Multiclinic Observations on the Simplified Diet in PKU
Phenylketonuria is an inborn error of metabolism that historically has been treated with a strict phenylalanine-restricted diet where all foods are weighed and measured. This is cumbersome and difficult for patients and caregivers, especially patients with high phenylalanine blood concentrations who...
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| Format: | Article |
| Language: | English |
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Wiley
2017-01-01
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| Series: | Journal of Nutrition and Metabolism |
| Online Access: | http://dx.doi.org/10.1155/2017/4083293 |
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| _version_ | 1832556220396863488 |
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| author | Laurie Bernstein Casey Burns Melissa Sailer-Hammons Angela Kurtz Frances Rohr |
| author_facet | Laurie Bernstein Casey Burns Melissa Sailer-Hammons Angela Kurtz Frances Rohr |
| author_sort | Laurie Bernstein |
| collection | DOAJ |
| description | Phenylketonuria is an inborn error of metabolism that historically has been treated with a strict phenylalanine-restricted diet where all foods are weighed and measured. This is cumbersome and difficult for patients and caregivers, especially patients with high phenylalanine blood concentrations who often have neurocognitive deficits. The Simplified Diet is an alternative approach that allows for increased flexibility, promotes healthy food choices, and is easier to manage than a traditional diet for PKU. This paper describes the implementation of the Simplified Diet and outlines education, counseling strategies, and challenges encountered by three metabolic clinics in the United States. |
| format | Article |
| id | doaj-art-cca24b59a69049de88e4dd81ddae3106 |
| institution | Kabale University |
| issn | 2090-0724 2090-0732 |
| language | English |
| publishDate | 2017-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Journal of Nutrition and Metabolism |
| spelling | doaj-art-cca24b59a69049de88e4dd81ddae31062025-02-03T05:46:02ZengWileyJournal of Nutrition and Metabolism2090-07242090-07322017-01-01201710.1155/2017/40832934083293Multiclinic Observations on the Simplified Diet in PKULaurie Bernstein0Casey Burns1Melissa Sailer-Hammons2Angela Kurtz3Frances Rohr4Inherited Metabolic Diseases Clinic, Children’s Hospital Colorado, Aurora, CO, USAInherited Metabolic Diseases Clinic, Children’s Hospital Colorado, Aurora, CO, USAInherited Metabolic Diseases Clinic, Children’s Hospital Colorado, Aurora, CO, USAMetabolic Nutrition Program, Division of Medical Genetics, Icahn School of Medicine at Mount Sinai, New York, NY, USADepartment of Nutrition, Boston Children’s Hospital, Boston, MA, USAPhenylketonuria is an inborn error of metabolism that historically has been treated with a strict phenylalanine-restricted diet where all foods are weighed and measured. This is cumbersome and difficult for patients and caregivers, especially patients with high phenylalanine blood concentrations who often have neurocognitive deficits. The Simplified Diet is an alternative approach that allows for increased flexibility, promotes healthy food choices, and is easier to manage than a traditional diet for PKU. This paper describes the implementation of the Simplified Diet and outlines education, counseling strategies, and challenges encountered by three metabolic clinics in the United States.http://dx.doi.org/10.1155/2017/4083293 |
| spellingShingle | Laurie Bernstein Casey Burns Melissa Sailer-Hammons Angela Kurtz Frances Rohr Multiclinic Observations on the Simplified Diet in PKU Journal of Nutrition and Metabolism |
| title | Multiclinic Observations on the Simplified Diet in PKU |
| title_full | Multiclinic Observations on the Simplified Diet in PKU |
| title_fullStr | Multiclinic Observations on the Simplified Diet in PKU |
| title_full_unstemmed | Multiclinic Observations on the Simplified Diet in PKU |
| title_short | Multiclinic Observations on the Simplified Diet in PKU |
| title_sort | multiclinic observations on the simplified diet in pku |
| url | http://dx.doi.org/10.1155/2017/4083293 |
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