Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach

Despite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder i...

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Main Authors: Mayra Gonçalves Menegueti, Alkmim-Teixeira Gil Cezar, Karin Aparecida Casarini, Kátia Simone Muniz Cordeiro, Anibal Basile-Filho, Olindo Assis Martins-Filho, Maria Auxiliadora-Martins
Format: Article
Language:English
Published: Wiley 2011-01-01
Series:Critical Care Research and Practice
Online Access:http://dx.doi.org/10.1155/2011/283690
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author Mayra Gonçalves Menegueti
Alkmim-Teixeira Gil Cezar
Karin Aparecida Casarini
Kátia Simone Muniz Cordeiro
Anibal Basile-Filho
Olindo Assis Martins-Filho
Maria Auxiliadora-Martins
author_facet Mayra Gonçalves Menegueti
Alkmim-Teixeira Gil Cezar
Karin Aparecida Casarini
Kátia Simone Muniz Cordeiro
Anibal Basile-Filho
Olindo Assis Martins-Filho
Maria Auxiliadora-Martins
author_sort Mayra Gonçalves Menegueti
collection DOAJ
description Despite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder in the intensive care unit are presented. We believe that acute intermittent porphyria should be borne in mind during performance of differential diagnosis of neurological, psychiatric, and gastroenterological disorders on patients whose routine investigation tests are normal, especially when precipitating factors exist. Intensive care measures and a multidisciplinary team approach are essential.
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institution Kabale University
issn 2090-1305
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language English
publishDate 2011-01-01
publisher Wiley
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series Critical Care Research and Practice
spelling doaj-art-d163c1b0460540388c91fa1b6f8893512025-02-03T00:59:16ZengWileyCritical Care Research and Practice2090-13052090-13132011-01-01201110.1155/2011/283690283690Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary ApproachMayra Gonçalves Menegueti0Alkmim-Teixeira Gil Cezar1Karin Aparecida Casarini2Kátia Simone Muniz Cordeiro3Anibal Basile-Filho4Olindo Assis Martins-Filho5Maria Auxiliadora-Martins6Divisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilLaboratório de Biomarcadores de Diagnóstico e Monitoração, Instituto René Rachou, Fundação Oswaldo Cruz, Belo Horizonte, MG, BrazilDivisão de Terapia Intensiva, Departamento de Cirurgia e Anatomia, Hospital das Clínicas, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, 14049-900 Ribeirão Preto, SP, BrazilDespite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder in the intensive care unit are presented. We believe that acute intermittent porphyria should be borne in mind during performance of differential diagnosis of neurological, psychiatric, and gastroenterological disorders on patients whose routine investigation tests are normal, especially when precipitating factors exist. Intensive care measures and a multidisciplinary team approach are essential.http://dx.doi.org/10.1155/2011/283690
spellingShingle Mayra Gonçalves Menegueti
Alkmim-Teixeira Gil Cezar
Karin Aparecida Casarini
Kátia Simone Muniz Cordeiro
Anibal Basile-Filho
Olindo Assis Martins-Filho
Maria Auxiliadora-Martins
Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
Critical Care Research and Practice
title Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_full Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_fullStr Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_full_unstemmed Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_short Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_sort acute intermittent porphyria associated with respiratory failure a multidisciplinary approach
url http://dx.doi.org/10.1155/2011/283690
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