Malignant Perivascular Epithelioid Cell Tumor of the Esophagus

Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was prese...

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Main Authors: Matteo Fassan, Mauro Cassaro, Massimo Vecchiato, Roberto Clemente, Gianmaria Pennelli, Stefano Merigliano, Giuseppe Altavilla
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Pathology
Online Access:http://dx.doi.org/10.1155/2012/438505
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author Matteo Fassan
Mauro Cassaro
Massimo Vecchiato
Roberto Clemente
Gianmaria Pennelli
Stefano Merigliano
Giuseppe Altavilla
author_facet Matteo Fassan
Mauro Cassaro
Massimo Vecchiato
Roberto Clemente
Gianmaria Pennelli
Stefano Merigliano
Giuseppe Altavilla
author_sort Matteo Fassan
collection DOAJ
description Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are exceptional findings, clinicians should not exclude this class of tumors in the diagnostic investigation of a bulky lesion of the esophageal wall.
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institution Kabale University
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publishDate 2012-01-01
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series Case Reports in Pathology
spelling doaj-art-808bcd0d151a47b2a236b6f87c272e5e2025-02-03T07:25:45ZengWileyCase Reports in Pathology2090-67812090-679X2012-01-01201210.1155/2012/438505438505Malignant Perivascular Epithelioid Cell Tumor of the EsophagusMatteo Fassan0Mauro Cassaro1Massimo Vecchiato2Roberto Clemente3Gianmaria Pennelli4Stefano Merigliano5Giuseppe Altavilla6Surgical Pathology and Cytopathology Unit, Department of Medicine (DIMED), University of Padua, 35121 Padua, ItalySurgical Pathology and Cytopathology Unit, Department of Medicine (DIMED), University of Padua, 35121 Padua, ItalySurgery Unit, Department of Surgery, Oncology and Gastroenterology (DiSCOG), University of Padua, 35121 Padua, ItalySurgical Pathology and Cytopathology Unit, Department of Medicine (DIMED), University of Padua, 35121 Padua, ItalySurgical Pathology and Cytopathology Unit, Department of Medicine (DIMED), University of Padua, 35121 Padua, ItalySurgery Unit, Department of Surgery, Oncology and Gastroenterology (DiSCOG), University of Padua, 35121 Padua, ItalySurgical Pathology and Cytopathology Unit, Department of Medicine (DIMED), University of Padua, 35121 Padua, ItalyMalignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are exceptional findings, clinicians should not exclude this class of tumors in the diagnostic investigation of a bulky lesion of the esophageal wall.http://dx.doi.org/10.1155/2012/438505
spellingShingle Matteo Fassan
Mauro Cassaro
Massimo Vecchiato
Roberto Clemente
Gianmaria Pennelli
Stefano Merigliano
Giuseppe Altavilla
Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
Case Reports in Pathology
title Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_full Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_fullStr Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_full_unstemmed Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_short Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_sort malignant perivascular epithelioid cell tumor of the esophagus
url http://dx.doi.org/10.1155/2012/438505
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