Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II Trial

Objective. Until recently, advanced medullary thyroid cancer (MTC) had few treatment options except surgery. The mTOR inhibitor everolimus has shown encouraging results in neuroendocrine tumors. As part of a prospective phase II study, we analyzed the safety and efficacy of everolimus in advanced MT...

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Main Authors: T. C. Schneider, D. de Wit, T. P. Links, N. P. van Erp, J. J. M. van der Hoeven, H. Gelderblom, T. van Wezel, R. van Eijk, H. Morreau, H. J. Guchelaar, E. Kapiteijn
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:International Journal of Endocrinology
Online Access:http://dx.doi.org/10.1155/2015/348124
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author T. C. Schneider
D. de Wit
T. P. Links
N. P. van Erp
J. J. M. van der Hoeven
H. Gelderblom
T. van Wezel
R. van Eijk
H. Morreau
H. J. Guchelaar
E. Kapiteijn
author_facet T. C. Schneider
D. de Wit
T. P. Links
N. P. van Erp
J. J. M. van der Hoeven
H. Gelderblom
T. van Wezel
R. van Eijk
H. Morreau
H. J. Guchelaar
E. Kapiteijn
author_sort T. C. Schneider
collection DOAJ
description Objective. Until recently, advanced medullary thyroid cancer (MTC) had few treatment options except surgery. The mTOR inhibitor everolimus has shown encouraging results in neuroendocrine tumors. As part of a prospective phase II study, we analyzed the safety and efficacy of everolimus in advanced MTC. Methods. Seven patients with per RECIST 1.1 documented advanced MTC were included and received everolimus 10 mg daily. The primary objective was determining treatment efficacy. Secondary endpoints included progression-free survival (PFS), overall survival (OS), toxicity, and pharmacokinetics (PK). Results. Median follow-up duration was 28 weeks (17–147). Five patients (71%) showed SD, of which 4 (57%) showed SD >24 weeks. Median PFS and OS were 33 (95%CI: 8–56) and 30 (95%CI: 15–45) weeks, respectively. Toxicity was predominantly grade 1/2 and included mucositis (43%), fatigue (43%), and hypertriglyceridemia (43%). Four MTCs harbored the somatic RET mutation c.2753T>C, p.Met918Thr. The best clinical response was seen in a MEN2A patient. PK characteristics were consistent with phase I data. One patient exhibited extensive toxicity accompanying elevated everolimus plasma concentrations. Conclusions. This study suggests that everolimus exerts clinically relevant antitumor activity in patients with advanced MTC. Given the high level of clinical benefit and the relatively low toxicity profile, further investigation of everolimus in these patients is warranted.
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spelling doaj-art-cfa67ea0c7d54ce4ae61aa60db8aa78c2025-08-20T03:19:46ZengWileyInternational Journal of Endocrinology1687-83371687-83452015-01-01201510.1155/2015/348124348124Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II TrialT. C. Schneider0D. de Wit1T. P. Links2N. P. van Erp3J. J. M. van der Hoeven4H. Gelderblom5T. van Wezel6R. van Eijk7H. Morreau8H. J. Guchelaar9E. Kapiteijn10Department of Medical Oncology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Clinical Pharmacy and Toxicology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Endocrinology, University Medical Center Groningen, 9700 RB Groningen, NetherlandsDepartment of Clinical Pharmacy, Radboud University Nijmegen Medical Center, 6525 GA Nijmegen, NetherlandsDepartment of Medical Oncology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Medical Oncology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Pathology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Pathology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Pathology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Clinical Pharmacy and Toxicology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsDepartment of Medical Oncology, Leiden University Medical Center, 2333 ZA Leiden, NetherlandsObjective. Until recently, advanced medullary thyroid cancer (MTC) had few treatment options except surgery. The mTOR inhibitor everolimus has shown encouraging results in neuroendocrine tumors. As part of a prospective phase II study, we analyzed the safety and efficacy of everolimus in advanced MTC. Methods. Seven patients with per RECIST 1.1 documented advanced MTC were included and received everolimus 10 mg daily. The primary objective was determining treatment efficacy. Secondary endpoints included progression-free survival (PFS), overall survival (OS), toxicity, and pharmacokinetics (PK). Results. Median follow-up duration was 28 weeks (17–147). Five patients (71%) showed SD, of which 4 (57%) showed SD >24 weeks. Median PFS and OS were 33 (95%CI: 8–56) and 30 (95%CI: 15–45) weeks, respectively. Toxicity was predominantly grade 1/2 and included mucositis (43%), fatigue (43%), and hypertriglyceridemia (43%). Four MTCs harbored the somatic RET mutation c.2753T>C, p.Met918Thr. The best clinical response was seen in a MEN2A patient. PK characteristics were consistent with phase I data. One patient exhibited extensive toxicity accompanying elevated everolimus plasma concentrations. Conclusions. This study suggests that everolimus exerts clinically relevant antitumor activity in patients with advanced MTC. Given the high level of clinical benefit and the relatively low toxicity profile, further investigation of everolimus in these patients is warranted.http://dx.doi.org/10.1155/2015/348124
spellingShingle T. C. Schneider
D. de Wit
T. P. Links
N. P. van Erp
J. J. M. van der Hoeven
H. Gelderblom
T. van Wezel
R. van Eijk
H. Morreau
H. J. Guchelaar
E. Kapiteijn
Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II Trial
International Journal of Endocrinology
title Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II Trial
title_full Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II Trial
title_fullStr Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II Trial
title_full_unstemmed Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II Trial
title_short Beneficial Effects of the mTOR Inhibitor Everolimus in Patients with Advanced Medullary Thyroid Carcinoma: Subgroup Results of a Phase II Trial
title_sort beneficial effects of the mtor inhibitor everolimus in patients with advanced medullary thyroid carcinoma subgroup results of a phase ii trial
url http://dx.doi.org/10.1155/2015/348124
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