Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor

Introduction. Solitary fibrous tumor is a rare type of mesenchymal, spindle-cell tumor reported mostly in the pleura. Retroperitoneal occurrence is rare and histopathological diagnosis is challenging. Case Presentation. A 55-year-old woman with nonspecific abdominal pain was found to have a retroper...

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Main Authors: D. Myoteri, D. Dellaportas, C. Nastos, I. Gioti, G. Gkiokas, E. Carvounis, T. Theodosopoulos
Format: Article
Language:English
Published: Wiley 2017-01-01
Series:Case Reports in Oncological Medicine
Online Access:http://dx.doi.org/10.1155/2017/4634235
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author D. Myoteri
D. Dellaportas
C. Nastos
I. Gioti
G. Gkiokas
E. Carvounis
T. Theodosopoulos
author_facet D. Myoteri
D. Dellaportas
C. Nastos
I. Gioti
G. Gkiokas
E. Carvounis
T. Theodosopoulos
author_sort D. Myoteri
collection DOAJ
description Introduction. Solitary fibrous tumor is a rare type of mesenchymal, spindle-cell tumor reported mostly in the pleura. Retroperitoneal occurrence is rare and histopathological diagnosis is challenging. Case Presentation. A 55-year-old woman with nonspecific abdominal pain was found to have a retroperitoneal/pelvic mass adjacent to the upper rectum. The patient underwent surgical resection in clear margins of this pelvic tumor, entering the total mesenteric excision surgical plane. Final histopathology revealed a solitary fibrous tumor and the case is presented herein. Discussion. Solitary fibrous tumor in the retroperitoneum is rarely found in the literature and to the best of our knowledge less than a hundred cases are described so far. Histopathological diagnosis is mostly based on a “patternless pattern” on microscopic examination, which is a storiform arrangement of spindle cells combined with a “hemangiopericytoma-like appearance” and increased vascularity of the lesion. Surgery is the mainstay of treatment and recurrence rates are generally low.
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institution Kabale University
issn 2090-6706
2090-6714
language English
publishDate 2017-01-01
publisher Wiley
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series Case Reports in Oncological Medicine
spelling doaj-art-7a3c610f142f40c49785e9a537a023602025-02-03T01:22:28ZengWileyCase Reports in Oncological Medicine2090-67062090-67142017-01-01201710.1155/2017/46342354634235Retroperitoneal Solitary Fibrous Tumor: A “Patternless” TumorD. Myoteri0D. Dellaportas1C. Nastos2I. Gioti3G. Gkiokas4E. Carvounis5T. Theodosopoulos6Pathology Department, Aretaieion University Hospital, Medical School of Athens, Athens, Greece2nd Department of Surgery, Aretaieion University Hospital, Medical School of Athens, Athens, Greece2nd Department of Surgery, Aretaieion University Hospital, Medical School of Athens, Athens, GreecePathology Department, Aretaieion University Hospital, Medical School of Athens, Athens, Greece2nd Department of Surgery, Aretaieion University Hospital, Medical School of Athens, Athens, GreecePathology Department, Aretaieion University Hospital, Medical School of Athens, Athens, Greece2nd Department of Surgery, Aretaieion University Hospital, Medical School of Athens, Athens, GreeceIntroduction. Solitary fibrous tumor is a rare type of mesenchymal, spindle-cell tumor reported mostly in the pleura. Retroperitoneal occurrence is rare and histopathological diagnosis is challenging. Case Presentation. A 55-year-old woman with nonspecific abdominal pain was found to have a retroperitoneal/pelvic mass adjacent to the upper rectum. The patient underwent surgical resection in clear margins of this pelvic tumor, entering the total mesenteric excision surgical plane. Final histopathology revealed a solitary fibrous tumor and the case is presented herein. Discussion. Solitary fibrous tumor in the retroperitoneum is rarely found in the literature and to the best of our knowledge less than a hundred cases are described so far. Histopathological diagnosis is mostly based on a “patternless pattern” on microscopic examination, which is a storiform arrangement of spindle cells combined with a “hemangiopericytoma-like appearance” and increased vascularity of the lesion. Surgery is the mainstay of treatment and recurrence rates are generally low.http://dx.doi.org/10.1155/2017/4634235
spellingShingle D. Myoteri
D. Dellaportas
C. Nastos
I. Gioti
G. Gkiokas
E. Carvounis
T. Theodosopoulos
Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor
Case Reports in Oncological Medicine
title Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor
title_full Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor
title_fullStr Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor
title_full_unstemmed Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor
title_short Retroperitoneal Solitary Fibrous Tumor: A “Patternless” Tumor
title_sort retroperitoneal solitary fibrous tumor a patternless tumor
url http://dx.doi.org/10.1155/2017/4634235
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AT igioti retroperitonealsolitaryfibroustumorapatternlesstumor
AT ggkiokas retroperitonealsolitaryfibroustumorapatternlesstumor
AT ecarvounis retroperitonealsolitaryfibroustumorapatternlesstumor
AT ttheodosopoulos retroperitonealsolitaryfibroustumorapatternlesstumor