A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature Review
Gastroschisis most often occurs as an isolated anomaly and extragastrointestinal associations are rare. Most commonly, the anomalies associated with gastroschisis are cardiac and central nervous system abnormalities. Respiratory insufficiency has sometimes been reported in association with giant abd...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Pathology |
| Online Access: | http://dx.doi.org/10.1155/2018/8378769 |
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| author | Surasak Puvabanditsin Robin Burger Vidya Puthenpura Lauren Walzer Adaora Madubuko Christine Minerowicz Rajeev Mehta |
| author_facet | Surasak Puvabanditsin Robin Burger Vidya Puthenpura Lauren Walzer Adaora Madubuko Christine Minerowicz Rajeev Mehta |
| author_sort | Surasak Puvabanditsin |
| collection | DOAJ |
| description | Gastroschisis most often occurs as an isolated anomaly and extragastrointestinal associations are rare. Most commonly, the anomalies associated with gastroschisis are cardiac and central nervous system abnormalities. Respiratory insufficiency has sometimes been reported in association with giant abdominal wall defects. Poor outcomes and prolonged ventilator support have been reported in giant gastroschisis and omphalocele, especially if associated with herniation of the majority of the liver. We report a case of a large gastroschisis that was associated with a kyphoscoliosis and pulmonary hypoplasia. |
| format | Article |
| id | doaj-art-a911c96894d44b7f93ecc97ae110080a |
| institution | Kabale University |
| issn | 2090-6781 2090-679X |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pathology |
| spelling | doaj-art-a911c96894d44b7f93ecc97ae110080a2025-02-03T05:57:32ZengWileyCase Reports in Pathology2090-67812090-679X2018-01-01201810.1155/2018/83787698378769A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature ReviewSurasak Puvabanditsin0Robin Burger1Vidya Puthenpura2Lauren Walzer3Adaora Madubuko4Christine Minerowicz5Rajeev Mehta6Department of Pediatrics, Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USADepartment of Pathology, Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USADepartment of Pediatrics, Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USADepartment of Pediatrics, Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USADepartment of Pediatrics, Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USADepartment of Pathology, Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USADepartment of Pediatrics, Rutgers Robert Wood Johnson Medical School, New Brunswick, NJ, USAGastroschisis most often occurs as an isolated anomaly and extragastrointestinal associations are rare. Most commonly, the anomalies associated with gastroschisis are cardiac and central nervous system abnormalities. Respiratory insufficiency has sometimes been reported in association with giant abdominal wall defects. Poor outcomes and prolonged ventilator support have been reported in giant gastroschisis and omphalocele, especially if associated with herniation of the majority of the liver. We report a case of a large gastroschisis that was associated with a kyphoscoliosis and pulmonary hypoplasia.http://dx.doi.org/10.1155/2018/8378769 |
| spellingShingle | Surasak Puvabanditsin Robin Burger Vidya Puthenpura Lauren Walzer Adaora Madubuko Christine Minerowicz Rajeev Mehta A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature Review Case Reports in Pathology |
| title | A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature Review |
| title_full | A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature Review |
| title_fullStr | A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature Review |
| title_full_unstemmed | A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature Review |
| title_short | A Giant Gastroschisis Associated with Pulmonary Hypoplasia and Spinal Anomaly: A Case Report and a Literature Review |
| title_sort | giant gastroschisis associated with pulmonary hypoplasia and spinal anomaly a case report and a literature review |
| url | http://dx.doi.org/10.1155/2018/8378769 |
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