Extremely Rare Case of Vulvar Myxoid Epithelioid Sarcoma
Epithelioid sarcoma is a distinct sarcoma type with specific morphology and immunophenotype. An epithelioid sarcoma of the vulva is an extremely rare and aggressive tumor and most commonly occurs on the labia majora in women of reproductive age. Only few cases have been reported, especially with the...
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| Format: | Article |
| Language: | English |
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Wiley
2015-01-01
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| Series: | Case Reports in Obstetrics and Gynecology |
| Online Access: | http://dx.doi.org/10.1155/2015/971217 |
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| author | Joana Lima Rego Georgia Fontes Cintra Ana Karina Junqueira Netto Lucas Faria Abrahão-Machado Audrey Tsunoda |
| author_facet | Joana Lima Rego Georgia Fontes Cintra Ana Karina Junqueira Netto Lucas Faria Abrahão-Machado Audrey Tsunoda |
| author_sort | Joana Lima Rego |
| collection | DOAJ |
| description | Epithelioid sarcoma is a distinct sarcoma type with specific morphology and immunophenotype. An epithelioid sarcoma of the vulva is an extremely rare and aggressive tumor and most commonly occurs on the labia majora in women of reproductive age. Only few cases have been reported, especially with the presence of focal myxoid changes. Early diagnosis is difficult because of its benign appearance as a painless subcutaneous nodule. Optimal treatment is not well established due to its rarity. We report a successfully approached case of vulvar epithelioid sarcoma that occurred in a 34-year-old female patient, treated with wide local excision, and review of the current medical literature. |
| format | Article |
| id | doaj-art-c91c8bb125884579ba3e2b94805b0c90 |
| institution | Kabale University |
| issn | 2090-6684 2090-6692 |
| language | English |
| publishDate | 2015-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Obstetrics and Gynecology |
| spelling | doaj-art-c91c8bb125884579ba3e2b94805b0c902025-02-03T01:09:47ZengWileyCase Reports in Obstetrics and Gynecology2090-66842090-66922015-01-01201510.1155/2015/971217971217Extremely Rare Case of Vulvar Myxoid Epithelioid SarcomaJoana Lima Rego0Georgia Fontes Cintra1Ana Karina Junqueira Netto2Lucas Faria Abrahão-Machado3Audrey Tsunoda4Gynecologic Department, Bissaya Barreto Maternity Hospital, CHUC, 3000-059 Coimbra, PortugalGynecologic Oncologic Department, Barretos Cancer Hospital, SP, BrazilRadiology Department, Barretos Cancer Hospital, SP, BrazilPathology Department, Barretos Hospital, SP, BrazilGynecologic Oncologic Department, Barretos Cancer Hospital, SP, BrazilEpithelioid sarcoma is a distinct sarcoma type with specific morphology and immunophenotype. An epithelioid sarcoma of the vulva is an extremely rare and aggressive tumor and most commonly occurs on the labia majora in women of reproductive age. Only few cases have been reported, especially with the presence of focal myxoid changes. Early diagnosis is difficult because of its benign appearance as a painless subcutaneous nodule. Optimal treatment is not well established due to its rarity. We report a successfully approached case of vulvar epithelioid sarcoma that occurred in a 34-year-old female patient, treated with wide local excision, and review of the current medical literature.http://dx.doi.org/10.1155/2015/971217 |
| spellingShingle | Joana Lima Rego Georgia Fontes Cintra Ana Karina Junqueira Netto Lucas Faria Abrahão-Machado Audrey Tsunoda Extremely Rare Case of Vulvar Myxoid Epithelioid Sarcoma Case Reports in Obstetrics and Gynecology |
| title | Extremely Rare Case of Vulvar Myxoid Epithelioid Sarcoma |
| title_full | Extremely Rare Case of Vulvar Myxoid Epithelioid Sarcoma |
| title_fullStr | Extremely Rare Case of Vulvar Myxoid Epithelioid Sarcoma |
| title_full_unstemmed | Extremely Rare Case of Vulvar Myxoid Epithelioid Sarcoma |
| title_short | Extremely Rare Case of Vulvar Myxoid Epithelioid Sarcoma |
| title_sort | extremely rare case of vulvar myxoid epithelioid sarcoma |
| url | http://dx.doi.org/10.1155/2015/971217 |
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