An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome
Mounier-Kuhn syndrome is a rare clinical and radiologic condition. It is characterized by tracheal and bronchial dilation. Diagnosis is made by computed tomography and bronchoscopy. An 81-year-old man presenting with an acute chest pain was referred to the pulmonology department. His chest computed...
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| Format: | Article |
| Language: | English |
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Wiley
2019-01-01
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| Series: | Case Reports in Pulmonology |
| Online Access: | http://dx.doi.org/10.1155/2019/5359309 |
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| author | Salim Naciri Rachida Zahraoui Mouna Soualhi Jamal-Eddine Bourkadi |
| author_facet | Salim Naciri Rachida Zahraoui Mouna Soualhi Jamal-Eddine Bourkadi |
| author_sort | Salim Naciri |
| collection | DOAJ |
| description | Mounier-Kuhn syndrome is a rare clinical and radiologic condition. It is characterized by tracheal and bronchial dilation. Diagnosis is made by computed tomography and bronchoscopy. An 81-year-old man presenting with an acute chest pain was referred to the pulmonology department. His chest computed tomographic scan showed a tracheobronchomegaly with an increase in the diameter of both the trachea and right and left main bronchi, associated with pneumomediastinum and fibrosis. Fiberoptic bronchoscopy revealed enlarged trachea and both main bronchi. These findings are consistent with a diagnosis of Mounier-Kuhn syndrome. Besides considering this long-neglected “orphan disease” when diagnosing spontaneous pneumomediastinum, clinicians should also be aware of an underlying Mounier-Kuhn syndrome in patients with recurrent respiratory infections, in order to avoid complications associated with the disease. |
| format | Article |
| id | doaj-art-8770b5ad17e640adab4b783988aca8b6 |
| institution | Kabale University |
| issn | 2090-6846 2090-6854 |
| language | English |
| publishDate | 2019-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pulmonology |
| spelling | doaj-art-8770b5ad17e640adab4b783988aca8b62025-02-03T07:24:47ZengWileyCase Reports in Pulmonology2090-68462090-68542019-01-01201910.1155/2019/53593095359309An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn SyndromeSalim Naciri0Rachida Zahraoui1Mouna Soualhi2Jamal-Eddine Bourkadi3Moulay Youssef Hospital, Pulmonary Unit, University Mohammed V of Rabat, MoroccoMoulay Youssef Hospital, Pulmonary Unit, University Mohammed V of Rabat, MoroccoMoulay Youssef Hospital, Pulmonary Unit, University Mohammed V of Rabat, MoroccoMoulay Youssef Hospital, Pulmonary Unit, University Mohammed V of Rabat, MoroccoMounier-Kuhn syndrome is a rare clinical and radiologic condition. It is characterized by tracheal and bronchial dilation. Diagnosis is made by computed tomography and bronchoscopy. An 81-year-old man presenting with an acute chest pain was referred to the pulmonology department. His chest computed tomographic scan showed a tracheobronchomegaly with an increase in the diameter of both the trachea and right and left main bronchi, associated with pneumomediastinum and fibrosis. Fiberoptic bronchoscopy revealed enlarged trachea and both main bronchi. These findings are consistent with a diagnosis of Mounier-Kuhn syndrome. Besides considering this long-neglected “orphan disease” when diagnosing spontaneous pneumomediastinum, clinicians should also be aware of an underlying Mounier-Kuhn syndrome in patients with recurrent respiratory infections, in order to avoid complications associated with the disease.http://dx.doi.org/10.1155/2019/5359309 |
| spellingShingle | Salim Naciri Rachida Zahraoui Mouna Soualhi Jamal-Eddine Bourkadi An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome Case Reports in Pulmonology |
| title | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
| title_full | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
| title_fullStr | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
| title_full_unstemmed | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
| title_short | An Unusual Cause of Spontaneous Pneumomediastinum: The Mounier-Kuhn Syndrome |
| title_sort | unusual cause of spontaneous pneumomediastinum the mounier kuhn syndrome |
| url | http://dx.doi.org/10.1155/2019/5359309 |
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