Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review
Severe pulmonary artery hypertension (PAH) is a rare initial presentation of systemic lupus erythematosus (SLE). SLE associated with PAH carries worse prognosis that isolated SLE. However, there has been improvement in mortality of the patients in the recent years owing to newer treatment options av...
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| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Wiley
2020-01-01
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| Series: | Case Reports in Rheumatology |
| Online Access: | http://dx.doi.org/10.1155/2020/6014572 |
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| _version_ | 1832560675405168640 |
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| author | Rabia Kiani Muhammad Danial Siddiqui Hamza Tantoush |
| author_facet | Rabia Kiani Muhammad Danial Siddiqui Hamza Tantoush |
| author_sort | Rabia Kiani |
| collection | DOAJ |
| description | Severe pulmonary artery hypertension (PAH) is a rare initial presentation of systemic lupus erythematosus (SLE). SLE associated with PAH carries worse prognosis that isolated SLE. However, there has been improvement in mortality of the patients in the recent years owing to newer treatment options available. Early recognition remains of prime importance. We present here a case of young female who presented with severe pulmonary hypertension with right heart failure leading to cardiogenic shock and was found to have SLE. She was started on appropriate treatment; however, given the severity of her illness, the patient did not survive. This case highlights the importance of early recognition and prompt treatment of SLE-associated PAH, which might improve the survival rate in the patients. |
| format | Article |
| id | doaj-art-7ad2869a3f4f411681a6b6620b14def7 |
| institution | Kabale University |
| issn | 2090-6889 2090-6897 |
| language | English |
| publishDate | 2020-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Rheumatology |
| spelling | doaj-art-7ad2869a3f4f411681a6b6620b14def72025-02-03T01:27:04ZengWileyCase Reports in Rheumatology2090-68892090-68972020-01-01202010.1155/2020/60145726014572Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature ReviewRabia Kiani0Muhammad Danial Siddiqui1Hamza Tantoush2Department of Internal Medicine, University of South Dakota, Vermillion, SD, USADepartment of Internal Medicine, University of South Dakota, Vermillion, SD, USADepartment of Internal Medicine, University of South Dakota, Vermillion, SD, USASevere pulmonary artery hypertension (PAH) is a rare initial presentation of systemic lupus erythematosus (SLE). SLE associated with PAH carries worse prognosis that isolated SLE. However, there has been improvement in mortality of the patients in the recent years owing to newer treatment options available. Early recognition remains of prime importance. We present here a case of young female who presented with severe pulmonary hypertension with right heart failure leading to cardiogenic shock and was found to have SLE. She was started on appropriate treatment; however, given the severity of her illness, the patient did not survive. This case highlights the importance of early recognition and prompt treatment of SLE-associated PAH, which might improve the survival rate in the patients.http://dx.doi.org/10.1155/2020/6014572 |
| spellingShingle | Rabia Kiani Muhammad Danial Siddiqui Hamza Tantoush Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review Case Reports in Rheumatology |
| title | Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review |
| title_full | Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review |
| title_fullStr | Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review |
| title_full_unstemmed | Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review |
| title_short | Severe Pulmonary Hypertension as Initial Presentation of SLE: A Case Report and Literature Review |
| title_sort | severe pulmonary hypertension as initial presentation of sle a case report and literature review |
| url | http://dx.doi.org/10.1155/2020/6014572 |
| work_keys_str_mv | AT rabiakiani severepulmonaryhypertensionasinitialpresentationofsleacasereportandliteraturereview AT muhammaddanialsiddiqui severepulmonaryhypertensionasinitialpresentationofsleacasereportandliteraturereview AT hamzatantoush severepulmonaryhypertensionasinitialpresentationofsleacasereportandliteraturereview |