Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative Complications
The authors present a rare clinical case of a patient with Bardet-Biedl syndrome and chronic kidney disease, who reached end-stage renal disease (ESRD) and underwent a long-term hemodialysis treatment, during which infections with Hepatitis C Virus (HCV) infection and Cytomegalovirus (CMV) infection...
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| Format: | Article |
| Language: | English |
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Wiley
2019-01-01
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| Series: | Case Reports in Surgery |
| Online Access: | http://dx.doi.org/10.1155/2019/8983174 |
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| author | Georgi Yankov Teodora Mihalova Rosen Petkov Evgeni Mekov Stefka Yankova Danail Petrov |
| author_facet | Georgi Yankov Teodora Mihalova Rosen Petkov Evgeni Mekov Stefka Yankova Danail Petrov |
| author_sort | Georgi Yankov |
| collection | DOAJ |
| description | The authors present a rare clinical case of a patient with Bardet-Biedl syndrome and chronic kidney disease, who reached end-stage renal disease (ESRD) and underwent a long-term hemodialysis treatment, during which infections with Hepatitis C Virus (HCV) infection and Cytomegalovirus (CMV) infection were established. Kidney transplantation from an alive unrelated donor was performed. Later, an adenocarcinoma of the esophagus was diagnosed at an early stage, treated surgically with resection of the esophagus and gastroesophagoplasty afterward. Seven months later, a rare complication of the immunosuppressive therapy with Cyclosporin A occurred, which consisted of spontaneous bilateral pleural hemorrhage. The same, as well as the postoperative ventral hernia, was successfully resolved. Concomitant HCV was also treated. Rare autosomal recessive syndrome with severe complications, adenocarcinoma of the esophagus, spontaneous bilateral pleural hemorrhage after the operation, and successful treatment were discussed. |
| format | Article |
| id | doaj-art-53981425d84847218a21df7d63b711db |
| institution | Kabale University |
| issn | 2090-6900 2090-6919 |
| language | English |
| publishDate | 2019-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Surgery |
| spelling | doaj-art-53981425d84847218a21df7d63b711db2025-02-03T06:11:22ZengWileyCase Reports in Surgery2090-69002090-69192019-01-01201910.1155/2019/89831748983174Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative ComplicationsGeorgi Yankov0Teodora Mihalova1Rosen Petkov2Evgeni Mekov3Stefka Yankova4Danail Petrov5Department of Pulmonary Diseases, Medical Faculty, Medical University-Sofia, MHATPD “Sveta Sofia, ” 19, “Acad. Ivan Geshov” Blvd, BulgariaDepartment of Pulmonary Diseases, Medical Faculty, Medical University-Sofia, MHATPD “Sveta Sofia, ” 19, “Acad. Ivan Geshov” Blvd, BulgariaDepartment of Pulmonary Diseases, Medical Faculty, Medical University-Sofia, MHATPD “Sveta Sofia, ” 19, “Acad. Ivan Geshov” Blvd, BulgariaDepartment of Pulmonary Diseases, Medical Faculty, Medical University-Sofia, MHATPD “Sveta Sofia, ” 19, “Acad. Ivan Geshov” Blvd, BulgariaDepartment of Nephrology and Hemodialysis “Prof. I. Mitеv, ” Medical Faculty, Medical University-Sofia, 11, “Acad. Ivan Geshov” Blvd, BulgariaDepartment of Pulmonary Diseases, Medical Faculty, Medical University-Sofia, MHATPD “Sveta Sofia, ” 19, “Acad. Ivan Geshov” Blvd, BulgariaThe authors present a rare clinical case of a patient with Bardet-Biedl syndrome and chronic kidney disease, who reached end-stage renal disease (ESRD) and underwent a long-term hemodialysis treatment, during which infections with Hepatitis C Virus (HCV) infection and Cytomegalovirus (CMV) infection were established. Kidney transplantation from an alive unrelated donor was performed. Later, an adenocarcinoma of the esophagus was diagnosed at an early stage, treated surgically with resection of the esophagus and gastroesophagoplasty afterward. Seven months later, a rare complication of the immunosuppressive therapy with Cyclosporin A occurred, which consisted of spontaneous bilateral pleural hemorrhage. The same, as well as the postoperative ventral hernia, was successfully resolved. Concomitant HCV was also treated. Rare autosomal recessive syndrome with severe complications, adenocarcinoma of the esophagus, spontaneous bilateral pleural hemorrhage after the operation, and successful treatment were discussed.http://dx.doi.org/10.1155/2019/8983174 |
| spellingShingle | Georgi Yankov Teodora Mihalova Rosen Petkov Evgeni Mekov Stefka Yankova Danail Petrov Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative Complications Case Reports in Surgery |
| title | Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative Complications |
| title_full | Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative Complications |
| title_fullStr | Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative Complications |
| title_full_unstemmed | Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative Complications |
| title_short | Bardet-Biedl Syndrome with a Kidney Transplant, Esophageal Adenocarcinoma, and Postoperative Complications |
| title_sort | bardet biedl syndrome with a kidney transplant esophageal adenocarcinoma and postoperative complications |
| url | http://dx.doi.org/10.1155/2019/8983174 |
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