Atypical Vascular Involvement in a Case of Behçet's Disease
Introduction. Behçet's disease (BD) is a form of vasculitis of unknown etiology which is rare in our environment. It is characterized by a variety of clinical manifestations and usually affects young adults. Recurrent oral and genital ulcers are a characteristic and extremely frequent symptom,...
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| Format: | Article |
| Language: | English |
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Wiley
2012-01-01
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| Series: | Case Reports in Surgery |
| Online Access: | http://dx.doi.org/10.1155/2012/848101 |
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| author | Alejandro Rodríguez Morata Ana Hidalgo Conde Carlos de la Cruz Cosme Susana Gómez Ramírez Rafael Gómez Medialdea |
| author_facet | Alejandro Rodríguez Morata Ana Hidalgo Conde Carlos de la Cruz Cosme Susana Gómez Ramírez Rafael Gómez Medialdea |
| author_sort | Alejandro Rodríguez Morata |
| collection | DOAJ |
| description | Introduction. Behçet's disease (BD) is a form of vasculitis of unknown etiology which is rare in our environment. It is characterized by a variety of clinical manifestations and usually affects young adults. Recurrent oral and genital ulcers are a characteristic and extremely frequent symptom, but mortality is linked with more significant symptoms such as aortic pseudoaneurysm, pulmonary pseudoaneurysm, and cerebral venous thrombosis. Patient and Method. We present a case of a young male with atypical BD and severe polyvascular involvement (previous cerebral venous thrombosis and current peripheral venous thrombosis, acute ischemia, and peripheral arterial pseudoaneurysm) who required urgent surgical intervention due to a symptomatic external iliac pseudoaneurysm. Result. The pseudoaneurysm was successfully treated, we performed an iliofemoral bypass, and we treated it with steroids and immunosuppressive therapy. Conclusions. These rare clinical manifestations highlight the importance of considering BD in young patients, even in usual cases of vascular intervention, whether arterial or venous in nature. |
| format | Article |
| id | doaj-art-4da34d6c00c74487b4879a34e69429fa |
| institution | Kabale University |
| issn | 2090-6900 2090-6919 |
| language | English |
| publishDate | 2012-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Surgery |
| spelling | doaj-art-4da34d6c00c74487b4879a34e69429fa2025-02-03T06:12:12ZengWileyCase Reports in Surgery2090-69002090-69192012-01-01201210.1155/2012/848101848101Atypical Vascular Involvement in a Case of Behçet's DiseaseAlejandro Rodríguez Morata0Ana Hidalgo Conde1Carlos de la Cruz Cosme2Susana Gómez Ramírez3Rafael Gómez Medialdea4Department of Angiology and Vascular Surgery, Hospital Virgen de la Victoria, Campus de Teatinos s/n, 29010 Málaga, SpainDepartment of Internal Medicine, Hospital Virgen de la Victoria, Campus de Teatinos s/n, 29010 Málaga, SpainDepartment of Neurology, Hospital Virgen de la Victoria, Campus de Teatinos s/n, 29010 Málaga, SpainDepartment of Internal Medicine, Hospital Virgen de la Victoria, Campus de Teatinos s/n, 29010 Málaga, SpainDepartment of Angiology and Vascular Surgery, Hospital Virgen de la Victoria, Campus de Teatinos s/n, 29010 Málaga, SpainIntroduction. Behçet's disease (BD) is a form of vasculitis of unknown etiology which is rare in our environment. It is characterized by a variety of clinical manifestations and usually affects young adults. Recurrent oral and genital ulcers are a characteristic and extremely frequent symptom, but mortality is linked with more significant symptoms such as aortic pseudoaneurysm, pulmonary pseudoaneurysm, and cerebral venous thrombosis. Patient and Method. We present a case of a young male with atypical BD and severe polyvascular involvement (previous cerebral venous thrombosis and current peripheral venous thrombosis, acute ischemia, and peripheral arterial pseudoaneurysm) who required urgent surgical intervention due to a symptomatic external iliac pseudoaneurysm. Result. The pseudoaneurysm was successfully treated, we performed an iliofemoral bypass, and we treated it with steroids and immunosuppressive therapy. Conclusions. These rare clinical manifestations highlight the importance of considering BD in young patients, even in usual cases of vascular intervention, whether arterial or venous in nature.http://dx.doi.org/10.1155/2012/848101 |
| spellingShingle | Alejandro Rodríguez Morata Ana Hidalgo Conde Carlos de la Cruz Cosme Susana Gómez Ramírez Rafael Gómez Medialdea Atypical Vascular Involvement in a Case of Behçet's Disease Case Reports in Surgery |
| title | Atypical Vascular Involvement in a Case of Behçet's Disease |
| title_full | Atypical Vascular Involvement in a Case of Behçet's Disease |
| title_fullStr | Atypical Vascular Involvement in a Case of Behçet's Disease |
| title_full_unstemmed | Atypical Vascular Involvement in a Case of Behçet's Disease |
| title_short | Atypical Vascular Involvement in a Case of Behçet's Disease |
| title_sort | atypical vascular involvement in a case of behcet s disease |
| url | http://dx.doi.org/10.1155/2012/848101 |
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