Psudoxanthoma elasticum: An Unusual Case of Gastrointestinal Bleeding
Pseudoxanchoma elasticum (PXE) is an inherited disorder of connective tissue, characterized by calcification and degeneration of elastin. Clinical manifestations of PXE are protean, with skin, eyes and arteries being most commonly involved. Although often a benign condition, gastrointestinal hemorrh...
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| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wiley
1989-01-01
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| Series: | Canadian Journal of Gastroenterology |
| Online Access: | http://dx.doi.org/10.1155/1989/974847 |
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| Summary: | Pseudoxanchoma elasticum (PXE) is an inherited disorder of
connective tissue, characterized by calcification and degeneration of elastin.
Clinical manifestations of PXE are protean, with skin, eyes and arteries being
most commonly involved. Although often a benign condition, gastrointestinal
hemorrhage is a potentially fatal complication. An unusual case of gastrointestinal
hemorrhage in a patient with PXE is described and the pathophysiology,
clinical presentation and complications of this rare condition are reviewed. |
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| ISSN: | 0835-7900 |