Eltrombopag in Good’s Syndrome
Good’s syndrome is a rare acquired immunodeficiency associated with thymoma. Eltrombopag is a thrombopoietin receptor agonist and has been shown to be a valuable supplement to the treatment of several types of refractory cytopenias. In this paper, we describe a male patient suffering from Good’s syn...
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Format: | Article |
Language: | English |
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Wiley
2014-01-01
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Series: | Case Reports in Hematology |
Online Access: | http://dx.doi.org/10.1155/2014/172139 |
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author | Håvard Anton Kristiansen Signe Spetalen Yngvar Fløisand Dag Heldal |
author_facet | Håvard Anton Kristiansen Signe Spetalen Yngvar Fløisand Dag Heldal |
author_sort | Håvard Anton Kristiansen |
collection | DOAJ |
description | Good’s syndrome is a rare acquired immunodeficiency associated with thymoma. Eltrombopag is a thrombopoietin receptor agonist and has been shown to be a valuable supplement to the treatment of several types of refractory cytopenias. In this paper, we describe a male patient suffering from Good’s syndrome with immune-mediated T-cell driven pancytopenia and absence of megakaryopoiesis. He was successfully treated with eltrombopag resulting in a multilineage clinical response. |
format | Article |
id | doaj-art-84bdb70b32f24206b0293cf8548ba8ed |
institution | Kabale University |
issn | 2090-6560 2090-6579 |
language | English |
publishDate | 2014-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Hematology |
spelling | doaj-art-84bdb70b32f24206b0293cf8548ba8ed2025-02-03T06:00:44ZengWileyCase Reports in Hematology2090-65602090-65792014-01-01201410.1155/2014/172139172139Eltrombopag in Good’s SyndromeHåvard Anton Kristiansen0Signe Spetalen1Yngvar Fløisand2Dag Heldal3Department of Internal Medicine, Innlandet Hospital Trust, 2629 Lillehammer, NorwayDepartment of Pathology, Oslo University Hospital, 0424 Oslo, NorwayDepartment of Hematology, Oslo University Hospital, Rikshospitalet, P.O. Box 4950, Nydalen, 0424 Oslo, NorwayDepartment of Hematology, Oslo University Hospital, Rikshospitalet, P.O. Box 4950, Nydalen, 0424 Oslo, NorwayGood’s syndrome is a rare acquired immunodeficiency associated with thymoma. Eltrombopag is a thrombopoietin receptor agonist and has been shown to be a valuable supplement to the treatment of several types of refractory cytopenias. In this paper, we describe a male patient suffering from Good’s syndrome with immune-mediated T-cell driven pancytopenia and absence of megakaryopoiesis. He was successfully treated with eltrombopag resulting in a multilineage clinical response.http://dx.doi.org/10.1155/2014/172139 |
spellingShingle | Håvard Anton Kristiansen Signe Spetalen Yngvar Fløisand Dag Heldal Eltrombopag in Good’s Syndrome Case Reports in Hematology |
title | Eltrombopag in Good’s Syndrome |
title_full | Eltrombopag in Good’s Syndrome |
title_fullStr | Eltrombopag in Good’s Syndrome |
title_full_unstemmed | Eltrombopag in Good’s Syndrome |
title_short | Eltrombopag in Good’s Syndrome |
title_sort | eltrombopag in good s syndrome |
url | http://dx.doi.org/10.1155/2014/172139 |
work_keys_str_mv | AT havardantonkristiansen eltrombopagingoodssyndrome AT signespetalen eltrombopagingoodssyndrome AT yngvarfløisand eltrombopagingoodssyndrome AT dagheldal eltrombopagingoodssyndrome |