Olmsted Syndrome

Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyper...

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Main Authors: Renata Elise Tonoli, Damiê De Villa, Renata Hübner Frainer, Luana Pizzarro Meneghello, Nelson Ricachnevsky, Maurício de Quadros
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Dermatological Medicine
Online Access:http://dx.doi.org/10.1155/2012/927305
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author Renata Elise Tonoli
Damiê De Villa
Renata Hübner Frainer
Luana Pizzarro Meneghello
Nelson Ricachnevsky
Maurício de Quadros
author_facet Renata Elise Tonoli
Damiê De Villa
Renata Hübner Frainer
Luana Pizzarro Meneghello
Nelson Ricachnevsky
Maurício de Quadros
author_sort Renata Elise Tonoli
collection DOAJ
description Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyperkeratotic plaques around the body orifices. It starts in the neonatal period or in childhood. The disease has a slow but progressive and extremely disabling course. Treatment of Olmsted syndrome is often based on topical therapy with retinoic acid, corticosteroid, emollients, and keratolytics. The present paper describes a case of Olmsted syndrome and its treatment.
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institution Kabale University
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publishDate 2012-01-01
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series Case Reports in Dermatological Medicine
spelling doaj-art-7ec97e7999ed485694b776374883af0f2025-02-03T01:09:44ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712012-01-01201210.1155/2012/927305927305Olmsted SyndromeRenata Elise Tonoli0Damiê De Villa1Renata Hübner Frainer2Luana Pizzarro Meneghello3Nelson Ricachnevsky4Maurício de Quadros5Department of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilDepartment of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilPediatric Dermatology Service, Department of Dermatology, Brazilian Society of Dermatology, Santo Antônio Hospital, Santa Casa de Midericórdia de Porto Alegre, Porto Alegre, RS, BrazilOlmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyperkeratotic plaques around the body orifices. It starts in the neonatal period or in childhood. The disease has a slow but progressive and extremely disabling course. Treatment of Olmsted syndrome is often based on topical therapy with retinoic acid, corticosteroid, emollients, and keratolytics. The present paper describes a case of Olmsted syndrome and its treatment.http://dx.doi.org/10.1155/2012/927305
spellingShingle Renata Elise Tonoli
Damiê De Villa
Renata Hübner Frainer
Luana Pizzarro Meneghello
Nelson Ricachnevsky
Maurício de Quadros
Olmsted Syndrome
Case Reports in Dermatological Medicine
title Olmsted Syndrome
title_full Olmsted Syndrome
title_fullStr Olmsted Syndrome
title_full_unstemmed Olmsted Syndrome
title_short Olmsted Syndrome
title_sort olmsted syndrome
url http://dx.doi.org/10.1155/2012/927305
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AT nelsonricachnevsky olmstedsyndrome
AT mauriciodequadros olmstedsyndrome