Eltrombopag in Good’s Syndrome

Good’s syndrome is a rare acquired immunodeficiency associated with thymoma. Eltrombopag is a thrombopoietin receptor agonist and has been shown to be a valuable supplement to the treatment of several types of refractory cytopenias. In this paper, we describe a male patient suffering from Good’s syn...

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Main Authors: Håvard Anton Kristiansen, Signe Spetalen, Yngvar Fløisand, Dag Heldal
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Hematology
Online Access:http://dx.doi.org/10.1155/2014/172139
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author Håvard Anton Kristiansen
Signe Spetalen
Yngvar Fløisand
Dag Heldal
author_facet Håvard Anton Kristiansen
Signe Spetalen
Yngvar Fløisand
Dag Heldal
author_sort Håvard Anton Kristiansen
collection DOAJ
description Good’s syndrome is a rare acquired immunodeficiency associated with thymoma. Eltrombopag is a thrombopoietin receptor agonist and has been shown to be a valuable supplement to the treatment of several types of refractory cytopenias. In this paper, we describe a male patient suffering from Good’s syndrome with immune-mediated T-cell driven pancytopenia and absence of megakaryopoiesis. He was successfully treated with eltrombopag resulting in a multilineage clinical response.
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institution Kabale University
issn 2090-6560
2090-6579
language English
publishDate 2014-01-01
publisher Wiley
record_format Article
series Case Reports in Hematology
spelling doaj-art-84bdb70b32f24206b0293cf8548ba8ed2025-02-03T06:00:44ZengWileyCase Reports in Hematology2090-65602090-65792014-01-01201410.1155/2014/172139172139Eltrombopag in Good’s SyndromeHåvard Anton Kristiansen0Signe Spetalen1Yngvar Fløisand2Dag Heldal3Department of Internal Medicine, Innlandet Hospital Trust, 2629 Lillehammer, NorwayDepartment of Pathology, Oslo University Hospital, 0424 Oslo, NorwayDepartment of Hematology, Oslo University Hospital, Rikshospitalet, P.O. Box 4950, Nydalen, 0424 Oslo, NorwayDepartment of Hematology, Oslo University Hospital, Rikshospitalet, P.O. Box 4950, Nydalen, 0424 Oslo, NorwayGood’s syndrome is a rare acquired immunodeficiency associated with thymoma. Eltrombopag is a thrombopoietin receptor agonist and has been shown to be a valuable supplement to the treatment of several types of refractory cytopenias. In this paper, we describe a male patient suffering from Good’s syndrome with immune-mediated T-cell driven pancytopenia and absence of megakaryopoiesis. He was successfully treated with eltrombopag resulting in a multilineage clinical response.http://dx.doi.org/10.1155/2014/172139
spellingShingle Håvard Anton Kristiansen
Signe Spetalen
Yngvar Fløisand
Dag Heldal
Eltrombopag in Good’s Syndrome
Case Reports in Hematology
title Eltrombopag in Good’s Syndrome
title_full Eltrombopag in Good’s Syndrome
title_fullStr Eltrombopag in Good’s Syndrome
title_full_unstemmed Eltrombopag in Good’s Syndrome
title_short Eltrombopag in Good’s Syndrome
title_sort eltrombopag in good s syndrome
url http://dx.doi.org/10.1155/2014/172139
work_keys_str_mv AT havardantonkristiansen eltrombopagingoodssyndrome
AT signespetalen eltrombopagingoodssyndrome
AT yngvarfløisand eltrombopagingoodssyndrome
AT dagheldal eltrombopagingoodssyndrome