Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation
Primary leiomyosarcomas (LMS) of vascular origin are rare tumors, and more than half of the cases arise in the inferior vena cava (IVC). Primary LMS of the renal vein are extremely rare tumors with only a few cases reported in the literature. Their diagnosis is made only by pathological features. Hi...
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| Format: | Article |
| Language: | English |
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Wiley
2021-01-01
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| Series: | Case Reports in Pathology |
| Online Access: | http://dx.doi.org/10.1155/2021/6637533 |
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| author | Amal Fekkar Hafsa Elouazzani Ahmed Jahid Kaoutar Znati Fouad Zouaidia Zakia Bernoussi |
| author_facet | Amal Fekkar Hafsa Elouazzani Ahmed Jahid Kaoutar Znati Fouad Zouaidia Zakia Bernoussi |
| author_sort | Amal Fekkar |
| collection | DOAJ |
| description | Primary leiomyosarcomas (LMS) of vascular origin are rare tumors, and more than half of the cases arise in the inferior vena cava (IVC). Primary LMS of the renal vein are extremely rare tumors with only a few cases reported in the literature. Their diagnosis is made only by pathological features. Histologically, they are made of atypical spindle-shaped cells arranged in long intersecting fascicles. Tumor cells stain positive for myogenic markers in immunohistochemistry. Standard treatment consists of radical nephrectomy followed by chemotherapy and/or radiotherapy. Because of insufficient histological data and follow-up, the prognosis factors are not well identified. Overall prognosis of renal vein LMS is poor. We report here an exceptional case of a huge LMS of the right renal vein mimicking a primitive renal cell carcinoma, occurring in a 56-year-old male patient. |
| format | Article |
| id | doaj-art-b673c3f3efcb45beb51e5dd0816ee622 |
| institution | Kabale University |
| issn | 2090-6781 2090-679X |
| language | English |
| publishDate | 2021-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pathology |
| spelling | doaj-art-b673c3f3efcb45beb51e5dd0816ee6222025-02-03T06:43:57ZengWileyCase Reports in Pathology2090-67812090-679X2021-01-01202110.1155/2021/66375336637533Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual PresentationAmal Fekkar0Hafsa Elouazzani1Ahmed Jahid2Kaoutar Znati3Fouad Zouaidia4Zakia Bernoussi5Department of Pathology, Ibn Sina University Hospital Center, Rabat, MoroccoDepartment of Pathology, Ibn Sina University Hospital Center, Rabat, MoroccoDepartment of Pathology, Ibn Sina University Hospital Center, Rabat, MoroccoDepartment of Pathology, Ibn Sina University Hospital Center, Rabat, MoroccoDepartment of Pathology, Ibn Sina University Hospital Center, Rabat, MoroccoDepartment of Pathology, Ibn Sina University Hospital Center, Rabat, MoroccoPrimary leiomyosarcomas (LMS) of vascular origin are rare tumors, and more than half of the cases arise in the inferior vena cava (IVC). Primary LMS of the renal vein are extremely rare tumors with only a few cases reported in the literature. Their diagnosis is made only by pathological features. Histologically, they are made of atypical spindle-shaped cells arranged in long intersecting fascicles. Tumor cells stain positive for myogenic markers in immunohistochemistry. Standard treatment consists of radical nephrectomy followed by chemotherapy and/or radiotherapy. Because of insufficient histological data and follow-up, the prognosis factors are not well identified. Overall prognosis of renal vein LMS is poor. We report here an exceptional case of a huge LMS of the right renal vein mimicking a primitive renal cell carcinoma, occurring in a 56-year-old male patient.http://dx.doi.org/10.1155/2021/6637533 |
| spellingShingle | Amal Fekkar Hafsa Elouazzani Ahmed Jahid Kaoutar Znati Fouad Zouaidia Zakia Bernoussi Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation Case Reports in Pathology |
| title | Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation |
| title_full | Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation |
| title_fullStr | Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation |
| title_full_unstemmed | Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation |
| title_short | Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation |
| title_sort | leiomyosarcoma of the renal vein mimicking a primitive renal cell carcinoma case report of an unusual presentation |
| url | http://dx.doi.org/10.1155/2021/6637533 |
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