When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic Sclerosis
Systemic sclerosis is a multisystem disease featured with autoimmunity and organ fibrosis. Although gastrointestinal (GI) tract involvement is common in patients with systemic sclerosis, colonic perforation is extremely rare. Benign pneumatosis intestinalis, a phenomenon more frequently seen in rheu...
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Format: | Article |
Language: | English |
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Wiley
2018-01-01
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Series: | Case Reports in Gastrointestinal Medicine |
Online Access: | http://dx.doi.org/10.1155/2018/5124145 |
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author | Jian Guan Alvina Munaf Alric V. Simmonds Irteza Inayat |
author_facet | Jian Guan Alvina Munaf Alric V. Simmonds Irteza Inayat |
author_sort | Jian Guan |
collection | DOAJ |
description | Systemic sclerosis is a multisystem disease featured with autoimmunity and organ fibrosis. Although gastrointestinal (GI) tract involvement is common in patients with systemic sclerosis, colonic perforation is extremely rare. Benign pneumatosis intestinalis, a phenomenon more frequently seen in rheumatologic conditions, makes the diagnosis of colonic perforation even more challenging. We report a unique case of colonic perforation in a patient with chronic systemic sclerosis. This patient initially presented with mild abdominal pain and hematemesis. Urgent upper endoscopy was unremarkable and radiology showed stable pneumatosis intestinalis. Due to worsening abdominal pain, laparotomy exploration was performed and colonic perforation with transmural ischemic necrosis was found. |
format | Article |
id | doaj-art-4e9a02c85e0b4740b199e68827ae8963 |
institution | Kabale University |
issn | 2090-6528 2090-6536 |
language | English |
publishDate | 2018-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Gastrointestinal Medicine |
spelling | doaj-art-4e9a02c85e0b4740b199e68827ae89632025-02-03T07:26:01ZengWileyCase Reports in Gastrointestinal Medicine2090-65282090-65362018-01-01201810.1155/2018/51241455124145When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic SclerosisJian Guan0Alvina Munaf1Alric V. Simmonds2Irteza Inayat3Department of Internal Medicine, Graduate Medical Education, Florida Hospital, 2501 N. Orange Suite 235, Orlando, FL 32804, USADepartment of Internal Medicine, Graduate Medical Education, Florida Hospital, 2501 N. Orange Suite 235, Orlando, FL 32804, USADepartment of General Surgery, Graduate Medical Education, Florida Hospital, 2415 N. Orange Ave., Suite 400, Orlando, FL 32804, USACentral Florida Hepatology & Gastroenterology, Florida Hospital, 2415 N. Orange Ave., Suite 200, Orlando, FL 32804, USASystemic sclerosis is a multisystem disease featured with autoimmunity and organ fibrosis. Although gastrointestinal (GI) tract involvement is common in patients with systemic sclerosis, colonic perforation is extremely rare. Benign pneumatosis intestinalis, a phenomenon more frequently seen in rheumatologic conditions, makes the diagnosis of colonic perforation even more challenging. We report a unique case of colonic perforation in a patient with chronic systemic sclerosis. This patient initially presented with mild abdominal pain and hematemesis. Urgent upper endoscopy was unremarkable and radiology showed stable pneumatosis intestinalis. Due to worsening abdominal pain, laparotomy exploration was performed and colonic perforation with transmural ischemic necrosis was found.http://dx.doi.org/10.1155/2018/5124145 |
spellingShingle | Jian Guan Alvina Munaf Alric V. Simmonds Irteza Inayat When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic Sclerosis Case Reports in Gastrointestinal Medicine |
title | When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic Sclerosis |
title_full | When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic Sclerosis |
title_fullStr | When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic Sclerosis |
title_full_unstemmed | When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic Sclerosis |
title_short | When the Benign Pneumatosis Intestinalis Becomes No Longer Benign: A Rare Case of Bowel Perforation in a Patient with Systemic Sclerosis |
title_sort | when the benign pneumatosis intestinalis becomes no longer benign a rare case of bowel perforation in a patient with systemic sclerosis |
url | http://dx.doi.org/10.1155/2018/5124145 |
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