ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORT

Myeloid Sarcoma (MS), also known as granulocytic sarcoma or chloroma, is a rare extramedullary tumor consisting of immature myeloid cells. It can occur as an isolated entity, concurrently with Acute Myeloid Leukemia (AML), or as a relapse manifestation. In cases where myeloid sarcoma presents withou...

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Main Authors: Elif Canpolat Hırfanoğlu, Ali Turunç, Birol Güvenç
Format: Article
Language:English
Published: Elsevier 2025-07-01
Series:Hematology, Transfusion and Cell Therapy
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Online Access:http://www.sciencedirect.com/science/article/pii/S2531137925001786
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author Elif Canpolat Hırfanoğlu
Ali Turunç
Birol Güvenç
author_facet Elif Canpolat Hırfanoğlu
Ali Turunç
Birol Güvenç
author_sort Elif Canpolat Hırfanoğlu
collection DOAJ
description Myeloid Sarcoma (MS), also known as granulocytic sarcoma or chloroma, is a rare extramedullary tumor consisting of immature myeloid cells. It can occur as an isolated entity, concurrently with Acute Myeloid Leukemia (AML), or as a relapse manifestation. In cases where myeloid sarcoma presents without prior hematologic malignancy and with normal peripheral blood counts, diagnosis can be significantly delayed, leading to disease progression. Recognizing MS as a potential early sign of AML is crucial to initiating timely treatment. A 48-year-old female with a history of hypertension and a prior L1 vertebral compression fracture in 2016 presented with new-onset lumbar pain in 2024. Lumbar MRI revealed a paraspinal soft tissue lesion at the T12‒L1 level, prompting further investigation. The patient’s hematologic parameters were within normal limits, with a white blood cell count of 8290 µL, hemoglobin of 13 g/dL, and platelet count of 400,000 µL. The lesion was surgically excised, and histopathological examination confirmed myeloid sarcoma. Following this diagnosis, hematology consultation was requested, and bone marrow aspiration and biopsy were performed. Although the blast percentage was only 7%‒8%, flow cytometry findings were consistent with AML. PET-CT revealed hypermetabolic activity in the paravertebral region with a maximum SUV of 10.94 and abnormal uptake in both humeri and femurs, suggesting possible bone marrow involvement. The patient was diagnosed with AML and started on 7+3 induction chemotherapy with cytarabine and daunorubicin, along with radiotherapy for local disease control. This case highlights the diagnostic challenge of isolated myeloid sarcoma in the absence of peripheral blood abnormalities and emphasizes the importance of early hematologic evaluation. PET-CT played a crucial role in detecting subclinical bone marrow involvement, guiding treatment decisions. Recognizing myeloid sarcoma as a potential precursor to AML is essential for timely diagnosis and intervention, as early systemic chemotherapy can prevent disease progression and improve patient outcomes.
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spelling doaj-art-742e7d4d64474e48bebbc82fb29b6ccf2025-08-20T03:31:31ZengElsevierHematology, Transfusion and Cell Therapy2531-13792025-07-014710391010.1016/j.htct.2025.103910ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORTElif Canpolat Hırfanoğlu0Ali Turunç1Birol Güvenç2Department of Internal Medicine, Cukurova University Medical Faculty Hospital, Adana, TurkeyDepartment of Internal Medicine, Cukurova University Medical Faculty Hospital, Division of Hematology, Adana, TurkeyDepartment of Internal Medicine, Cukurova University Medical Faculty Hospital, Division of Hematology, Adana, TurkeyMyeloid Sarcoma (MS), also known as granulocytic sarcoma or chloroma, is a rare extramedullary tumor consisting of immature myeloid cells. It can occur as an isolated entity, concurrently with Acute Myeloid Leukemia (AML), or as a relapse manifestation. In cases where myeloid sarcoma presents without prior hematologic malignancy and with normal peripheral blood counts, diagnosis can be significantly delayed, leading to disease progression. Recognizing MS as a potential early sign of AML is crucial to initiating timely treatment. A 48-year-old female with a history of hypertension and a prior L1 vertebral compression fracture in 2016 presented with new-onset lumbar pain in 2024. Lumbar MRI revealed a paraspinal soft tissue lesion at the T12‒L1 level, prompting further investigation. The patient’s hematologic parameters were within normal limits, with a white blood cell count of 8290 µL, hemoglobin of 13 g/dL, and platelet count of 400,000 µL. The lesion was surgically excised, and histopathological examination confirmed myeloid sarcoma. Following this diagnosis, hematology consultation was requested, and bone marrow aspiration and biopsy were performed. Although the blast percentage was only 7%‒8%, flow cytometry findings were consistent with AML. PET-CT revealed hypermetabolic activity in the paravertebral region with a maximum SUV of 10.94 and abnormal uptake in both humeri and femurs, suggesting possible bone marrow involvement. The patient was diagnosed with AML and started on 7+3 induction chemotherapy with cytarabine and daunorubicin, along with radiotherapy for local disease control. This case highlights the diagnostic challenge of isolated myeloid sarcoma in the absence of peripheral blood abnormalities and emphasizes the importance of early hematologic evaluation. PET-CT played a crucial role in detecting subclinical bone marrow involvement, guiding treatment decisions. Recognizing myeloid sarcoma as a potential precursor to AML is essential for timely diagnosis and intervention, as early systemic chemotherapy can prevent disease progression and improve patient outcomes.http://www.sciencedirect.com/science/article/pii/S25311379250017867+3 ChemotherapyAcute Myeloid LeukemiaExtramedullary LeukemiaMyeloid SarcomaSoft Tissue Involvement
spellingShingle Elif Canpolat Hırfanoğlu
Ali Turunç
Birol Güvenç
ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORT
Hematology, Transfusion and Cell Therapy
7+3 Chemotherapy
Acute Myeloid Leukemia
Extramedullary Leukemia
Myeloid Sarcoma
Soft Tissue Involvement
title ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORT
title_full ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORT
title_fullStr ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORT
title_full_unstemmed ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORT
title_short ACUTE MYELOID LEUKEMIA PRESENTING AS ISOLATED MYELOID SARCOMA: A CASE REPORT
title_sort acute myeloid leukemia presenting as isolated myeloid sarcoma a case report
topic 7+3 Chemotherapy
Acute Myeloid Leukemia
Extramedullary Leukemia
Myeloid Sarcoma
Soft Tissue Involvement
url http://www.sciencedirect.com/science/article/pii/S2531137925001786
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AT birolguvenc acutemyeloidleukemiapresentingasisolatedmyeloidsarcomaacasereport