A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of Jadassohn
Nevus sebaceus of Jadassohn, or “organoid nevus,” is a common, benign hamartoma of the skin consisting of epithelial and adnexal components. Its natural history and association with neoplastic growths is well documented. The majority of concomitant neoplasms are benign—trichoblastoma and syringocyst...
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| Format: | Article |
| Language: | English |
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Wiley
2021-01-01
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| Series: | Case Reports in Dermatological Medicine |
| Online Access: | http://dx.doi.org/10.1155/2021/7598086 |
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| author | Drew C. Mitchell Gina J. Kuehn Glynis A. Scott Timothy D. Doerr Francisco Tausk |
| author_facet | Drew C. Mitchell Gina J. Kuehn Glynis A. Scott Timothy D. Doerr Francisco Tausk |
| author_sort | Drew C. Mitchell |
| collection | DOAJ |
| description | Nevus sebaceus of Jadassohn, or “organoid nevus,” is a common, benign hamartoma of the skin consisting of epithelial and adnexal components. Its natural history and association with neoplastic growths is well documented. The majority of concomitant neoplasms are benign—trichoblastoma and syringocystadenoma papilliferum are most frequently discovered—but malignant tumors have been described. We present the case of a 58-year-old male with a congenital nevus sebaceus of Jadassohn on his left parietal scalp that had been enlarging, changing color, and bleeding over the prior year. Clinical exam and histology disclosed the presence of a trichoblastoma and porocarcinoma arising within the nevus sebaceus. Porocarcinoma is a rare, intermediately aggressive, malignant eccrine gland tumor that is frequently metastasized at presentation. Otolaryngology performed wide local resection with sentinel lymph node biopsy. This case highlights the diversity of tumors associated with nevus sebaceus of Jadassohn, potential for malignant expansion, and necessity for close monitoring and maintaining a low threshold for biopsy in evolving lesions. |
| format | Article |
| id | doaj-art-ac4b843e098a440392b9990d5a877cb7 |
| institution | Kabale University |
| issn | 2090-6463 2090-6471 |
| language | English |
| publishDate | 2021-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dermatological Medicine |
| spelling | doaj-art-ac4b843e098a440392b9990d5a877cb72025-02-03T06:07:38ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712021-01-01202110.1155/2021/75980867598086A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of JadassohnDrew C. Mitchell0Gina J. Kuehn1Glynis A. Scott2Timothy D. Doerr3Francisco Tausk4University of Rochester School of Medicine & Dentistry, 601 Elmwood Avenue Box 400, Rochester, NY 14642, USADepartment of Dermatology, University of Rochester Medical Center, 40 Celebration Drive, Rochester, NY 14642, USADepartment of Dermatology, University of Rochester Medical Center, 40 Celebration Drive, Rochester, NY 14642, USADepartment of Otolaryngology, University of Rochester Medical Center, 601 Elmwood Avenue Box 629, Rochester, NY 14642, USADepartment of Dermatology, University of Rochester Medical Center, 40 Celebration Drive, Rochester, NY 14642, USANevus sebaceus of Jadassohn, or “organoid nevus,” is a common, benign hamartoma of the skin consisting of epithelial and adnexal components. Its natural history and association with neoplastic growths is well documented. The majority of concomitant neoplasms are benign—trichoblastoma and syringocystadenoma papilliferum are most frequently discovered—but malignant tumors have been described. We present the case of a 58-year-old male with a congenital nevus sebaceus of Jadassohn on his left parietal scalp that had been enlarging, changing color, and bleeding over the prior year. Clinical exam and histology disclosed the presence of a trichoblastoma and porocarcinoma arising within the nevus sebaceus. Porocarcinoma is a rare, intermediately aggressive, malignant eccrine gland tumor that is frequently metastasized at presentation. Otolaryngology performed wide local resection with sentinel lymph node biopsy. This case highlights the diversity of tumors associated with nevus sebaceus of Jadassohn, potential for malignant expansion, and necessity for close monitoring and maintaining a low threshold for biopsy in evolving lesions.http://dx.doi.org/10.1155/2021/7598086 |
| spellingShingle | Drew C. Mitchell Gina J. Kuehn Glynis A. Scott Timothy D. Doerr Francisco Tausk A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of Jadassohn Case Reports in Dermatological Medicine |
| title | A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of Jadassohn |
| title_full | A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of Jadassohn |
| title_fullStr | A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of Jadassohn |
| title_full_unstemmed | A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of Jadassohn |
| title_short | A Rare Case of Porocarcinoma and Trichoblastoma Arising in a Nevus Sebaceus of Jadassohn |
| title_sort | rare case of porocarcinoma and trichoblastoma arising in a nevus sebaceus of jadassohn |
| url | http://dx.doi.org/10.1155/2021/7598086 |
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