Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare Müllerian duct anomaly, commonly characterized by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. While these are the three most common genitourinary anomalies in OHVIRA syndrome, a spectrum o...
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| Format: | Article |
| Language: | English |
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The Korean Society of Radiology
2025-01-01
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| Series: | Journal of the Korean Society of Radiology |
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| Online Access: | https://doi.org/10.3348/jksr.2024.0018 |
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| author | Hyun Jeong Kim Eun Ji Lee Yun-Woo Chang Seong Sook Hong Jiyoung Hwang Boda Nam Sung Hwan Bae |
| author_facet | Hyun Jeong Kim Eun Ji Lee Yun-Woo Chang Seong Sook Hong Jiyoung Hwang Boda Nam Sung Hwan Bae |
| author_sort | Hyun Jeong Kim |
| collection | DOAJ |
| description | Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare Müllerian
duct anomaly, commonly characterized by uterus didelphys, obstructed hemivagina, and
ipsilateral renal agenesis. While these are the three most common genitourinary anomalies
in OHVIRA syndrome, a spectrum of urogenital anomalies can be present. Knowledge of this
spectrum is crucial for proper patient management and treatment planning. In this case series,
we report on five patients with OHVIRA syndrome, each presenting with a urogenital
anomaly other than the typical renal agenesis or uterus didelphys. We highlight the gynecological
complications encountered, which clinicians and radiologists should be aware of. |
| format | Article |
| id | doaj-art-9ec70a60414249bcb2c8d0e2f87570dd |
| institution | Kabale University |
| issn | 2951-0805 |
| language | English |
| publishDate | 2025-01-01 |
| publisher | The Korean Society of Radiology |
| record_format | Article |
| series | Journal of the Korean Society of Radiology |
| spelling | doaj-art-9ec70a60414249bcb2c8d0e2f87570dd2025-01-31T07:35:50ZengThe Korean Society of RadiologyJournal of the Korean Society of Radiology2951-08052025-01-01861129140https://doi.org/10.3348/jksr.2024.0018Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case SeriesHyun Jeong KimEun Ji LeeYun-Woo ChangSeong Sook HongJiyoung HwangBoda NamSung Hwan BaeObstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare Müllerian duct anomaly, commonly characterized by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. While these are the three most common genitourinary anomalies in OHVIRA syndrome, a spectrum of urogenital anomalies can be present. Knowledge of this spectrum is crucial for proper patient management and treatment planning. In this case series, we report on five patients with OHVIRA syndrome, each presenting with a urogenital anomaly other than the typical renal agenesis or uterus didelphys. We highlight the gynecological complications encountered, which clinicians and radiologists should be aware of.https://doi.org/10.3348/jksr.2024.0018ohvira syndromeurogenital anomalyectopic ureterclassificationvaginal cancer |
| spellingShingle | Hyun Jeong Kim Eun Ji Lee Yun-Woo Chang Seong Sook Hong Jiyoung Hwang Boda Nam Sung Hwan Bae Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series Journal of the Korean Society of Radiology ohvira syndrome urogenital anomaly ectopic ureter classification vaginal cancer |
| title | Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series |
| title_full | Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series |
| title_fullStr | Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series |
| title_full_unstemmed | Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series |
| title_short | Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series |
| title_sort | anatomical variations genitourinary anomalies and clinical presentations in obstructed hemivagina and ipsilateral renal anomaly syndrome case series |
| topic | ohvira syndrome urogenital anomaly ectopic ureter classification vaginal cancer |
| url | https://doi.org/10.3348/jksr.2024.0018 |
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