Dyschromatosis Symmetrica Hereditaria of Late Onset?

Dyschromatosis symmetrica hereditaria (DSH), also known as reticulated acropigmentation of Dohi, is an autosomal dominant disease with high penetrance, characterized by hypo- and hyperpigmented macules of varying sizes on the dorsal of the extremities with reticulated pattern. This paper presents a...

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Main Authors: Caroline Balvedi Gaiewski, Sergio Zuneda Serafini, Betina Werner, Janyana M. D. Deonizio
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Dermatological Medicine
Online Access:http://dx.doi.org/10.1155/2014/639537
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author Caroline Balvedi Gaiewski
Sergio Zuneda Serafini
Betina Werner
Janyana M. D. Deonizio
author_facet Caroline Balvedi Gaiewski
Sergio Zuneda Serafini
Betina Werner
Janyana M. D. Deonizio
author_sort Caroline Balvedi Gaiewski
collection DOAJ
description Dyschromatosis symmetrica hereditaria (DSH), also known as reticulated acropigmentation of Dohi, is an autosomal dominant disease with high penetrance, characterized by hypo- and hyperpigmented macules of varying sizes on the dorsal of the extremities with reticulated pattern. This paper presents a female patient with typical dermatological lesions, but only diagnosed in adulthood. It is necessary to perform differential diagnosis with other pigmentary disorders. This entity is not very common in South America, and the vast majority of cases were described in Japanese population. Since it is a benign disease, it is important to be aware of this diagnosis in order to establish the correct conduct for these patients.
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institution Kabale University
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publishDate 2014-01-01
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series Case Reports in Dermatological Medicine
spelling doaj-art-949ad9cf38344895a7fe8ef7041fed4e2025-02-03T01:00:01ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712014-01-01201410.1155/2014/639537639537Dyschromatosis Symmetrica Hereditaria of Late Onset?Caroline Balvedi Gaiewski0Sergio Zuneda Serafini1Betina Werner2Janyana M. D. Deonizio3Dermatology Department, Federal University of Parana, 80530-905 Curitiba, PR, BrazilDermatology Department, Federal University of Parana, 80530-905 Curitiba, PR, BrazilPathology Department, Federal University of Parana, 80530-905 Curitiba, PR, BrazilDermatology Department, Federal University of Parana, 80530-905 Curitiba, PR, BrazilDyschromatosis symmetrica hereditaria (DSH), also known as reticulated acropigmentation of Dohi, is an autosomal dominant disease with high penetrance, characterized by hypo- and hyperpigmented macules of varying sizes on the dorsal of the extremities with reticulated pattern. This paper presents a female patient with typical dermatological lesions, but only diagnosed in adulthood. It is necessary to perform differential diagnosis with other pigmentary disorders. This entity is not very common in South America, and the vast majority of cases were described in Japanese population. Since it is a benign disease, it is important to be aware of this diagnosis in order to establish the correct conduct for these patients.http://dx.doi.org/10.1155/2014/639537
spellingShingle Caroline Balvedi Gaiewski
Sergio Zuneda Serafini
Betina Werner
Janyana M. D. Deonizio
Dyschromatosis Symmetrica Hereditaria of Late Onset?
Case Reports in Dermatological Medicine
title Dyschromatosis Symmetrica Hereditaria of Late Onset?
title_full Dyschromatosis Symmetrica Hereditaria of Late Onset?
title_fullStr Dyschromatosis Symmetrica Hereditaria of Late Onset?
title_full_unstemmed Dyschromatosis Symmetrica Hereditaria of Late Onset?
title_short Dyschromatosis Symmetrica Hereditaria of Late Onset?
title_sort dyschromatosis symmetrica hereditaria of late onset
url http://dx.doi.org/10.1155/2014/639537
work_keys_str_mv AT carolinebalvedigaiewski dyschromatosissymmetricahereditariaoflateonset
AT sergiozunedaserafini dyschromatosissymmetricahereditariaoflateonset
AT betinawerner dyschromatosissymmetricahereditariaoflateonset
AT janyanamddeonizio dyschromatosissymmetricahereditariaoflateonset