Spinal Nerve Root Haemangioblastoma Associated with Reactive Polycythemia
Haemangioblastomas are uncommon tumours that usually occur in the cerebellum and, less commonly, in the intramedullary spinal cord. The extramedullary spinal canal is an uncommon location for these tumours. Also haemangioblastoma at this site is not known to be associated with polycythemia. We prese...
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| Format: | Article |
| Language: | English |
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Wiley
2014-01-01
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| Series: | Case Reports in Radiology |
| Online Access: | http://dx.doi.org/10.1155/2014/798620 |
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| author | Eric K. C. Law Ryan K. L. Lee James F. Griffith Deyond Y. W. Siu Ho Keung Ng |
| author_facet | Eric K. C. Law Ryan K. L. Lee James F. Griffith Deyond Y. W. Siu Ho Keung Ng |
| author_sort | Eric K. C. Law |
| collection | DOAJ |
| description | Haemangioblastomas are uncommon tumours that usually occur in the cerebellum and, less commonly, in the intramedullary spinal cord. The extramedullary spinal canal is an uncommon location for these tumours. Also haemangioblastoma at this site is not known to be associated with polycythemia. We present the clinical, imaging, and histological findings of an adult patient with extramedullary spinal haemangioblastoma and reactive polycythemia. Radiography and computed tomography (CT) revealed a medium-sized tumour that most likely arose from an extramedullary spinal nerve root. This tumour appeared to be slow growing as evidenced by the accompanying well-defined bony resorption with a sclerotic rim and mild neural foraminal widening. Magnetic resonance imaging revealed prominent flow voids consistent with tumoural hypervascularity. CT-guided biopsy was performed. Although preoperative angiographic embolisation was technically successful, excessive intraoperative tumour bleeding necessitated tumour debulking rather than complete tumour resection. Histology of the resected specimen revealed haemangioblastoma. Seven months postoperatively, the patients back pain and polycythemia have resolved. |
| format | Article |
| id | doaj-art-5de962d359ff49869f4489cc9a533e1c |
| institution | Kabale University |
| issn | 2090-6862 2090-6870 |
| language | English |
| publishDate | 2014-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Radiology |
| spelling | doaj-art-5de962d359ff49869f4489cc9a533e1c2025-02-03T01:31:00ZengWileyCase Reports in Radiology2090-68622090-68702014-01-01201410.1155/2014/798620798620Spinal Nerve Root Haemangioblastoma Associated with Reactive PolycythemiaEric K. C. Law0Ryan K. L. Lee1James F. Griffith2Deyond Y. W. Siu3Ho Keung Ng4Department of Imaging & Interventional Radiology, Prince of Wales Hospital, The Chinese University of Hong Kong, 30-32 Ngan Shing Street, Shatin, New Territories, Hong KongDepartment of Imaging & Interventional Radiology, Prince of Wales Hospital, The Chinese University of Hong Kong, 30-32 Ngan Shing Street, Shatin, New Territories, Hong KongDepartment of Imaging & Interventional Radiology, Prince of Wales Hospital, The Chinese University of Hong Kong, 30-32 Ngan Shing Street, Shatin, New Territories, Hong KongDepartment of Imaging & Interventional Radiology, Prince of Wales Hospital, The Chinese University of Hong Kong, 30-32 Ngan Shing Street, Shatin, New Territories, Hong KongDepartment of Anatomical & Cellular Pathology, Prince of Wales Hospital, The Chinese University of Hong Kong, Hong KongHaemangioblastomas are uncommon tumours that usually occur in the cerebellum and, less commonly, in the intramedullary spinal cord. The extramedullary spinal canal is an uncommon location for these tumours. Also haemangioblastoma at this site is not known to be associated with polycythemia. We present the clinical, imaging, and histological findings of an adult patient with extramedullary spinal haemangioblastoma and reactive polycythemia. Radiography and computed tomography (CT) revealed a medium-sized tumour that most likely arose from an extramedullary spinal nerve root. This tumour appeared to be slow growing as evidenced by the accompanying well-defined bony resorption with a sclerotic rim and mild neural foraminal widening. Magnetic resonance imaging revealed prominent flow voids consistent with tumoural hypervascularity. CT-guided biopsy was performed. Although preoperative angiographic embolisation was technically successful, excessive intraoperative tumour bleeding necessitated tumour debulking rather than complete tumour resection. Histology of the resected specimen revealed haemangioblastoma. Seven months postoperatively, the patients back pain and polycythemia have resolved.http://dx.doi.org/10.1155/2014/798620 |
| spellingShingle | Eric K. C. Law Ryan K. L. Lee James F. Griffith Deyond Y. W. Siu Ho Keung Ng Spinal Nerve Root Haemangioblastoma Associated with Reactive Polycythemia Case Reports in Radiology |
| title | Spinal Nerve Root Haemangioblastoma Associated with Reactive Polycythemia |
| title_full | Spinal Nerve Root Haemangioblastoma Associated with Reactive Polycythemia |
| title_fullStr | Spinal Nerve Root Haemangioblastoma Associated with Reactive Polycythemia |
| title_full_unstemmed | Spinal Nerve Root Haemangioblastoma Associated with Reactive Polycythemia |
| title_short | Spinal Nerve Root Haemangioblastoma Associated with Reactive Polycythemia |
| title_sort | spinal nerve root haemangioblastoma associated with reactive polycythemia |
| url | http://dx.doi.org/10.1155/2014/798620 |
| work_keys_str_mv | AT erickclaw spinalnerveroothaemangioblastomaassociatedwithreactivepolycythemia AT ryankllee spinalnerveroothaemangioblastomaassociatedwithreactivepolycythemia AT jamesfgriffith spinalnerveroothaemangioblastomaassociatedwithreactivepolycythemia AT deyondywsiu spinalnerveroothaemangioblastomaassociatedwithreactivepolycythemia AT hokeungng spinalnerveroothaemangioblastomaassociatedwithreactivepolycythemia |