Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapies

Abstract Objective Neuromodulation for pediatric refractory epilepsy (PRE) is preferred when the seizure onset zone is not amenable to surgical resection, due to multifocal onset or involvement of eloquent cortex. Given its rapidly evolving landscape, we describe our institutional experience with ne...

Full description

Saved in:
Bibliographic Details
Main Authors: Rohin Singh, Megan M. J. Bauman, Karimul Islam, Panagiotis Kerezoudis, Sanjeet S. Grewal, Jonathon J. Parker, Jamie J. Van Gompel, Kai J. Miller, Brian N. Lundstrom, Keith Starnes
Format: Article
Language:English
Published: Wiley 2025-06-01
Series:Epilepsia Open
Subjects:
Online Access:https://doi.org/10.1002/epi4.70006
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850223383003791360
author Rohin Singh
Megan M. J. Bauman
Karimul Islam
Panagiotis Kerezoudis
Sanjeet S. Grewal
Jonathon J. Parker
Jamie J. Van Gompel
Kai J. Miller
Brian N. Lundstrom
Keith Starnes
author_facet Rohin Singh
Megan M. J. Bauman
Karimul Islam
Panagiotis Kerezoudis
Sanjeet S. Grewal
Jonathon J. Parker
Jamie J. Van Gompel
Kai J. Miller
Brian N. Lundstrom
Keith Starnes
author_sort Rohin Singh
collection DOAJ
description Abstract Objective Neuromodulation for pediatric refractory epilepsy (PRE) is preferred when the seizure onset zone is not amenable to surgical resection, due to multifocal onset or involvement of eloquent cortex. Given its rapidly evolving landscape, we describe our institutional experience with neurostimulation therapies including deep brain stimulation (DBS) of the anterior nucleus (DBS‐ANT), the centromedian nucleus (DBS‐CM), responsive neurostimulation (RNS), and chronic subthreshold stimulation (CSS) to treat PRE. Methods A retrospective chart review was conducted to identify pediatric patients (≤18 years of age) who presented to our institution with PRE. Patients were included who had at least 1 year of follow‐up after neurostimulation was started. Patients with ≥50% seizure frequency reduction at last follow‐up compared to baseline were classified as responders. Results A total of 35 patients (21 females) were included in the series. Nine patients underwent DBS‐ANT, 9 underwent DBS‐CM (+ ANT in 7 patients), 5 underwent RNS, and 12 underwent CSS. The median age at seizure onset and surgery was 8 and 16 years, respectively. Structural lesions were the most common etiology of epilepsy (54%). Eighteen patients had prior interventions and 13 received invasive EEG. Post‐operative complications following neurostimulation implantation were noted in three patients (9%). However, no permanent deficits were noted. Median follow‐up time was 46 months (range 13–162 months). Twenty‐three patients (59%) were responders (3/9 DBS‐ANT; 7/9 DBS‐CM; 4/5 RNS; 9/12 CSS). Further, median seizure reduction was 25% (DBS‐ANT), 89% (DBS‐CM), 87% (RNS), and 88% (CSS) across the cohort. Six patients (17%) had improved subjective neurocognitive outcomes while the other 29 had stable neurocognitive outcomes. Significance DBS, RNS, and CSS are safe and effective options for PRE. An understanding of treatment approaches can optimize results by tailoring therapy to individual patients. Plain Language Summary This study investigates the use of various neurostimulation therapies for treating pediatric refractory epilepsy (PRE) including deep brain stimulation (DBS), responsive neurostimulation (RNS), and chronic subthreshold stimulation (CSS). Overall, neuromodulation was found to be effective in reducing seizures in most patients, with 59% of patients showing at least a 50% reduction in seizure frequency. Additionally, the treatments were generally safe, with few complications and no instances of permanent deficits.
format Article
id doaj-art-88dff9ec43d6455d9e3ad236a79122ea
institution OA Journals
issn 2470-9239
language English
publishDate 2025-06-01
publisher Wiley
record_format Article
series Epilepsia Open
spelling doaj-art-88dff9ec43d6455d9e3ad236a79122ea2025-08-20T02:05:59ZengWileyEpilepsia Open2470-92392025-06-0110369470410.1002/epi4.70006Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapiesRohin Singh0Megan M. J. Bauman1Karimul Islam2Panagiotis Kerezoudis3Sanjeet S. Grewal4Jonathon J. Parker5Jamie J. Van Gompel6Kai J. Miller7Brian N. Lundstrom8Keith Starnes9Department of Neurosurgery University of Rochester Rochester New York USADepartment of Neurosurgery Mayo Clinic Rochester Minnesota USADepartment of Neurology Mayo Clinic Rochester Minnesota USADepartment of Neurosurgery Mayo Clinic Rochester Minnesota USADepartment of Neurosurgery Mayo Clinic Jacksonville Florida USADepartment of Neurosurgery Mayo Clinic Phoenix Arizona USADepartment of Neurosurgery Mayo Clinic Rochester Minnesota USADepartment of Neurosurgery Mayo Clinic Rochester Minnesota USADepartment of Neurology Mayo Clinic Rochester Minnesota USADepartment of Neurology Mayo Clinic Rochester Minnesota USAAbstract Objective Neuromodulation for pediatric refractory epilepsy (PRE) is preferred when the seizure onset zone is not amenable to surgical resection, due to multifocal onset or involvement of eloquent cortex. Given its rapidly evolving landscape, we describe our institutional experience with neurostimulation therapies including deep brain stimulation (DBS) of the anterior nucleus (DBS‐ANT), the centromedian nucleus (DBS‐CM), responsive neurostimulation (RNS), and chronic subthreshold stimulation (CSS) to treat PRE. Methods A retrospective chart review was conducted to identify pediatric patients (≤18 years of age) who presented to our institution with PRE. Patients were included who had at least 1 year of follow‐up after neurostimulation was started. Patients with ≥50% seizure frequency reduction at last follow‐up compared to baseline were classified as responders. Results A total of 35 patients (21 females) were included in the series. Nine patients underwent DBS‐ANT, 9 underwent DBS‐CM (+ ANT in 7 patients), 5 underwent RNS, and 12 underwent CSS. The median age at seizure onset and surgery was 8 and 16 years, respectively. Structural lesions were the most common etiology of epilepsy (54%). Eighteen patients had prior interventions and 13 received invasive EEG. Post‐operative complications following neurostimulation implantation were noted in three patients (9%). However, no permanent deficits were noted. Median follow‐up time was 46 months (range 13–162 months). Twenty‐three patients (59%) were responders (3/9 DBS‐ANT; 7/9 DBS‐CM; 4/5 RNS; 9/12 CSS). Further, median seizure reduction was 25% (DBS‐ANT), 89% (DBS‐CM), 87% (RNS), and 88% (CSS) across the cohort. Six patients (17%) had improved subjective neurocognitive outcomes while the other 29 had stable neurocognitive outcomes. Significance DBS, RNS, and CSS are safe and effective options for PRE. An understanding of treatment approaches can optimize results by tailoring therapy to individual patients. Plain Language Summary This study investigates the use of various neurostimulation therapies for treating pediatric refractory epilepsy (PRE) including deep brain stimulation (DBS), responsive neurostimulation (RNS), and chronic subthreshold stimulation (CSS). Overall, neuromodulation was found to be effective in reducing seizures in most patients, with 59% of patients showing at least a 50% reduction in seizure frequency. Additionally, the treatments were generally safe, with few complications and no instances of permanent deficits.https://doi.org/10.1002/epi4.70006epilepsy neurostimulationneuromodulationpediatric DBSpediatric epilepsypediatric neurostimulationpediatric RNS
spellingShingle Rohin Singh
Megan M. J. Bauman
Karimul Islam
Panagiotis Kerezoudis
Sanjeet S. Grewal
Jonathon J. Parker
Jamie J. Van Gompel
Kai J. Miller
Brian N. Lundstrom
Keith Starnes
Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapies
Epilepsia Open
epilepsy neurostimulation
neuromodulation
pediatric DBS
pediatric epilepsy
pediatric neurostimulation
pediatric RNS
title Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapies
title_full Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapies
title_fullStr Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapies
title_full_unstemmed Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapies
title_short Intracranial stimulation for pediatric refractory epilepsy: A single institutional experience using evolving therapies
title_sort intracranial stimulation for pediatric refractory epilepsy a single institutional experience using evolving therapies
topic epilepsy neurostimulation
neuromodulation
pediatric DBS
pediatric epilepsy
pediatric neurostimulation
pediatric RNS
url https://doi.org/10.1002/epi4.70006
work_keys_str_mv AT rohinsingh intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT meganmjbauman intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT karimulislam intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT panagiotiskerezoudis intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT sanjeetsgrewal intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT jonathonjparker intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT jamiejvangompel intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT kaijmiller intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT briannlundstrom intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies
AT keithstarnes intracranialstimulationforpediatricrefractoryepilepsyasingleinstitutionalexperienceusingevolvingtherapies