Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS
Prader-Willi syndrome (PWS) is the most prevalent syndromic form of obesity, which starts during early childhood in the setting of hyperphagia. Due to the development of obesity, there is a high prevalence of obstructive sleep apnea (OSA) among these patients. This case report presents a patient wit...
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| Format: | Article |
| Language: | English |
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Wiley
2023-01-01
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| Series: | Case Reports in Medicine |
| Online Access: | http://dx.doi.org/10.1155/2023/9925144 |
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| author | Nauras Hwig Montserrat Diaz-Abad Victor T. Peng Jennifer Y. So Anayansi Lasso-Pirot |
| author_facet | Nauras Hwig Montserrat Diaz-Abad Victor T. Peng Jennifer Y. So Anayansi Lasso-Pirot |
| author_sort | Nauras Hwig |
| collection | DOAJ |
| description | Prader-Willi syndrome (PWS) is the most prevalent syndromic form of obesity, which starts during early childhood in the setting of hyperphagia. Due to the development of obesity, there is a high prevalence of obstructive sleep apnea (OSA) among these patients. This case report presents a patient with PWS with morbid obesity, severe OSA, and obesity hypoventilation syndrome admitted to the hospital for hypoxemic and hypercapnic respiratory failure. Noninvasive ventilation (NIV) with average volume-assured pressure support, a newer NIV modality, was used successfully to treat this patient, achieving major clinical and gas exchange improvement both during the hospitalization and long term after discharge. |
| format | Article |
| id | doaj-art-ad691c820a77450c8cfe04bd8f850450 |
| institution | Kabale University |
| issn | 1687-9635 |
| language | English |
| publishDate | 2023-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Medicine |
| spelling | doaj-art-ad691c820a77450c8cfe04bd8f8504502025-02-03T06:42:37ZengWileyCase Reports in Medicine1687-96352023-01-01202310.1155/2023/9925144Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPSNauras Hwig0Montserrat Diaz-Abad1Victor T. Peng2Jennifer Y. So3Anayansi Lasso-Pirot4Sleep Disorders CenterDepartment of MedicineSleep Disorders CenterDepartment of MedicineDepartment of PediatricsPrader-Willi syndrome (PWS) is the most prevalent syndromic form of obesity, which starts during early childhood in the setting of hyperphagia. Due to the development of obesity, there is a high prevalence of obstructive sleep apnea (OSA) among these patients. This case report presents a patient with PWS with morbid obesity, severe OSA, and obesity hypoventilation syndrome admitted to the hospital for hypoxemic and hypercapnic respiratory failure. Noninvasive ventilation (NIV) with average volume-assured pressure support, a newer NIV modality, was used successfully to treat this patient, achieving major clinical and gas exchange improvement both during the hospitalization and long term after discharge.http://dx.doi.org/10.1155/2023/9925144 |
| spellingShingle | Nauras Hwig Montserrat Diaz-Abad Victor T. Peng Jennifer Y. So Anayansi Lasso-Pirot Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS Case Reports in Medicine |
| title | Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS |
| title_full | Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS |
| title_fullStr | Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS |
| title_full_unstemmed | Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS |
| title_short | Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS |
| title_sort | successful treatment of respiratory failure in a patient with prader willi syndrome with noninvasive ventilation with avaps |
| url | http://dx.doi.org/10.1155/2023/9925144 |
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