Novel Technique of Surgical Management of Scimitar Syndrome
Scimitar syndrome is a rare congenital abnormality resulting from right-sided pulmonary venous return to the inferior vena cava rather than to the left atrium. It is usually detected in early childhood with symptoms of recurrent chest infection and finding of pulmonary hypertension due to left to ri...
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Format: | Article |
Language: | English |
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Wiley
2019-01-01
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Series: | Case Reports in Cardiology |
Online Access: | http://dx.doi.org/10.1155/2019/6932680 |
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author | Mary Lark Amanda Cai Phillip Rideout David Gregg Pal Suranyi Fred A. Crawford Valerian L. Fernandes |
author_facet | Mary Lark Amanda Cai Phillip Rideout David Gregg Pal Suranyi Fred A. Crawford Valerian L. Fernandes |
author_sort | Mary Lark |
collection | DOAJ |
description | Scimitar syndrome is a rare congenital abnormality resulting from right-sided pulmonary venous return to the inferior vena cava rather than to the left atrium. It is usually detected in early childhood with symptoms of recurrent chest infection and finding of pulmonary hypertension due to left to right shunt. We report a case of a 40-year-old woman with scimitar syndrome discovered on chest X-ray during evaluation of recurrent pneumonia. Surgical correction was achieved with a novel technique of using a synthetic graft connecting the scimitar vein across the right atrium to the left atrium along with ligation of the scimitar vein connection to the inferior vena cava. The patient continues to do well 10 years after surgery, and the shunt graft shows good flow on echocardiogram. We present her clinical and imaging data and details of the surgical technique along with a brief review of surgical literature. |
format | Article |
id | doaj-art-71f54fb5e14e4e1fad3b39c1da88255a |
institution | Kabale University |
issn | 2090-6404 2090-6412 |
language | English |
publishDate | 2019-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Cardiology |
spelling | doaj-art-71f54fb5e14e4e1fad3b39c1da88255a2025-02-03T06:13:12ZengWileyCase Reports in Cardiology2090-64042090-64122019-01-01201910.1155/2019/69326806932680Novel Technique of Surgical Management of Scimitar SyndromeMary Lark0Amanda Cai1Phillip Rideout2David Gregg3Pal Suranyi4Fred A. Crawford5Valerian L. Fernandes6College of Medicine, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Cardiology, Medical University of South Carolina, Charleston, SC 29425, USACollege of Medicine, Medical University of South Carolina, Charleston, SC 29425, USACollege of Medicine, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Cardiology, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Surgery, Medical University of South Carolina, Charleston, SC 29425, USADepartment of Cardiology, Medical University of South Carolina, Charleston, SC 29425, USAScimitar syndrome is a rare congenital abnormality resulting from right-sided pulmonary venous return to the inferior vena cava rather than to the left atrium. It is usually detected in early childhood with symptoms of recurrent chest infection and finding of pulmonary hypertension due to left to right shunt. We report a case of a 40-year-old woman with scimitar syndrome discovered on chest X-ray during evaluation of recurrent pneumonia. Surgical correction was achieved with a novel technique of using a synthetic graft connecting the scimitar vein across the right atrium to the left atrium along with ligation of the scimitar vein connection to the inferior vena cava. The patient continues to do well 10 years after surgery, and the shunt graft shows good flow on echocardiogram. We present her clinical and imaging data and details of the surgical technique along with a brief review of surgical literature.http://dx.doi.org/10.1155/2019/6932680 |
spellingShingle | Mary Lark Amanda Cai Phillip Rideout David Gregg Pal Suranyi Fred A. Crawford Valerian L. Fernandes Novel Technique of Surgical Management of Scimitar Syndrome Case Reports in Cardiology |
title | Novel Technique of Surgical Management of Scimitar Syndrome |
title_full | Novel Technique of Surgical Management of Scimitar Syndrome |
title_fullStr | Novel Technique of Surgical Management of Scimitar Syndrome |
title_full_unstemmed | Novel Technique of Surgical Management of Scimitar Syndrome |
title_short | Novel Technique of Surgical Management of Scimitar Syndrome |
title_sort | novel technique of surgical management of scimitar syndrome |
url | http://dx.doi.org/10.1155/2019/6932680 |
work_keys_str_mv | AT marylark noveltechniqueofsurgicalmanagementofscimitarsyndrome AT amandacai noveltechniqueofsurgicalmanagementofscimitarsyndrome AT philliprideout noveltechniqueofsurgicalmanagementofscimitarsyndrome AT davidgregg noveltechniqueofsurgicalmanagementofscimitarsyndrome AT palsuranyi noveltechniqueofsurgicalmanagementofscimitarsyndrome AT fredacrawford noveltechniqueofsurgicalmanagementofscimitarsyndrome AT valerianlfernandes noveltechniqueofsurgicalmanagementofscimitarsyndrome |