Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections
Linear scleroderma “en coup de sabre” (LSCS) is a form of localized scleroderma presents as band-like sclerotic lesions of the frontoparietal area. It has been reported in association with diverse neurological manifestations like seizures, migraine, neuromyotonia, dystonia and abnormalities in MRI...
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| Format: | Article |
| Language: | English |
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Wiley
2012-01-01
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| Series: | Case Reports in Medicine |
| Online Access: | http://dx.doi.org/10.1155/2012/691314 |
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| author | Carlos A. Cañas Jorge L. Orozco Andrea Caicedo Paredes Fabio Bonilla-Abadía |
| author_facet | Carlos A. Cañas Jorge L. Orozco Andrea Caicedo Paredes Fabio Bonilla-Abadía |
| author_sort | Carlos A. Cañas |
| collection | DOAJ |
| description | Linear scleroderma “en coup de sabre” (LSCS) is a form of localized scleroderma presents as band-like sclerotic lesions of the frontoparietal area. It has been reported in association with diverse neurological manifestations like seizures, migraine, neuromyotonia, dystonia and abnormalities in MRI and CT studies as cerebral atrophy, white matter lesions, intraparenchymal calcification, meningeocortical alterations, and skull atrophy. We describe a patient with LSCS associated with two abnormal movements: permanent myokimia of right masseter muscle and recurrent spasmodic retraction of right cigomatic and depressor labii inferioris muscles. He was initially treated with methotrexate and steroids without response, so later on he underwent repeated Botox injections with remarkable improvement. |
| format | Article |
| id | doaj-art-a26eb73e6197469bbca53e60a3580788 |
| institution | Kabale University |
| issn | 1687-9627 1687-9635 |
| language | English |
| publishDate | 2012-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Medicine |
| spelling | doaj-art-a26eb73e6197469bbca53e60a35807882025-02-03T05:46:45ZengWileyCase Reports in Medicine1687-96271687-96352012-01-01201210.1155/2012/691314691314Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox InjectionsCarlos A. Cañas0Jorge L. Orozco1Andrea Caicedo Paredes2Fabio Bonilla-Abadía3Department of Rheumatology, Fundación Valle del Lili, ICESI University, Cali, ColombiaDepartament of Neurology, Fundación Valle del Lili, Cali, ColombiaDepartment of Internal Medicine, Fundación Valle del Lili, Cali, ColombiaDepartment of Rheumatology, Fundación Valle del Lili, ICESI University, Cali, ColombiaLinear scleroderma “en coup de sabre” (LSCS) is a form of localized scleroderma presents as band-like sclerotic lesions of the frontoparietal area. It has been reported in association with diverse neurological manifestations like seizures, migraine, neuromyotonia, dystonia and abnormalities in MRI and CT studies as cerebral atrophy, white matter lesions, intraparenchymal calcification, meningeocortical alterations, and skull atrophy. We describe a patient with LSCS associated with two abnormal movements: permanent myokimia of right masseter muscle and recurrent spasmodic retraction of right cigomatic and depressor labii inferioris muscles. He was initially treated with methotrexate and steroids without response, so later on he underwent repeated Botox injections with remarkable improvement.http://dx.doi.org/10.1155/2012/691314 |
| spellingShingle | Carlos A. Cañas Jorge L. Orozco Andrea Caicedo Paredes Fabio Bonilla-Abadía Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections Case Reports in Medicine |
| title | Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections |
| title_full | Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections |
| title_fullStr | Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections |
| title_full_unstemmed | Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections |
| title_short | Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections |
| title_sort | successful treatment of hemifacial myokymia and dystonia associated to linear scleroderma en coup de sabre with repeated botox injections |
| url | http://dx.doi.org/10.1155/2012/691314 |
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