Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
Despite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder i...
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Format: | Article |
Language: | English |
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Wiley
2011-01-01
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Series: | Critical Care Research and Practice |
Online Access: | http://dx.doi.org/10.1155/2011/283690 |
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author | Mayra Gonçalves Menegueti Alkmim-Teixeira Gil Cezar Karin Aparecida Casarini Kátia Simone Muniz Cordeiro Anibal Basile-Filho Olindo Assis Martins-Filho Maria Auxiliadora-Martins |
author_facet | Mayra Gonçalves Menegueti Alkmim-Teixeira Gil Cezar Karin Aparecida Casarini Kátia Simone Muniz Cordeiro Anibal Basile-Filho Olindo Assis Martins-Filho Maria Auxiliadora-Martins |
author_sort | Mayra Gonçalves Menegueti |
collection | DOAJ |
description | Despite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder in the intensive care unit are presented. We believe that acute intermittent porphyria should be borne in mind during performance of differential diagnosis of neurological, psychiatric, and gastroenterological disorders on patients whose routine investigation tests are normal, especially when precipitating factors exist. Intensive care measures and a multidisciplinary team approach are essential. |
format | Article |
id | doaj-art-d163c1b0460540388c91fa1b6f889351 |
institution | Kabale University |
issn | 2090-1305 2090-1313 |
language | English |
publishDate | 2011-01-01 |
publisher | Wiley |
record_format | Article |
series | Critical Care Research and Practice |
spelling | doaj-art-d163c1b0460540388c91fa1b6f8893512025-02-03T00:59:16ZengWileyCritical Care Research and Practice2090-13052090-13132011-01-01201110.1155/2011/283690283690Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary ApproachMayra Gonçalves Menegueti0Alkmim-Teixeira Gil Cezar1Karin Aparecida Casarini2Kátia Simone Muniz Cordeiro3Anibal Basile-Filho4Olindo Assis Martins-Filho5Maria Auxiliadora-Martins6Divisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilLaboratório de Biomarcadores de Diagnóstico e Monitoração, Instituto René Rachou, Fundação Oswaldo Cruz, Belo Horizonte, MG, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDespite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder in the intensive care unit are presented. We believe that acute intermittent porphyria should be borne in mind during performance of differential diagnosis of neurological, psychiatric, and gastroenterological disorders on patients whose routine investigation tests are normal, especially when precipitating factors exist. Intensive care measures and a multidisciplinary team approach are essential.http://dx.doi.org/10.1155/2011/283690 |
spellingShingle | Mayra Gonçalves Menegueti Alkmim-Teixeira Gil Cezar Karin Aparecida Casarini Kátia Simone Muniz Cordeiro Anibal Basile-Filho Olindo Assis Martins-Filho Maria Auxiliadora-Martins Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach Critical Care Research and Practice |
title | Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach |
title_full | Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach |
title_fullStr | Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach |
title_full_unstemmed | Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach |
title_short | Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach |
title_sort | acute intermittent porphyria associated with respiratory failure a multidisciplinary approach |
url | http://dx.doi.org/10.1155/2011/283690 |
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