Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding
Pseudoxanchoma elasticum (PXE) is an inherited disorder of connective tissue, characterized by calcification and degeneration of elastin. Clinical manifestations of PXE are protean, with skin, eyes and arteries being most commonly involved. Although often a benign condition, gastrointestinal hemorrh...
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Format: | Article |
Language: | English |
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Wiley
1989-01-01
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Series: | Canadian Journal of Gastroenterology |
Online Access: | http://dx.doi.org/10.1155/1989/974847 |
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author | Deborah J. Cook Samih S. Salama Robert J. Tuttle |
author_facet | Deborah J. Cook Samih S. Salama Robert J. Tuttle |
author_sort | Deborah J. Cook |
collection | DOAJ |
description | Pseudoxanchoma elasticum (PXE) is an inherited disorder of
connective tissue, characterized by calcification and degeneration of elastin.
Clinical manifestations of PXE are protean, with skin, eyes and arteries being
most commonly involved. Although often a benign condition, gastrointestinal
hemorrhage is a potentially fatal complication. An unusual case of gastrointestinal
hemorrhage in a patient with PXE is described and the pathophysiology,
clinical presentation and complications of this rare condition are reviewed. |
format | Article |
id | doaj-art-732cb47b224343cdbbd021f528a59d58 |
institution | Kabale University |
issn | 0835-7900 |
language | English |
publishDate | 1989-01-01 |
publisher | Wiley |
record_format | Article |
series | Canadian Journal of Gastroenterology |
spelling | doaj-art-732cb47b224343cdbbd021f528a59d582025-02-03T06:00:47ZengWileyCanadian Journal of Gastroenterology0835-79001989-01-013414114410.1155/1989/974847Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal BleedingDeborah J. Cook0Samih S. Salama1Robert J. Tuttle2Departments of Medicine, Pathology and Radiology, St Joseph’s Hospital, McMaster University, Hamilton, Ontario, CanadaDepartments of Medicine, Pathology and Radiology, St Joseph’s Hospital, McMaster University, Hamilton, Ontario, CanadaDepartments of Medicine, Pathology and Radiology, St Joseph’s Hospital, McMaster University, Hamilton, Ontario, CanadaPseudoxanchoma elasticum (PXE) is an inherited disorder of connective tissue, characterized by calcification and degeneration of elastin. Clinical manifestations of PXE are protean, with skin, eyes and arteries being most commonly involved. Although often a benign condition, gastrointestinal hemorrhage is a potentially fatal complication. An unusual case of gastrointestinal hemorrhage in a patient with PXE is described and the pathophysiology, clinical presentation and complications of this rare condition are reviewed.http://dx.doi.org/10.1155/1989/974847 |
spellingShingle | Deborah J. Cook Samih S. Salama Robert J. Tuttle Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding Canadian Journal of Gastroenterology |
title | Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding |
title_full | Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding |
title_fullStr | Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding |
title_full_unstemmed | Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding |
title_short | Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding |
title_sort | psudoxanthoma elasticum an unusual case of gastrointestinal bleeding |
url | http://dx.doi.org/10.1155/1989/974847 |
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