Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case report
Abstract Proximal Interruption of the Pulmonary Artery (PIPA) is a rare congenital condition with an incidence of 1 in 200,000–300,000 individuals. We report the case of a 67-year-old woman with PIPA who presented with massive haemoptysis. Imaging revealed a small calibre right main pulmonary artery...
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| Language: | English |
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SpringerOpen
2025-08-01
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| Series: | CVIR Endovascular |
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| Online Access: | https://doi.org/10.1186/s42155-025-00519-0 |
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| author | Runlin Yang Robert Ng Albert Goh Richard Pow |
| author_facet | Runlin Yang Robert Ng Albert Goh Richard Pow |
| author_sort | Runlin Yang |
| collection | DOAJ |
| description | Abstract Proximal Interruption of the Pulmonary Artery (PIPA) is a rare congenital condition with an incidence of 1 in 200,000–300,000 individuals. We report the case of a 67-year-old woman with PIPA who presented with massive haemoptysis. Imaging revealed a small calibre right main pulmonary artery, absence of upper/middle lobe pulmonary arteries, and tortuous right systemic collateral arteries. A multidisciplinary meeting favoured bronchial artery embolisation over right pneumonectomy, due to the bleeding risk associated with extensive transpleural systemic collateral arteries. The patient underwent two staged bronchial artery embolisation and remained free of haemoptysis at the most recent 13-month follow-up. This case highlights the potential for bronchial artery embolisation to serve as a first-line treatment in managing PIPA, as a less invasive alternative to surgery. |
| format | Article |
| id | doaj-art-b2432d548a1c42e3aa0e4c8e8b0589e1 |
| institution | Kabale University |
| issn | 2520-8934 |
| language | English |
| publishDate | 2025-08-01 |
| publisher | SpringerOpen |
| record_format | Article |
| series | CVIR Endovascular |
| spelling | doaj-art-b2432d548a1c42e3aa0e4c8e8b0589e12025-08-20T03:43:37ZengSpringerOpenCVIR Endovascular2520-89342025-08-01811610.1186/s42155-025-00519-0Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case reportRunlin Yang0Robert Ng1Albert Goh2Richard Pow3Department of Interventional Radiology, Royal North Shore HospitalDepartment of Interventional Radiology, Royal North Shore HospitalDepartment of Interventional Radiology, Royal North Shore HospitalDepartment of Interventional Radiology, Royal North Shore HospitalAbstract Proximal Interruption of the Pulmonary Artery (PIPA) is a rare congenital condition with an incidence of 1 in 200,000–300,000 individuals. We report the case of a 67-year-old woman with PIPA who presented with massive haemoptysis. Imaging revealed a small calibre right main pulmonary artery, absence of upper/middle lobe pulmonary arteries, and tortuous right systemic collateral arteries. A multidisciplinary meeting favoured bronchial artery embolisation over right pneumonectomy, due to the bleeding risk associated with extensive transpleural systemic collateral arteries. The patient underwent two staged bronchial artery embolisation and remained free of haemoptysis at the most recent 13-month follow-up. This case highlights the potential for bronchial artery embolisation to serve as a first-line treatment in managing PIPA, as a less invasive alternative to surgery.https://doi.org/10.1186/s42155-025-00519-0Proximal interruption of the pulmonary arteryBronchial artery embolisation |
| spellingShingle | Runlin Yang Robert Ng Albert Goh Richard Pow Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case report CVIR Endovascular Proximal interruption of the pulmonary artery Bronchial artery embolisation |
| title | Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case report |
| title_full | Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case report |
| title_fullStr | Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case report |
| title_full_unstemmed | Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case report |
| title_short | Proximal interruption of the pulmonary artery with systemic bronchial/intercostal aneurysm formation: a case report |
| title_sort | proximal interruption of the pulmonary artery with systemic bronchial intercostal aneurysm formation a case report |
| topic | Proximal interruption of the pulmonary artery Bronchial artery embolisation |
| url | https://doi.org/10.1186/s42155-025-00519-0 |
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