Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series

Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare Müllerian duct anomaly, commonly characterized by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. While these are the three most common genitourinary anomalies in OHVIRA syndrome, a spectrum o...

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Bibliographic Details
Main Authors: Hyun Jeong Kim, Eun Ji Lee, Yun-Woo Chang, Seong Sook Hong, Jiyoung Hwang, Boda Nam, Sung Hwan Bae
Format: Article
Language:English
Published: The Korean Society of Radiology 2025-01-01
Series:Journal of the Korean Society of Radiology
Subjects:
ohvira syndrome
urogenital anomaly
ectopic ureter
classification
vaginal cancer
Online Access:https://doi.org/10.3348/jksr.2024.0018
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Summary:Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare Müllerian duct anomaly, commonly characterized by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. While these are the three most common genitourinary anomalies in OHVIRA syndrome, a spectrum of urogenital anomalies can be present. Knowledge of this spectrum is crucial for proper patient management and treatment planning. In this case series, we report on five patients with OHVIRA syndrome, each presenting with a urogenital anomaly other than the typical renal agenesis or uterus didelphys. We highlight the gynecological complications encountered, which clinicians and radiologists should be aware of.
ISSN:2951-0805

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