Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT
Fibromuscular Dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disorder predominantly affecting women aged 18 to 65 years. This case report highlights a 74-year-old female diagnosed with FMD incidentally during evaluation for deep vein thrombosis (DVT). Imaging revealed significant...
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Elsevier
2025-03-01
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author | Abderrahmane Ibenyahia, MD Oumaima Elkaddouri, MD Mounir Salek, MD Salma Boustani, MD Soufiane Bigi, MD Said Adnor, MD Wassila Bouissar, MD Soukaina Wakrim, MD |
author_facet | Abderrahmane Ibenyahia, MD Oumaima Elkaddouri, MD Mounir Salek, MD Salma Boustani, MD Soufiane Bigi, MD Said Adnor, MD Wassila Bouissar, MD Soukaina Wakrim, MD |
author_sort | Abderrahmane Ibenyahia, MD |
collection | DOAJ |
description | Fibromuscular Dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disorder predominantly affecting women aged 18 to 65 years. This case report highlights a 74-year-old female diagnosed with FMD incidentally during evaluation for deep vein thrombosis (DVT). Imaging revealed significant vascular anomalies, including a giant intracranial carotid aneurysm and a hypoplastic iliac vein with extensive collateral formation. Early detection and tailored management are crucial to prevent complications such as arterial dissections, aneurysms, and stroke. The patient showed favorable evolution without anticoagulation therapy, and interventional embolization was planned to mitigate rupture risks. Differential diagnosis includes atherosclerotic aneurysms, Ehlers-Danlos syndrome, Marfan syndrome, neurofibromatosis type 1, and polyarteritis nodosa, which must be distinguished through comprehensive imaging and clinical evaluation. The prognosis of FMD varies widely and depends on the extent and location of arterial involvement. This case underscores the importance of advanced imaging in accurately diagnosing and guiding long-term follow-up for FMD management. |
format | Article |
id | doaj-art-45ce22f7251f4eb093f4c26074ef74cb |
institution | Kabale University |
issn | 1930-0433 |
language | English |
publishDate | 2025-03-01 |
publisher | Elsevier |
record_format | Article |
series | Radiology Case Reports |
spelling | doaj-art-45ce22f7251f4eb093f4c26074ef74cb2025-01-18T05:04:07ZengElsevierRadiology Case Reports1930-04332025-03-0120316311636Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVTAbderrahmane Ibenyahia, MD0Oumaima Elkaddouri, MD1Mounir Salek, MD2Salma Boustani, MD3Soufiane Bigi, MD4Said Adnor, MD5Wassila Bouissar, MD6Soukaina Wakrim, MD7Radiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, Morocco; Corresponding author.Department of Internal Medicine, Faculty of Medicine and Pharmacy of Agadir, University Ibn Zohr, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoDepartment of Internal Medicine, Faculty of Medicine and Pharmacy of Agadir, University Ibn Zohr, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoDepartment of Internal Medicine, Faculty of Medicine and Pharmacy of Agadir, University Ibn Zohr, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoFibromuscular Dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disorder predominantly affecting women aged 18 to 65 years. This case report highlights a 74-year-old female diagnosed with FMD incidentally during evaluation for deep vein thrombosis (DVT). Imaging revealed significant vascular anomalies, including a giant intracranial carotid aneurysm and a hypoplastic iliac vein with extensive collateral formation. Early detection and tailored management are crucial to prevent complications such as arterial dissections, aneurysms, and stroke. The patient showed favorable evolution without anticoagulation therapy, and interventional embolization was planned to mitigate rupture risks. Differential diagnosis includes atherosclerotic aneurysms, Ehlers-Danlos syndrome, Marfan syndrome, neurofibromatosis type 1, and polyarteritis nodosa, which must be distinguished through comprehensive imaging and clinical evaluation. The prognosis of FMD varies widely and depends on the extent and location of arterial involvement. This case underscores the importance of advanced imaging in accurately diagnosing and guiding long-term follow-up for FMD management.http://www.sciencedirect.com/science/article/pii/S1930043324013803Fibromuscular dysplasiaFMDGiant carotid aneurysmBuds pearl signHypoplastic iliac veinBone island |
spellingShingle | Abderrahmane Ibenyahia, MD Oumaima Elkaddouri, MD Mounir Salek, MD Salma Boustani, MD Soufiane Bigi, MD Said Adnor, MD Wassila Bouissar, MD Soukaina Wakrim, MD Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT Radiology Case Reports Fibromuscular dysplasia FMD Giant carotid aneurysm Buds pearl sign Hypoplastic iliac vein Bone island |
title | Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT |
title_full | Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT |
title_fullStr | Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT |
title_full_unstemmed | Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT |
title_short | Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT |
title_sort | radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected dvt |
topic | Fibromuscular dysplasia FMD Giant carotid aneurysm Buds pearl sign Hypoplastic iliac vein Bone island |
url | http://www.sciencedirect.com/science/article/pii/S1930043324013803 |
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