Esophageal Leiomyomatosis – An Unusual Cause of Pseudoachalasia
Esophageal leiomyomatosis is a rare hamartomatous disorder with varied presentation. In the literature, it is described mostly in children, and is associated with Alport’s syndrome. A case of leiomyomatosis that presented as achalasia not associated with Alport’s syndrome is described in a 35-year-o...
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| Format: | Article |
| Language: | English |
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Wiley
2008-01-01
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| Series: | Canadian Journal of Gastroenterology |
| Online Access: | http://dx.doi.org/10.1155/2008/603105 |
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| author | Sukanta Ray Sundeep Singh Saluja Ruchika Gupta Tushar Kanti Chattopadhyay |
| author_facet | Sukanta Ray Sundeep Singh Saluja Ruchika Gupta Tushar Kanti Chattopadhyay |
| author_sort | Sukanta Ray |
| collection | DOAJ |
| description | Esophageal leiomyomatosis is a rare hamartomatous disorder with varied presentation. In the literature, it is described mostly in children, and is associated with Alport’s syndrome. A case of leiomyomatosis that presented as achalasia not associated with Alport’s syndrome is described in a 35-year-old woman with a 16-year history of dysphagia. Barium swallow showed a smooth narrowing at the lower end of the esophagus with a longer than usual stricture length. Endoscopy showed a dilated esophagus with a submucosal nodule in the region of the cardia. A computed tomography scan revealed circumferential thickening of the esophagus involving the gastroesophageal junction, with fat planes maintained with the adjacent structure. Endoscopic ultrasound demonstrated a lesion arising from the muscularis propria. The manometry findings were suggestive of achalasia. She underwent transhiatal esophagectomy with gastric pull-up. |
| format | Article |
| id | doaj-art-61729bcf629f49fab140f147523d0b54 |
| institution | Kabale University |
| issn | 0835-7900 |
| language | English |
| publishDate | 2008-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Canadian Journal of Gastroenterology |
| spelling | doaj-art-61729bcf629f49fab140f147523d0b542025-02-03T01:32:51ZengWileyCanadian Journal of Gastroenterology0835-79002008-01-0122218718910.1155/2008/603105Esophageal Leiomyomatosis – An Unusual Cause of PseudoachalasiaSukanta Ray0Sundeep Singh Saluja1Ruchika Gupta2Tushar Kanti Chattopadhyay3Department of Gastrointestinal Surgery, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, IndiaDepartment of Gastrointestinal Surgery, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, IndiaDepartment of Pathology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, IndiaDepartment of Gastrointestinal Surgery, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, IndiaEsophageal leiomyomatosis is a rare hamartomatous disorder with varied presentation. In the literature, it is described mostly in children, and is associated with Alport’s syndrome. A case of leiomyomatosis that presented as achalasia not associated with Alport’s syndrome is described in a 35-year-old woman with a 16-year history of dysphagia. Barium swallow showed a smooth narrowing at the lower end of the esophagus with a longer than usual stricture length. Endoscopy showed a dilated esophagus with a submucosal nodule in the region of the cardia. A computed tomography scan revealed circumferential thickening of the esophagus involving the gastroesophageal junction, with fat planes maintained with the adjacent structure. Endoscopic ultrasound demonstrated a lesion arising from the muscularis propria. The manometry findings were suggestive of achalasia. She underwent transhiatal esophagectomy with gastric pull-up.http://dx.doi.org/10.1155/2008/603105 |
| spellingShingle | Sukanta Ray Sundeep Singh Saluja Ruchika Gupta Tushar Kanti Chattopadhyay Esophageal Leiomyomatosis – An Unusual Cause of Pseudoachalasia Canadian Journal of Gastroenterology |
| title | Esophageal Leiomyomatosis – An Unusual Cause of Pseudoachalasia |
| title_full | Esophageal Leiomyomatosis – An Unusual Cause of Pseudoachalasia |
| title_fullStr | Esophageal Leiomyomatosis – An Unusual Cause of Pseudoachalasia |
| title_full_unstemmed | Esophageal Leiomyomatosis – An Unusual Cause of Pseudoachalasia |
| title_short | Esophageal Leiomyomatosis – An Unusual Cause of Pseudoachalasia |
| title_sort | esophageal leiomyomatosis an unusual cause of pseudoachalasia |
| url | http://dx.doi.org/10.1155/2008/603105 |
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