Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome
Hereditary kidney cancer patients with bilateral multiple kidney tumors represent challenges in the era of rapidly growing minimal invasive treatment techniques. Birt-Hogg-Dubé Syndrome (BHDS) is an autosomal dominant genodermatosis characterized by a triad of benign skin tumors (fibrofolliculomas,...
Saved in:
| Main Authors: | , , , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wiley
2012-01-01
|
| Series: | Case Reports in Medicine |
| Online Access: | http://dx.doi.org/10.1155/2012/639629 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1832554234234535936 |
|---|---|
| author | Ahmet Tefekli Ayşe Deniz Akkaya Kamil Peker Terman Gümüş Metin Vural Fatin Cezayirli Ahmet Musaoglu Tarık Esen |
| author_facet | Ahmet Tefekli Ayşe Deniz Akkaya Kamil Peker Terman Gümüş Metin Vural Fatin Cezayirli Ahmet Musaoglu Tarık Esen |
| author_sort | Ahmet Tefekli |
| collection | DOAJ |
| description | Hereditary kidney cancer patients with bilateral multiple kidney tumors represent challenges in the era of rapidly growing minimal invasive treatment techniques. Birt-Hogg-Dubé Syndrome (BHDS) is an autosomal dominant genodermatosis characterized by a triad of benign skin tumors (fibrofolliculomas, trichodiscomas, acrochordons) together with an increased risk of developing malignant renal tumors and pulmonary disease such as pneumothoraces and multiple lung cysts. The morbidity and mortality of the affected patients is determined by the presence of the kidney tumors, which tend to be multifocal and bilateral, as observed in other hereditary kidney cancer syndromes like von Hippel-Lindau disease, familial leiomyomatosis, and hereditary papillary renal cell carcinoma. Herein, a patient with BHDS, presenting with synchronous bilateral multiple kidney tumors, is reported. The report describes the management of kidney tumors with two-stage open nephron-sparing surgery in which the nonvascular clamping technique was utilized. |
| format | Article |
| id | doaj-art-902de5428a6b476f8afc340cee940ba2 |
| institution | Kabale University |
| issn | 1687-9627 1687-9635 |
| language | English |
| publishDate | 2012-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Medicine |
| spelling | doaj-art-902de5428a6b476f8afc340cee940ba22025-02-03T05:51:59ZengWileyCase Reports in Medicine1687-96271687-96352012-01-01201210.1155/2012/639629639629Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé SyndromeAhmet Tefekli0Ayşe Deniz Akkaya1Kamil Peker2Terman Gümüş3Metin Vural4Fatin Cezayirli5Ahmet Musaoglu6Tarık Esen7Department of Urology, VKF American Hospital, 34365 Istanbul, TurkeyDepartment of Dermatology, VKF American Hospital, 34365 Istanbul, TurkeyIstanbul Pathology Group, 34365 Istanbul, TurkeyDepartment of Radiology, VKF American Hospital, 34365 Istanbul, TurkeyDepartment of Radiology, VKF American Hospital, 34365 Istanbul, TurkeyDepartment of Urology, VKF American Hospital, 34365 Istanbul, TurkeyDepartment of Urology, VKF American Hospital, 34365 Istanbul, TurkeyDepartment of Urology, VKF American Hospital, 34365 Istanbul, TurkeyHereditary kidney cancer patients with bilateral multiple kidney tumors represent challenges in the era of rapidly growing minimal invasive treatment techniques. Birt-Hogg-Dubé Syndrome (BHDS) is an autosomal dominant genodermatosis characterized by a triad of benign skin tumors (fibrofolliculomas, trichodiscomas, acrochordons) together with an increased risk of developing malignant renal tumors and pulmonary disease such as pneumothoraces and multiple lung cysts. The morbidity and mortality of the affected patients is determined by the presence of the kidney tumors, which tend to be multifocal and bilateral, as observed in other hereditary kidney cancer syndromes like von Hippel-Lindau disease, familial leiomyomatosis, and hereditary papillary renal cell carcinoma. Herein, a patient with BHDS, presenting with synchronous bilateral multiple kidney tumors, is reported. The report describes the management of kidney tumors with two-stage open nephron-sparing surgery in which the nonvascular clamping technique was utilized.http://dx.doi.org/10.1155/2012/639629 |
| spellingShingle | Ahmet Tefekli Ayşe Deniz Akkaya Kamil Peker Terman Gümüş Metin Vural Fatin Cezayirli Ahmet Musaoglu Tarık Esen Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome Case Reports in Medicine |
| title | Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome |
| title_full | Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome |
| title_fullStr | Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome |
| title_full_unstemmed | Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome |
| title_short | Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome |
| title_sort | staged open no ischemia nephron sparing surgery for bilateral multiple kidney tumors in a patient with birt hogg dube syndrome |
| url | http://dx.doi.org/10.1155/2012/639629 |
| work_keys_str_mv | AT ahmettefekli stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome AT aysedenizakkaya stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome AT kamilpeker stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome AT termangumus stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome AT metinvural stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome AT fatincezayirli stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome AT ahmetmusaoglu stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome AT tarıkesen stagedopennoischemianephronsparingsurgeryforbilateralmultiplekidneytumorsinapatientwithbirthoggdubesyndrome |