Novel Technique of Surgical Management of Scimitar Syndrome

Scimitar syndrome is a rare congenital abnormality resulting from right-sided pulmonary venous return to the inferior vena cava rather than to the left atrium. It is usually detected in early childhood with symptoms of recurrent chest infection and finding of pulmonary hypertension due to left to ri...

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Main Authors: Mary Lark, Amanda Cai, Phillip Rideout, David Gregg, Pal Suranyi, Fred A. Crawford, Valerian L. Fernandes
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Case Reports in Cardiology
Online Access:http://dx.doi.org/10.1155/2019/6932680
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author Mary Lark
Amanda Cai
Phillip Rideout
David Gregg
Pal Suranyi
Fred A. Crawford
Valerian L. Fernandes
author_facet Mary Lark
Amanda Cai
Phillip Rideout
David Gregg
Pal Suranyi
Fred A. Crawford
Valerian L. Fernandes
author_sort Mary Lark
collection DOAJ
description Scimitar syndrome is a rare congenital abnormality resulting from right-sided pulmonary venous return to the inferior vena cava rather than to the left atrium. It is usually detected in early childhood with symptoms of recurrent chest infection and finding of pulmonary hypertension due to left to right shunt. We report a case of a 40-year-old woman with scimitar syndrome discovered on chest X-ray during evaluation of recurrent pneumonia. Surgical correction was achieved with a novel technique of using a synthetic graft connecting the scimitar vein across the right atrium to the left atrium along with ligation of the scimitar vein connection to the inferior vena cava. The patient continues to do well 10 years after surgery, and the shunt graft shows good flow on echocardiogram. We present her clinical and imaging data and details of the surgical technique along with a brief review of surgical literature.
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institution Kabale University
issn 2090-6404
2090-6412
language English
publishDate 2019-01-01
publisher Wiley
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series Case Reports in Cardiology
spelling doaj-art-71f54fb5e14e4e1fad3b39c1da88255a2025-02-03T06:13:12ZengWileyCase Reports in Cardiology2090-64042090-64122019-01-01201910.1155/2019/69326806932680Novel Technique of Surgical Management of Scimitar SyndromeMary Lark0Amanda Cai1Phillip Rideout2David Gregg3Pal Suranyi4Fred A. Crawford5Valerian L. Fernandes6College of Medicine, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Cardiology, Medical University of South Carolina, Charleston, SC 29425, USACollege of Medicine, Medical University of South Carolina, Charleston, SC 29425, USACollege of Medicine, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Cardiology, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Surgery, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Cardiology, Medical University of South Carolina, Charleston, SC 29425, USAScimitar syndrome is a rare congenital abnormality resulting from right-sided pulmonary venous return to the inferior vena cava rather than to the left atrium. It is usually detected in early childhood with symptoms of recurrent chest infection and finding of pulmonary hypertension due to left to right shunt. We report a case of a 40-year-old woman with scimitar syndrome discovered on chest X-ray during evaluation of recurrent pneumonia. Surgical correction was achieved with a novel technique of using a synthetic graft connecting the scimitar vein across the right atrium to the left atrium along with ligation of the scimitar vein connection to the inferior vena cava. The patient continues to do well 10 years after surgery, and the shunt graft shows good flow on echocardiogram. We present her clinical and imaging data and details of the surgical technique along with a brief review of surgical literature.http://dx.doi.org/10.1155/2019/6932680
spellingShingle Mary Lark
Amanda Cai
Phillip Rideout
David Gregg
Pal Suranyi
Fred A. Crawford
Valerian L. Fernandes
Novel Technique of Surgical Management of Scimitar Syndrome
Case Reports in Cardiology
title Novel Technique of Surgical Management of Scimitar Syndrome
title_full Novel Technique of Surgical Management of Scimitar Syndrome
title_fullStr Novel Technique of Surgical Management of Scimitar Syndrome
title_full_unstemmed Novel Technique of Surgical Management of Scimitar Syndrome
title_short Novel Technique of Surgical Management of Scimitar Syndrome
title_sort novel technique of surgical management of scimitar syndrome
url http://dx.doi.org/10.1155/2019/6932680
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