A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid Hemangioendothelioma
Epithelioid hemangioendothelioma (EHE) is a rare tumor of intermediate malignancy. We report a case of intracranial and intraorbitar EHE. A 3-year-old girl presented with a 3-month history of progressive left exophthalmia. Neuroradiologic imaging (CT scan and MRI) showed an intraorbitar process wit...
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| Format: | Article |
| Language: | English |
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Wiley
2012-01-01
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| Series: | Case Reports in Neurological Medicine |
| Online Access: | http://dx.doi.org/10.1155/2012/396097 |
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| author | K. Aniba M. Laghmari M. Lmejjati H. Ghannane S. Ait Benali |
| author_facet | K. Aniba M. Laghmari M. Lmejjati H. Ghannane S. Ait Benali |
| author_sort | K. Aniba |
| collection | DOAJ |
| description | Epithelioid hemangioendothelioma (EHE) is a rare tumor of intermediate malignancy.
We report a case of intracranial and intraorbitar EHE. A 3-year-old girl presented with a 3-month history of progressive left exophthalmia. Neuroradiologic imaging (CT scan and MRI) showed an intraorbitar process with an intense enhancement extending to temporal fossa, ethmoidal bone, nasal fossa, maxillary sinus, and cavernous sinus. The angiogram was normal.
The tumor was operated through subfrontal approach but only a partial resection was performed. The histological diagnosis was epithelioid hemangioendothelioma. The patient was neurologically intact 2 months after surgery without exophtalmia. However 4 months after surgery he displayed a fall of the right eye vision with intense headache. Control CT scan showed persistence of important tumoral residue. Epithelioid hemangioendothelioma is a hemorrhagic tumor. Total removal must be possible. Otherwise, we recommend a complementary chemoradiotherapy and close followup. We propose this interesting case history of a tragical evolution of EHE in contradiction with what has already been reported. |
| format | Article |
| id | doaj-art-710a713b3bab436183337eb733feddc6 |
| institution | Kabale University |
| issn | 2090-6668 2090-6676 |
| language | English |
| publishDate | 2012-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Neurological Medicine |
| spelling | doaj-art-710a713b3bab436183337eb733feddc62025-02-03T01:23:31ZengWileyCase Reports in Neurological Medicine2090-66682090-66762012-01-01201210.1155/2012/396097396097A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid HemangioendotheliomaK. Aniba0M. Laghmari1M. Lmejjati2H. Ghannane3S. Ait Benali4Department of Neurosurgery, Mohammed VI University Medical Centre, and Cadi Ayyad University, Marrakesh, MoroccoDepartment of Neurosurgery, Mohammed VI University Medical Centre, and Cadi Ayyad University, Marrakesh, MoroccoDepartment of Neurosurgery, Mohammed VI University Medical Centre, and Cadi Ayyad University, Marrakesh, MoroccoDepartment of Neurosurgery, Mohammed VI University Medical Centre, and Cadi Ayyad University, Marrakesh, MoroccoDepartment of Neurosurgery, Mohammed VI University Medical Centre, and Cadi Ayyad University, Marrakesh, MoroccoEpithelioid hemangioendothelioma (EHE) is a rare tumor of intermediate malignancy. We report a case of intracranial and intraorbitar EHE. A 3-year-old girl presented with a 3-month history of progressive left exophthalmia. Neuroradiologic imaging (CT scan and MRI) showed an intraorbitar process with an intense enhancement extending to temporal fossa, ethmoidal bone, nasal fossa, maxillary sinus, and cavernous sinus. The angiogram was normal. The tumor was operated through subfrontal approach but only a partial resection was performed. The histological diagnosis was epithelioid hemangioendothelioma. The patient was neurologically intact 2 months after surgery without exophtalmia. However 4 months after surgery he displayed a fall of the right eye vision with intense headache. Control CT scan showed persistence of important tumoral residue. Epithelioid hemangioendothelioma is a hemorrhagic tumor. Total removal must be possible. Otherwise, we recommend a complementary chemoradiotherapy and close followup. We propose this interesting case history of a tragical evolution of EHE in contradiction with what has already been reported.http://dx.doi.org/10.1155/2012/396097 |
| spellingShingle | K. Aniba M. Laghmari M. Lmejjati H. Ghannane S. Ait Benali A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid Hemangioendothelioma Case Reports in Neurological Medicine |
| title | A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid Hemangioendothelioma |
| title_full | A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid Hemangioendothelioma |
| title_fullStr | A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid Hemangioendothelioma |
| title_full_unstemmed | A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid Hemangioendothelioma |
| title_short | A Tragical Paediatric Case History of Intraorbital and Intracranial Epithelioid Hemangioendothelioma |
| title_sort | tragical paediatric case history of intraorbital and intracranial epithelioid hemangioendothelioma |
| url | http://dx.doi.org/10.1155/2012/396097 |
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