Olmsted Syndrome
Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyper...
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Format: | Article |
Language: | English |
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Wiley
2012-01-01
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Series: | Case Reports in Dermatological Medicine |
Online Access: | http://dx.doi.org/10.1155/2012/927305 |
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author | Renata Elise Tonoli Damiê De Villa Renata Hübner Frainer Luana Pizzarro Meneghello Nelson Ricachnevsky Maurício de Quadros |
author_facet | Renata Elise Tonoli Damiê De Villa Renata Hübner Frainer Luana Pizzarro Meneghello Nelson Ricachnevsky Maurício de Quadros |
author_sort | Renata Elise Tonoli |
collection | DOAJ |
description | Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyperkeratotic plaques around the body orifices. It starts in the neonatal period or in childhood. The disease has a slow but progressive and extremely disabling course. Treatment of Olmsted syndrome is often based on topical therapy with retinoic acid, corticosteroid, emollients, and keratolytics. The present paper describes a case of Olmsted syndrome and its treatment. |
format | Article |
id | doaj-art-7ec97e7999ed485694b776374883af0f |
institution | Kabale University |
issn | 2090-6463 2090-6471 |
language | English |
publishDate | 2012-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Dermatological Medicine |
spelling | doaj-art-7ec97e7999ed485694b776374883af0f2025-02-03T01:09:44ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712012-01-01201210.1155/2012/927305927305Olmsted SyndromeRenata Elise Tonoli0Damiê De Villa1Renata Hübner Frainer2Luana Pizzarro Meneghello3Nelson Ricachnevsky4Maurício de Quadros5Department of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilPediatric Dermatology Service, Department of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilOlmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyperkeratotic plaques around the body orifices. It starts in the neonatal period or in childhood. The disease has a slow but progressive and extremely disabling course. Treatment of Olmsted syndrome is often based on topical therapy with retinoic acid, corticosteroid, emollients, and keratolytics. The present paper describes a case of Olmsted syndrome and its treatment.http://dx.doi.org/10.1155/2012/927305 |
spellingShingle | Renata Elise Tonoli Damiê De Villa Renata Hübner Frainer Luana Pizzarro Meneghello Nelson Ricachnevsky Maurício de Quadros Olmsted Syndrome Case Reports in Dermatological Medicine |
title | Olmsted Syndrome |
title_full | Olmsted Syndrome |
title_fullStr | Olmsted Syndrome |
title_full_unstemmed | Olmsted Syndrome |
title_short | Olmsted Syndrome |
title_sort | olmsted syndrome |
url | http://dx.doi.org/10.1155/2012/927305 |
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