Small intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)

Abstract Variant transthyretin amyloidosis (A-ATTRv) can lead to sensory, motor, and autonomic neuropathy, as well as a variety of gastrointestinal (GI) disorders. While previous studies have explored gastrointestinal symptoms in A-ATTRv, no studies have definitively examined the role of bacterial o...

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Main Authors: Ana Moreno García, Mireia Grimalt Oliver, Juan González-Moreno, María Antonia Ribot-Sansó, Eugenia Cisneros-Barroso, Inés Losada López
Format: Article
Language:English
Published: BMC 2025-05-01
Series:Orphanet Journal of Rare Diseases
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Online Access:https://doi.org/10.1186/s13023-025-03727-y
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author Ana Moreno García
Mireia Grimalt Oliver
Juan González-Moreno
María Antonia Ribot-Sansó
Eugenia Cisneros-Barroso
Inés Losada López
author_facet Ana Moreno García
Mireia Grimalt Oliver
Juan González-Moreno
María Antonia Ribot-Sansó
Eugenia Cisneros-Barroso
Inés Losada López
author_sort Ana Moreno García
collection DOAJ
description Abstract Variant transthyretin amyloidosis (A-ATTRv) can lead to sensory, motor, and autonomic neuropathy, as well as a variety of gastrointestinal (GI) disorders. While previous studies have explored gastrointestinal symptoms in A-ATTRv, no studies have definitively examined the role of bacterial overgrowth, such as SIBO, in exacerbating these symptoms. Identifying the presence of SIBO in A-ATTRv patients could lead to better-targeted treatments for gastrointestinal complications. We conducted a cross-sectional, unicentric observational pilot study, analysing the presence of SIBO using a lactitol breath test in 39 individuals carrying the V30M mutation: 21 asymptomatic carriers and 18 patients with A-ATTRv. We did not find a higher prevalence of SIBO, among patients with A-ATTRv compared to asymptomatic carriers. Though no significant relationship between SIBO and A-ATTRv was found, notable differences in gastrointestinal symptoms suggest these may be independent of SIBO. Furthermore, no relationship was found between the presence of SIBO and gender. Given the limitations of this pilot study, we did not find a relationship between A-ATTRv and intestinal microbiota disorders. Future research with larger sample sizes and more sensitive diagnostic tools is required to further explore this potential link.
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spelling doaj-art-451fd57e394d405c92c926f15e6576122025-08-20T01:47:30ZengBMCOrphanet Journal of Rare Diseases1750-11722025-05-012011910.1186/s13023-025-03727-ySmall intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)Ana Moreno García0Mireia Grimalt Oliver1Juan González-Moreno2María Antonia Ribot-Sansó3Eugenia Cisneros-Barroso4Inés Losada López5Universitat de les Illes BalearsEndocrinology and Nutrition, Hospital Universitario Son LlàtzerSudden Death and TTR Amyloidosis, Balearic Research Group in Genetic Cardiopathies, Health Research Institute of the Balearic Islands (IdISBa)Sudden Death and TTR Amyloidosis, Balearic Research Group in Genetic Cardiopathies, Health Research Institute of the Balearic Islands (IdISBa)Sudden Death and TTR Amyloidosis, Balearic Research Group in Genetic Cardiopathies, Health Research Institute of the Balearic Islands (IdISBa)Sudden Death and TTR Amyloidosis, Balearic Research Group in Genetic Cardiopathies, Health Research Institute of the Balearic Islands (IdISBa)Abstract Variant transthyretin amyloidosis (A-ATTRv) can lead to sensory, motor, and autonomic neuropathy, as well as a variety of gastrointestinal (GI) disorders. While previous studies have explored gastrointestinal symptoms in A-ATTRv, no studies have definitively examined the role of bacterial overgrowth, such as SIBO, in exacerbating these symptoms. Identifying the presence of SIBO in A-ATTRv patients could lead to better-targeted treatments for gastrointestinal complications. We conducted a cross-sectional, unicentric observational pilot study, analysing the presence of SIBO using a lactitol breath test in 39 individuals carrying the V30M mutation: 21 asymptomatic carriers and 18 patients with A-ATTRv. We did not find a higher prevalence of SIBO, among patients with A-ATTRv compared to asymptomatic carriers. Though no significant relationship between SIBO and A-ATTRv was found, notable differences in gastrointestinal symptoms suggest these may be independent of SIBO. Furthermore, no relationship was found between the presence of SIBO and gender. Given the limitations of this pilot study, we did not find a relationship between A-ATTRv and intestinal microbiota disorders. Future research with larger sample sizes and more sensitive diagnostic tools is required to further explore this potential link.https://doi.org/10.1186/s13023-025-03727-yATTRTransthyretin amyloidosisSmall intestine bacterial overgrowthDigestive symptomsBreath test
spellingShingle Ana Moreno García
Mireia Grimalt Oliver
Juan González-Moreno
María Antonia Ribot-Sansó
Eugenia Cisneros-Barroso
Inés Losada López
Small intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)
Orphanet Journal of Rare Diseases
ATTR
Transthyretin amyloidosis
Small intestine bacterial overgrowth
Digestive symptoms
Breath test
title Small intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)
title_full Small intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)
title_fullStr Small intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)
title_full_unstemmed Small intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)
title_short Small intestinal bacterial overgrowth in variant transthyretin amyloidosis (A-ATTRv)
title_sort small intestinal bacterial overgrowth in variant transthyretin amyloidosis a attrv
topic ATTR
Transthyretin amyloidosis
Small intestine bacterial overgrowth
Digestive symptoms
Breath test
url https://doi.org/10.1186/s13023-025-03727-y
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