Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special Considerations

Intestinal malrotation usually presents in the pediatric population with midgut volvulus requiring emergency Ladd’s procedure. Rarely, it remains asymptomatic and is discovered incidentally only during adulthood when it seldom causes intestinal complications. The scenario of a cirrhotic adult being...

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Main Authors: Vatche Melkonian, Pablo Quadri, Chintalapati R. Varma, Mustafa Nazzal, Henry B. Randall, Minh-Tri J. P. Nguyen
Format: Article
Language:English
Published: Wiley 2020-01-01
Series:Case Reports in Surgery
Online Access:http://dx.doi.org/10.1155/2020/4196012
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author Vatche Melkonian
Pablo Quadri
Chintalapati R. Varma
Mustafa Nazzal
Henry B. Randall
Minh-Tri J. P. Nguyen
author_facet Vatche Melkonian
Pablo Quadri
Chintalapati R. Varma
Mustafa Nazzal
Henry B. Randall
Minh-Tri J. P. Nguyen
author_sort Vatche Melkonian
collection DOAJ
description Intestinal malrotation usually presents in the pediatric population with midgut volvulus requiring emergency Ladd’s procedure. Rarely, it remains asymptomatic and is discovered incidentally only during adulthood when it seldom causes intestinal complications. The scenario of a cirrhotic adult being diagnosed with asymptomatic intestinal malrotation with subsequent intestinal complications is thus extremely rare and to our knowledge has not been previously reported. We describe a 56-year-old man with decompensated alcoholic cirrhosis (Child-Pugh class C, MELD score 22) who was initially observed after an incidental diagnosis of intestinal malrotation on computed tomography. Observation continued as his liver disease improved with alcohol cessation (Child-Pugh class A, MELD score 8). He later presented with a closed loop bowel obstruction secondary to midgut volvulus at the time of alcohol relapse and liver redecompensation (Child-Pugh class C, MELD score 22-29). He underwent emergency Ladd’s procedure during which his midjejunum was volvulized into an internal hernia space created by a thick Ladd’s band containing large varices. The postoperative course was complicated by ileus and loculated bacterial peritonitis. Based on our experience, we discuss special considerations with regard to the surgical technique and timing of Ladd’s procedure when encountering intestinal malrotation in a cirrhotic adult with portal hypertension.
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spelling doaj-art-4c775dea4635438fa773346e263e9a632025-02-03T01:04:47ZengWileyCase Reports in Surgery2090-69002090-69192020-01-01202010.1155/2020/41960124196012Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special ConsiderationsVatche Melkonian0Pablo Quadri1Chintalapati R. Varma2Mustafa Nazzal3Henry B. Randall4Minh-Tri J. P. Nguyen5Division of Abdominal Transplant, Department of Surgery, Saint Louis University, Saint Louis, MO, USADivision of Abdominal Transplant, Department of Surgery, Saint Louis University, Saint Louis, MO, USADivision of Abdominal Transplant, Department of Surgery, Saint Louis University, Saint Louis, MO, USADivision of Abdominal Transplant, Department of Surgery, Saint Louis University, Saint Louis, MO, USADivision of Abdominal Transplant, Department of Surgery, Saint Louis University, Saint Louis, MO, USADivision of Abdominal Transplant, Department of Surgery, Saint Louis University, Saint Louis, MO, USAIntestinal malrotation usually presents in the pediatric population with midgut volvulus requiring emergency Ladd’s procedure. Rarely, it remains asymptomatic and is discovered incidentally only during adulthood when it seldom causes intestinal complications. The scenario of a cirrhotic adult being diagnosed with asymptomatic intestinal malrotation with subsequent intestinal complications is thus extremely rare and to our knowledge has not been previously reported. We describe a 56-year-old man with decompensated alcoholic cirrhosis (Child-Pugh class C, MELD score 22) who was initially observed after an incidental diagnosis of intestinal malrotation on computed tomography. Observation continued as his liver disease improved with alcohol cessation (Child-Pugh class A, MELD score 8). He later presented with a closed loop bowel obstruction secondary to midgut volvulus at the time of alcohol relapse and liver redecompensation (Child-Pugh class C, MELD score 22-29). He underwent emergency Ladd’s procedure during which his midjejunum was volvulized into an internal hernia space created by a thick Ladd’s band containing large varices. The postoperative course was complicated by ileus and loculated bacterial peritonitis. Based on our experience, we discuss special considerations with regard to the surgical technique and timing of Ladd’s procedure when encountering intestinal malrotation in a cirrhotic adult with portal hypertension.http://dx.doi.org/10.1155/2020/4196012
spellingShingle Vatche Melkonian
Pablo Quadri
Chintalapati R. Varma
Mustafa Nazzal
Henry B. Randall
Minh-Tri J. P. Nguyen
Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special Considerations
Case Reports in Surgery
title Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special Considerations
title_full Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special Considerations
title_fullStr Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special Considerations
title_full_unstemmed Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special Considerations
title_short Asymptomatic Intestinal Malrotation Progressing to Midgut Volvulus in a Decompensated Alcoholic Cirrhotic Adult: A Rare Scenario Requiring Special Considerations
title_sort asymptomatic intestinal malrotation progressing to midgut volvulus in a decompensated alcoholic cirrhotic adult a rare scenario requiring special considerations
url http://dx.doi.org/10.1155/2020/4196012
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