An unexpected and tumultuous diagnosis of a left atrial mass
This case presents a curious diagnosis in a young male presenting with chest pain. The first imaging tests suggested the presence of a hypovascular left atrial tumor. After cardiac magnetic resonance and the exclusion of extra-cardiac lesions, sarcoma emerged as the main diagnostic hypothesis. Unex...
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PAGEPress Publications
2025-01-01
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Series: | Monaldi Archives for Chest Disease |
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Online Access: | https://www.monaldi-archives.org/macd/article/view/3221 |
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author | Catarina Amaral Marques Carlos Xavier Resende João Rebelo Paulo Pinho Mariana Vasconcelos Rui André Rodrigues |
author_facet | Catarina Amaral Marques Carlos Xavier Resende João Rebelo Paulo Pinho Mariana Vasconcelos Rui André Rodrigues |
author_sort | Catarina Amaral Marques |
collection | DOAJ |
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This case presents a curious diagnosis in a young male presenting with chest pain. The first imaging tests suggested the presence of a hypovascular left atrial tumor. After cardiac magnetic resonance and the exclusion of extra-cardiac lesions, sarcoma emerged as the main diagnostic hypothesis. Unexpectedly, the histopathological study revealed the absence of malignancy, identifiable inflammatory and cardiac muscle tissue, and fibrosis. This pattern was compatible with inflammatory myofibroblastic tumor diagnosis, a rare entity with uncertain behavior but a known risk of recurrence and/or potentially fatal complications. This is a unique case of an unexpected finding at presentation, as well as a complex diagnostic work-up and a surprisingly unusual final diagnosis. It also highlights the increasing importance of the multimodality imaging approach, as well as the critical role of multidisciplinary discussion in optimizing patient management in such complex cases.
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format | Article |
id | doaj-art-5d66ceaef67a4fffa1bcb4077940a412 |
institution | Kabale University |
issn | 1122-0643 2532-5264 |
language | English |
publishDate | 2025-01-01 |
publisher | PAGEPress Publications |
record_format | Article |
series | Monaldi Archives for Chest Disease |
spelling | doaj-art-5d66ceaef67a4fffa1bcb4077940a4122025-01-22T01:39:26ZengPAGEPress PublicationsMonaldi Archives for Chest Disease1122-06432532-52642025-01-0110.4081/monaldi.2025.3221An unexpected and tumultuous diagnosis of a left atrial massCatarina Amaral Marques0Carlos Xavier Resende1João Rebelo2Paulo Pinho3Mariana Vasconcelos4https://orcid.org/0000-0002-6287-9562Rui André Rodrigues5Local Health Unit of São João, PortoLocal Health Unit of São João, PortoLocal Health Unit of São João, PortoLocal Health Unit of São João, PortoLocal Health Unit of São João, PortoLocal Health Unit of São João, Porto This case presents a curious diagnosis in a young male presenting with chest pain. The first imaging tests suggested the presence of a hypovascular left atrial tumor. After cardiac magnetic resonance and the exclusion of extra-cardiac lesions, sarcoma emerged as the main diagnostic hypothesis. Unexpectedly, the histopathological study revealed the absence of malignancy, identifiable inflammatory and cardiac muscle tissue, and fibrosis. This pattern was compatible with inflammatory myofibroblastic tumor diagnosis, a rare entity with uncertain behavior but a known risk of recurrence and/or potentially fatal complications. This is a unique case of an unexpected finding at presentation, as well as a complex diagnostic work-up and a surprisingly unusual final diagnosis. It also highlights the increasing importance of the multimodality imaging approach, as well as the critical role of multidisciplinary discussion in optimizing patient management in such complex cases. https://www.monaldi-archives.org/macd/article/view/3221Cardiac imagingcardiac massesinflammatory myofibroblastic tumormultimodality imaging |
spellingShingle | Catarina Amaral Marques Carlos Xavier Resende João Rebelo Paulo Pinho Mariana Vasconcelos Rui André Rodrigues An unexpected and tumultuous diagnosis of a left atrial mass Monaldi Archives for Chest Disease Cardiac imaging cardiac masses inflammatory myofibroblastic tumor multimodality imaging |
title | An unexpected and tumultuous diagnosis of a left atrial mass |
title_full | An unexpected and tumultuous diagnosis of a left atrial mass |
title_fullStr | An unexpected and tumultuous diagnosis of a left atrial mass |
title_full_unstemmed | An unexpected and tumultuous diagnosis of a left atrial mass |
title_short | An unexpected and tumultuous diagnosis of a left atrial mass |
title_sort | unexpected and tumultuous diagnosis of a left atrial mass |
topic | Cardiac imaging cardiac masses inflammatory myofibroblastic tumor multimodality imaging |
url | https://www.monaldi-archives.org/macd/article/view/3221 |
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