A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy

The aortopulmonary window (APW) is an abnormal communication between the ascending aorta and the pulmonary trunk in the presence of two separate semilunar valves. It is a rare congenital malformation which represents 0.1% of all congenital cardiac diseases. Herein, we report a very rare case of 27-y...

Full description

Saved in:
Bibliographic Details
Main Authors: Murat Kose, Serra Ucar, Samim Emet, Timur Selcuk Akpinar, Kıvanc Yalin
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:Case Reports in Cardiology
Online Access:http://dx.doi.org/10.1155/2015/935253
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1832556181005008896
author Murat Kose
Serra Ucar
Samim Emet
Timur Selcuk Akpinar
Kıvanc Yalin
author_facet Murat Kose
Serra Ucar
Samim Emet
Timur Selcuk Akpinar
Kıvanc Yalin
author_sort Murat Kose
collection DOAJ
description The aortopulmonary window (APW) is an abnormal communication between the ascending aorta and the pulmonary trunk in the presence of two separate semilunar valves. It is a rare congenital malformation which represents 0.1% of all congenital cardiac diseases. Herein, we report a very rare case of 27-year-old patient with unrepaired APW causing Eisenmenger syndrome and pulmonary hypertension who was asymptomatic until her first pregnancy. The median survival of uncorrected APW is 33 years. Aortopulmonary window is a very rare congenital anomaly. To our knowledge, asymptomatic adult case has not been reported until now. APW should be considered in the differential diagnosis of the severe pulmonary hypertension also in adult patients.
format Article
id doaj-art-4717d02f237340159ec048c1b9a23bf4
institution Kabale University
issn 2090-6404
2090-6412
language English
publishDate 2015-01-01
publisher Wiley
record_format Article
series Case Reports in Cardiology
spelling doaj-art-4717d02f237340159ec048c1b9a23bf42025-02-03T05:46:00ZengWileyCase Reports in Cardiology2090-64042090-64122015-01-01201510.1155/2015/935253935253A Case of Aortopulmonary Window: Asymptomatic until the First PregnancyMurat Kose0Serra Ucar1Samim Emet2Timur Selcuk Akpinar3Kıvanc Yalin4Department of Internal Medicine, Istanbul University Istanbul Medical Faculty, TurkeyDepartment of Nephrology, Istanbul University Istanbul Medical Faculty, TurkeyDepartment of Cardiology, Istanbul University Istanbul Medical Faculty, TurkeyDepartment of Internal Medicine, Istanbul University Istanbul Medical Faculty, TurkeyDepartment of Cardiology, Istanbul University Istanbul Medical Faculty, TurkeyThe aortopulmonary window (APW) is an abnormal communication between the ascending aorta and the pulmonary trunk in the presence of two separate semilunar valves. It is a rare congenital malformation which represents 0.1% of all congenital cardiac diseases. Herein, we report a very rare case of 27-year-old patient with unrepaired APW causing Eisenmenger syndrome and pulmonary hypertension who was asymptomatic until her first pregnancy. The median survival of uncorrected APW is 33 years. Aortopulmonary window is a very rare congenital anomaly. To our knowledge, asymptomatic adult case has not been reported until now. APW should be considered in the differential diagnosis of the severe pulmonary hypertension also in adult patients.http://dx.doi.org/10.1155/2015/935253
spellingShingle Murat Kose
Serra Ucar
Samim Emet
Timur Selcuk Akpinar
Kıvanc Yalin
A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy
Case Reports in Cardiology
title A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy
title_full A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy
title_fullStr A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy
title_full_unstemmed A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy
title_short A Case of Aortopulmonary Window: Asymptomatic until the First Pregnancy
title_sort case of aortopulmonary window asymptomatic until the first pregnancy
url http://dx.doi.org/10.1155/2015/935253
work_keys_str_mv AT muratkose acaseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT serraucar acaseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT samimemet acaseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT timurselcukakpinar acaseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT kıvancyalin acaseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT muratkose caseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT serraucar caseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT samimemet caseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT timurselcukakpinar caseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy
AT kıvancyalin caseofaortopulmonarywindowasymptomaticuntilthefirstpregnancy