Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate Diagnosis

Raghib Syndrome is a rare developmental complex, which consists of persistence of the left superior vena cava (PLSVC) along with coronary sinus ostial atresia and atrial septal defect. This Raghib complex anomaly has also been associated with other congenital malformations including ventricular sept...

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Main Authors: Vistasp J. Daruwalla, Keyur Parekh, Hassan Tahir, Jeremy D. Collins, James Carr
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:Case Reports in Cardiology
Online Access:http://dx.doi.org/10.1155/2015/921247
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author Vistasp J. Daruwalla
Keyur Parekh
Hassan Tahir
Jeremy D. Collins
James Carr
author_facet Vistasp J. Daruwalla
Keyur Parekh
Hassan Tahir
Jeremy D. Collins
James Carr
author_sort Vistasp J. Daruwalla
collection DOAJ
description Raghib Syndrome is a rare developmental complex, which consists of persistence of the left superior vena cava (PLSVC) along with coronary sinus ostial atresia and atrial septal defect. This Raghib complex anomaly has also been associated with other congenital malformations including ventricular septal defects, enlargement of the tricuspid annulus, and pulmonary stenosis. Our case demonstrates an isolated PLSVC draining into the left atrium along with coronary sinus atresia in a young patient presenting with cryptogenic stroke without the atrial septal defect. Majority of the cases reported in the literature were found to have the lesion during the postmortem evaluation or were characterized at angiography and/or echocardiography. We stress the importance of modern day imaging like the computed tomography (CT) angiography and cardiac MRI in diagnosis and surgical management of such rare lesions leading to cryptogenic strokes.
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institution Kabale University
issn 2090-6404
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publisher Wiley
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series Case Reports in Cardiology
spelling doaj-art-435b637e79314d518adcc0d400b41ad02025-02-03T01:32:40ZengWileyCase Reports in Cardiology2090-64042090-64122015-01-01201510.1155/2015/921247921247Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate DiagnosisVistasp J. Daruwalla0Keyur Parekh1Hassan Tahir2Jeremy D. Collins3James Carr4Conemaugh Memorial Hospital/Temple University, USADepartment of Cardiovascular Radiology, Northwestern University Feinberg School of Medicine, USAConemaugh Memorial Hospital/Temple University, USADepartment of Cardiovascular Radiology, Northwestern University Feinberg School of Medicine, USADepartment of Cardiovascular Radiology, Northwestern University Feinberg School of Medicine, USARaghib Syndrome is a rare developmental complex, which consists of persistence of the left superior vena cava (PLSVC) along with coronary sinus ostial atresia and atrial septal defect. This Raghib complex anomaly has also been associated with other congenital malformations including ventricular septal defects, enlargement of the tricuspid annulus, and pulmonary stenosis. Our case demonstrates an isolated PLSVC draining into the left atrium along with coronary sinus atresia in a young patient presenting with cryptogenic stroke without the atrial septal defect. Majority of the cases reported in the literature were found to have the lesion during the postmortem evaluation or were characterized at angiography and/or echocardiography. We stress the importance of modern day imaging like the computed tomography (CT) angiography and cardiac MRI in diagnosis and surgical management of such rare lesions leading to cryptogenic strokes.http://dx.doi.org/10.1155/2015/921247
spellingShingle Vistasp J. Daruwalla
Keyur Parekh
Hassan Tahir
Jeremy D. Collins
James Carr
Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate Diagnosis
Case Reports in Cardiology
title Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate Diagnosis
title_full Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate Diagnosis
title_fullStr Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate Diagnosis
title_full_unstemmed Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate Diagnosis
title_short Raghib Syndrome Presenting as a Cryptogenic Stroke: Role of Cardiac MRI in Accurate Diagnosis
title_sort raghib syndrome presenting as a cryptogenic stroke role of cardiac mri in accurate diagnosis
url http://dx.doi.org/10.1155/2015/921247
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