Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the Mediastinum
Paraneoplastic Pemphigus (PNP) is an autoimmune bullous disease characterized by severe stomatitis, polymorphous skin eruptions, and underlying neoplasms. Diagnosis of cutaneous paraneoplastic disorders requires high index of suspicion. We describe a patient with PNP associated with follicular dendr...
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| Format: | Article |
| Language: | English |
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Wiley
2016-01-01
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| Series: | Case Reports in Dermatological Medicine |
| Online Access: | http://dx.doi.org/10.1155/2016/6901539 |
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| author | Aparna Mullangath Prakasan Anne Jennifer Prabhu Kanmani Velarasan Selvamani Backianathan Thomas Samuel Ram |
| author_facet | Aparna Mullangath Prakasan Anne Jennifer Prabhu Kanmani Velarasan Selvamani Backianathan Thomas Samuel Ram |
| author_sort | Aparna Mullangath Prakasan |
| collection | DOAJ |
| description | Paraneoplastic Pemphigus (PNP) is an autoimmune bullous disease characterized by severe stomatitis, polymorphous skin eruptions, and underlying neoplasms. Diagnosis of cutaneous paraneoplastic disorders requires high index of suspicion. We describe a patient with PNP associated with follicular dendritic cell (FDC) tumor in the mediastinum, a rare neoplasm originating from follicular dendritic cells. Its management requires identification of underlying malignancy and treatment of the same. Our patient showed remission of PNP upon excision of the tumor and remained disease-free for 8 years. |
| format | Article |
| id | doaj-art-bc7e1047fd9841eea972936cf4a8f1bd |
| institution | Kabale University |
| issn | 2090-6463 2090-6471 |
| language | English |
| publishDate | 2016-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dermatological Medicine |
| spelling | doaj-art-bc7e1047fd9841eea972936cf4a8f1bd2025-02-03T05:51:26ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712016-01-01201610.1155/2016/69015396901539Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the MediastinumAparna Mullangath Prakasan0Anne Jennifer Prabhu1Kanmani Velarasan2Selvamani Backianathan3Thomas Samuel Ram4Ida B Scudder Cancer Centre, Radiation Oncology Unit 1, Christian Medical College, Ida Scudder Road, Vellore, Tamil Nadu 632004, IndiaDepartment of Pathology, Christian Medical College, Ida Scudder Road, Vellore, Tamil Nadu 632004, IndiaIda B Scudder Cancer Centre, Radiation Oncology Unit 1, Christian Medical College, Ida Scudder Road, Vellore, Tamil Nadu 632004, IndiaIda B Scudder Cancer Centre, Radiation Oncology Unit 1, Christian Medical College, Ida Scudder Road, Vellore, Tamil Nadu 632004, IndiaIda B Scudder Cancer Centre, Radiation Oncology Unit 1, Christian Medical College, Ida Scudder Road, Vellore, Tamil Nadu 632004, IndiaParaneoplastic Pemphigus (PNP) is an autoimmune bullous disease characterized by severe stomatitis, polymorphous skin eruptions, and underlying neoplasms. Diagnosis of cutaneous paraneoplastic disorders requires high index of suspicion. We describe a patient with PNP associated with follicular dendritic cell (FDC) tumor in the mediastinum, a rare neoplasm originating from follicular dendritic cells. Its management requires identification of underlying malignancy and treatment of the same. Our patient showed remission of PNP upon excision of the tumor and remained disease-free for 8 years.http://dx.doi.org/10.1155/2016/6901539 |
| spellingShingle | Aparna Mullangath Prakasan Anne Jennifer Prabhu Kanmani Velarasan Selvamani Backianathan Thomas Samuel Ram Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the Mediastinum Case Reports in Dermatological Medicine |
| title | Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the Mediastinum |
| title_full | Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the Mediastinum |
| title_fullStr | Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the Mediastinum |
| title_full_unstemmed | Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the Mediastinum |
| title_short | Paraneoplastic Pemphigus Associated with Follicular Dendritic Cell Tumor in the Mediastinum |
| title_sort | paraneoplastic pemphigus associated with follicular dendritic cell tumor in the mediastinum |
| url | http://dx.doi.org/10.1155/2016/6901539 |
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