http://dx.doi.org/10.1155/2017/7257230 |
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| _version_ | 1832562079613059072 |
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| author | Sabrina Congedi Chiara Di Pede Maurizio Scarpa Angelica Rampazzo Franca Benini |
| author_facet | Sabrina Congedi Chiara Di Pede Maurizio Scarpa Angelica Rampazzo Franca Benini |
| author_sort | Sabrina Congedi |
| collection | DOAJ |
| description | Mucopolysaccharidoses (MPSs) are a group of rare, genetic lysosomal storage disorders. They are caused by deficiencies of the lysosomal enzymes involved in the degradation of glycosaminoglycans (GAGs). Pain is a common feature in mucopolysaccharidoses. However, the pathophysiology of pain in this group of diseases is still unclear and genesis of pain is multifactorial. Currently, poor data about pain management in these patients are available. Here, we present our clinical experience in complex pain management in three children with MPS. |
| format | Article |
| id | doaj-art-d2918d58c0454c5ab27d370c3e3694c3 |
| institution | Kabale University |
| issn | 2090-6803 2090-6811 |
| language | English |
| publishDate | 2017-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pediatrics |
| spelling | doaj-art-d2918d58c0454c5ab27d370c3e3694c32025-02-03T01:23:28ZengWileyCase Reports in Pediatrics2090-68032090-68112017-01-01201710.1155/2017/72572307257230The Complexity of Pain Management in Children Affected by MucopolysaccharidosesSabrina Congedi0Chiara Di Pede1Maurizio Scarpa2Angelica Rampazzo3Franca Benini4Pediatric Pain and Palliative Care Service, Department of Women’s and Children’s Health, University of Padova, Via Giustiniani 3, 35128 Padova, ItalyPediatric Pain and Palliative Care Service, Department of Women’s and Children’s Health, University of Padova, Via Giustiniani 3, 35128 Padova, ItalyPediatric Pain and Palliative Care Service, Department of Women’s and Children’s Health, University of Padova, Via Giustiniani 3, 35128 Padova, ItalyPediatric Pain and Palliative Care Service, Department of Women’s and Children’s Health, University of Padova, Via Giustiniani 3, 35128 Padova, ItalyPediatric Pain and Palliative Care Service, Department of Women’s and Children’s Health, University of Padova, Via Giustiniani 3, 35128 Padova, ItalyMucopolysaccharidoses (MPSs) are a group of rare, genetic lysosomal storage disorders. They are caused by deficiencies of the lysosomal enzymes involved in the degradation of glycosaminoglycans (GAGs). Pain is a common feature in mucopolysaccharidoses. However, the pathophysiology of pain in this group of diseases is still unclear and genesis of pain is multifactorial. Currently, poor data about pain management in these patients are available. Here, we present our clinical experience in complex pain management in three children with MPS.http://dx.doi.org/10.1155/2017/7257230 |
| spellingShingle | Sabrina Congedi Chiara Di Pede Maurizio Scarpa Angelica Rampazzo Franca Benini The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses Case Reports in Pediatrics |
| title | The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses |
| title_full | The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses |
| title_fullStr | The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses |
| title_full_unstemmed | The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses |
| title_short | The Complexity of Pain Management in Children Affected by Mucopolysaccharidoses |
| title_sort | complexity of pain management in children affected by mucopolysaccharidoses |
| url | http://dx.doi.org/10.1155/2017/7257230 |
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