Desquamative interstitial pneumonia: If there is smoke there is fire
Desquamative interstitial pneumonia (DIP) is a rare type of idiopathic interstitial lung disease (ILD) predominantly seen in smokers. Connective tissue diseases (CTDs) are one of the important causes of ILD and may have lung involvement antedating their usual manifestations, making the diagnosis dif...
Saved in:
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2023-12-01
|
| Series: | The Journal of Association of Chest Physicians |
| Subjects: | |
| Online Access: | https://journals.lww.com/10.4103/jacp.jacp_39_23 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1832593943737401344 |
|---|---|
| author | Amit Panjwani Husain Kadhem Saadeya Naji Abdulkarim Umesh Nabar |
| author_facet | Amit Panjwani Husain Kadhem Saadeya Naji Abdulkarim Umesh Nabar |
| author_sort | Amit Panjwani |
| collection | DOAJ |
| description | Desquamative interstitial pneumonia (DIP) is a rare type of idiopathic interstitial lung disease (ILD) predominantly seen in smokers. Connective tissue diseases (CTDs) are one of the important causes of ILD and may have lung involvement antedating their usual manifestations, making the diagnosis difficult. Interstitial pneumonia with autoimmune features (IPAFs) are ILDs having autoimmune features but not fulfilling the criteria for a definite CTD. A small minority of IPAF cases may progress to CTD–related ILD over a period. Usual interstitial pneumonia (UIP) and nonspecific interstitial pneumonia are common radiological and histopathological patterns associated with IPAF. DIP is a rare manifestation of IPAF. Patients with IPAF and a non-UIP pattern may benefit from immunomodulation. We present a rare case of DIP in a nonsmoker, who was initially labeled as idiopathic ILD but eventually evolved into IPAF and exhibited a good response to immunosuppressive treatment. |
| format | Article |
| id | doaj-art-8f068348e99f4f41b4a792f147754e6d |
| institution | Kabale University |
| issn | 2320-8775 |
| language | English |
| publishDate | 2023-12-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | The Journal of Association of Chest Physicians |
| spelling | doaj-art-8f068348e99f4f41b4a792f147754e6d2025-01-20T07:27:36ZengWolters Kluwer Medknow PublicationsThe Journal of Association of Chest Physicians2320-87752023-12-0111423624010.4103/jacp.jacp_39_23Desquamative interstitial pneumonia: If there is smoke there is fireAmit PanjwaniHusain KadhemSaadeya Naji AbdulkarimUmesh NabarDesquamative interstitial pneumonia (DIP) is a rare type of idiopathic interstitial lung disease (ILD) predominantly seen in smokers. Connective tissue diseases (CTDs) are one of the important causes of ILD and may have lung involvement antedating their usual manifestations, making the diagnosis difficult. Interstitial pneumonia with autoimmune features (IPAFs) are ILDs having autoimmune features but not fulfilling the criteria for a definite CTD. A small minority of IPAF cases may progress to CTD–related ILD over a period. Usual interstitial pneumonia (UIP) and nonspecific interstitial pneumonia are common radiological and histopathological patterns associated with IPAF. DIP is a rare manifestation of IPAF. Patients with IPAF and a non-UIP pattern may benefit from immunomodulation. We present a rare case of DIP in a nonsmoker, who was initially labeled as idiopathic ILD but eventually evolved into IPAF and exhibited a good response to immunosuppressive treatment.https://journals.lww.com/10.4103/jacp.jacp_39_23desquamative interstitial pneumonianonsmokerinterstitial pneumonia with autoimmune featuressteroids |
| spellingShingle | Amit Panjwani Husain Kadhem Saadeya Naji Abdulkarim Umesh Nabar Desquamative interstitial pneumonia: If there is smoke there is fire The Journal of Association of Chest Physicians desquamative interstitial pneumonia nonsmoker interstitial pneumonia with autoimmune features steroids |
| title | Desquamative interstitial pneumonia: If there is smoke there is fire |
| title_full | Desquamative interstitial pneumonia: If there is smoke there is fire |
| title_fullStr | Desquamative interstitial pneumonia: If there is smoke there is fire |
| title_full_unstemmed | Desquamative interstitial pneumonia: If there is smoke there is fire |
| title_short | Desquamative interstitial pneumonia: If there is smoke there is fire |
| title_sort | desquamative interstitial pneumonia if there is smoke there is fire |
| topic | desquamative interstitial pneumonia nonsmoker interstitial pneumonia with autoimmune features steroids |
| url | https://journals.lww.com/10.4103/jacp.jacp_39_23 |
| work_keys_str_mv | AT amitpanjwani desquamativeinterstitialpneumoniaifthereissmokethereisfire AT husainkadhem desquamativeinterstitialpneumoniaifthereissmokethereisfire AT saadeyanajiabdulkarim desquamativeinterstitialpneumoniaifthereissmokethereisfire AT umeshnabar desquamativeinterstitialpneumoniaifthereissmokethereisfire |