Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis Complex
Tuberous sclerosis complex (TSC) is an autosomal dominant, variably expressed multisystem disease. The predominant pulmonary features of TSC are identical to those of lymphangioleiomyomatosis (LAM). Pneumothorax, multifocal micronodular pneumocyte hyperplasia, and chylothorax are rare complications...
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| Format: | Article |
| Language: | English |
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Wiley
2015-01-01
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| Series: | Case Reports in Critical Care |
| Online Access: | http://dx.doi.org/10.1155/2015/509094 |
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| author | Mohsin Ijaz Arsalan Rafiq Sindhaghatta Venkatram Gilda Diaz-Fuentes |
| author_facet | Mohsin Ijaz Arsalan Rafiq Sindhaghatta Venkatram Gilda Diaz-Fuentes |
| author_sort | Mohsin Ijaz |
| collection | DOAJ |
| description | Tuberous sclerosis complex (TSC) is an autosomal dominant, variably expressed multisystem disease. The predominant pulmonary features of TSC are identical to those of lymphangioleiomyomatosis (LAM). Pneumothorax, multifocal micronodular pneumocyte hyperplasia, and chylothorax are rare complications of TSC. We report a young male with pneumothorax, lung nodules, and chylous effusion who developed empyema thoracis after esophageal rupture. Hospital course was complicated by respiratory failure. Family opted to transfer to hospice care. Chylothorax is a rare complication of TSC with few scattered reports mostly in female patients. Patients with TSC are usually managed by multispecialists and it is important to be aware of the rare pulmonary manifestations of this disease. A male patient with TSC having lung nodules presenting with chylothorax and empyema thoracis from Boerhaave syndrome makes our case unique. |
| format | Article |
| id | doaj-art-bb7a05d99ebe41a8bd45161b0dde53c6 |
| institution | Kabale University |
| issn | 2090-6420 2090-6439 |
| language | English |
| publishDate | 2015-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Critical Care |
| spelling | doaj-art-bb7a05d99ebe41a8bd45161b0dde53c62025-02-03T05:45:14ZengWileyCase Reports in Critical Care2090-64202090-64392015-01-01201510.1155/2015/509094509094Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis ComplexMohsin Ijaz0Arsalan Rafiq1Sindhaghatta Venkatram2Gilda Diaz-Fuentes3Division of Critical Care Medicine, Montefiore Medical Center, Albert Einstein College of Medicine, Bronx, NY 10467, USADivision of Cardiology, Mount Sinai St. Luke’s Hospital, New York, NY 10025, USADivision of Pulmonary and Critical Care Medicine, Bronx-Lebanon Hospital Center, Bronx, NY 10457, USADivision of Pulmonary and Critical Care Medicine, Bronx-Lebanon Hospital Center, Bronx, NY 10457, USATuberous sclerosis complex (TSC) is an autosomal dominant, variably expressed multisystem disease. The predominant pulmonary features of TSC are identical to those of lymphangioleiomyomatosis (LAM). Pneumothorax, multifocal micronodular pneumocyte hyperplasia, and chylothorax are rare complications of TSC. We report a young male with pneumothorax, lung nodules, and chylous effusion who developed empyema thoracis after esophageal rupture. Hospital course was complicated by respiratory failure. Family opted to transfer to hospice care. Chylothorax is a rare complication of TSC with few scattered reports mostly in female patients. Patients with TSC are usually managed by multispecialists and it is important to be aware of the rare pulmonary manifestations of this disease. A male patient with TSC having lung nodules presenting with chylothorax and empyema thoracis from Boerhaave syndrome makes our case unique.http://dx.doi.org/10.1155/2015/509094 |
| spellingShingle | Mohsin Ijaz Arsalan Rafiq Sindhaghatta Venkatram Gilda Diaz-Fuentes Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis Complex Case Reports in Critical Care |
| title | Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis Complex |
| title_full | Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis Complex |
| title_fullStr | Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis Complex |
| title_full_unstemmed | Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis Complex |
| title_short | Boerhaave Syndrome, Pneumothorax, and Chylothorax in a Critically Ill Patient with Tuberous Sclerosis Complex |
| title_sort | boerhaave syndrome pneumothorax and chylothorax in a critically ill patient with tuberous sclerosis complex |
| url | http://dx.doi.org/10.1155/2015/509094 |
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