Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis
The most detectable form of pulmonary fibrosis in MPA (microscopic polyangiitis) is UIP (usual interstitial pneumonia), occurring in 48 % of MPA patients with pulmonary fibrosis. In some cases, ILD (interstitial lung disease) is the initial clinical manifestation of MPA (22 % of cases). Here, we des...
Saved in:
| Main Author: | |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2024-01-01
|
| Series: | Respiratory Medicine Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S221300712400145X |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1850244844199346176 |
|---|---|
| author | Brittany Duchene |
| author_facet | Brittany Duchene |
| author_sort | Brittany Duchene |
| collection | DOAJ |
| description | The most detectable form of pulmonary fibrosis in MPA (microscopic polyangiitis) is UIP (usual interstitial pneumonia), occurring in 48 % of MPA patients with pulmonary fibrosis. In some cases, ILD (interstitial lung disease) is the initial clinical manifestation of MPA (22 % of cases). Here, we describe a patient diagnosed with IPF (idiopathic pulmonary fibrosis) who later developed pulmonary infiltrates on CT and hemoptysis, found to have diffuse alveolar hemorrhage on bronchoscopy and ultimately was diagnosed with MPA. There are no guidelines recommending routine screening of vasculitis in cases of suspected IPF, which may result in more misdiagnoses of vasculitides. |
| format | Article |
| id | doaj-art-8b00a0ca288646c8a6e0736d3b6a1533 |
| institution | OA Journals |
| issn | 2213-0071 |
| language | English |
| publishDate | 2024-01-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Respiratory Medicine Case Reports |
| spelling | doaj-art-8b00a0ca288646c8a6e0736d3b6a15332025-08-20T01:59:38ZengElsevierRespiratory Medicine Case Reports2213-00712024-01-015210212210.1016/j.rmcr.2024.102122Microscopic polyangiitis presenting as idiopathic pulmonary fibrosisBrittany Duchene0Northeastern Vermont Regional Hospital, 1315 Hospital Drive, St. Johnsbury, VT, 05819, USAThe most detectable form of pulmonary fibrosis in MPA (microscopic polyangiitis) is UIP (usual interstitial pneumonia), occurring in 48 % of MPA patients with pulmonary fibrosis. In some cases, ILD (interstitial lung disease) is the initial clinical manifestation of MPA (22 % of cases). Here, we describe a patient diagnosed with IPF (idiopathic pulmonary fibrosis) who later developed pulmonary infiltrates on CT and hemoptysis, found to have diffuse alveolar hemorrhage on bronchoscopy and ultimately was diagnosed with MPA. There are no guidelines recommending routine screening of vasculitis in cases of suspected IPF, which may result in more misdiagnoses of vasculitides.http://www.sciencedirect.com/science/article/pii/S221300712400145XMicroscopic polyangiitisIdiopathic pulmonary fibrosisInterstitial lung diseaseANCA-Associated vasculitisDiffuse alveolar hemorrhage |
| spellingShingle | Brittany Duchene Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis Respiratory Medicine Case Reports Microscopic polyangiitis Idiopathic pulmonary fibrosis Interstitial lung disease ANCA-Associated vasculitis Diffuse alveolar hemorrhage |
| title | Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis |
| title_full | Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis |
| title_fullStr | Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis |
| title_full_unstemmed | Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis |
| title_short | Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis |
| title_sort | microscopic polyangiitis presenting as idiopathic pulmonary fibrosis |
| topic | Microscopic polyangiitis Idiopathic pulmonary fibrosis Interstitial lung disease ANCA-Associated vasculitis Diffuse alveolar hemorrhage |
| url | http://www.sciencedirect.com/science/article/pii/S221300712400145X |
| work_keys_str_mv | AT brittanyduchene microscopicpolyangiitispresentingasidiopathicpulmonaryfibrosis |