Lung Transplantation in a Patient with COPA Syndrome
COPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral...
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| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wiley
2020-01-01
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| Series: | Case Reports in Transplantation |
| Online Access: | http://dx.doi.org/10.1155/2020/3624795 |
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| _version_ | 1832547713508442112 |
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| author | Jorge M. Mallea Anna Kornafeld Andras Khoor David B. Erasmus |
| author_facet | Jorge M. Mallea Anna Kornafeld Andras Khoor David B. Erasmus |
| author_sort | Jorge M. Mallea |
| collection | DOAJ |
| description | COPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral lung transplant for COPA syndrome. At 15 months posttransplant, her pulmonary function is stable with no episodes of acute cellular- or antibody-mediated rejection and no evidence of disease recurrence. |
| format | Article |
| id | doaj-art-7e6963854a1a4cdcb2f187269353bead |
| institution | Kabale University |
| issn | 2090-6943 2090-6951 |
| language | English |
| publishDate | 2020-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Transplantation |
| spelling | doaj-art-7e6963854a1a4cdcb2f187269353bead2025-02-03T06:43:40ZengWileyCase Reports in Transplantation2090-69432090-69512020-01-01202010.1155/2020/36247953624795Lung Transplantation in a Patient with COPA SyndromeJorge M. Mallea0Anna Kornafeld1Andras Khoor2David B. Erasmus3Mayo Clinic, 4500 San Pablo Rd S, Jacksonville, FL 32224, USAMayo Clinic, 4500 San Pablo Rd S, Jacksonville, FL 32224, USAMayo Clinic, 4500 San Pablo Rd S, Jacksonville, FL 32224, USAMayo Clinic, 4500 San Pablo Rd S, Jacksonville, FL 32224, USACOPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral lung transplant for COPA syndrome. At 15 months posttransplant, her pulmonary function is stable with no episodes of acute cellular- or antibody-mediated rejection and no evidence of disease recurrence.http://dx.doi.org/10.1155/2020/3624795 |
| spellingShingle | Jorge M. Mallea Anna Kornafeld Andras Khoor David B. Erasmus Lung Transplantation in a Patient with COPA Syndrome Case Reports in Transplantation |
| title | Lung Transplantation in a Patient with COPA Syndrome |
| title_full | Lung Transplantation in a Patient with COPA Syndrome |
| title_fullStr | Lung Transplantation in a Patient with COPA Syndrome |
| title_full_unstemmed | Lung Transplantation in a Patient with COPA Syndrome |
| title_short | Lung Transplantation in a Patient with COPA Syndrome |
| title_sort | lung transplantation in a patient with copa syndrome |
| url | http://dx.doi.org/10.1155/2020/3624795 |
| work_keys_str_mv | AT jorgemmallea lungtransplantationinapatientwithcopasyndrome AT annakornafeld lungtransplantationinapatientwithcopasyndrome AT andraskhoor lungtransplantationinapatientwithcopasyndrome AT davidberasmus lungtransplantationinapatientwithcopasyndrome |