Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy)
Intestinal epithelial dysplasia (tufting enteropathy) is an uncommon congenital disorder. Furthermore, its association with chronic inflammatory arthropathy is rarely documented in the literature. Low prevalence rates of 1 in 100,000 live births in Western Europe exist, with higher rates in North Af...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Orthopedics |
| Online Access: | http://dx.doi.org/10.1155/2018/4630759 |
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| _version_ | 1832562597599117312 |
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| author | Colin Ng Kurt Magri Ryan Giordmaina Duncan Whitwell |
| author_facet | Colin Ng Kurt Magri Ryan Giordmaina Duncan Whitwell |
| author_sort | Colin Ng |
| collection | DOAJ |
| description | Intestinal epithelial dysplasia (tufting enteropathy) is an uncommon congenital disorder. Furthermore, its association with chronic inflammatory arthropathy is rarely documented in the literature. Low prevalence rates of 1 in 100,000 live births in Western Europe exist, with higher rates in North Africa and Middle Eastern countries. Malta, being a small Mediterranean island at the cusp between Europe and North Africa, has an anecdotal sevenfold prevalence rate. This is the first documented case report of a patient with both intestinal epithelial dysplasia and severe bilateral hip and knee arthropathy that required simultaneous bilateral hip followed by, after a short interval, unilateral knee arthroplasties. Our aim is to highlight the rapid progression of associated arthropathy as well as the successful treatment with joint arthroplasties in such extreme cases. Surgical treatment may be a necessity despite best medical efforts to halt the disease. |
| format | Article |
| id | doaj-art-42e2f976f5804b78a9efd60d162cbf0c |
| institution | Kabale University |
| issn | 2090-6749 2090-6757 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Orthopedics |
| spelling | doaj-art-42e2f976f5804b78a9efd60d162cbf0c2025-02-03T01:22:11ZengWileyCase Reports in Orthopedics2090-67492090-67572018-01-01201810.1155/2018/46307594630759Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy)Colin Ng0Kurt Magri1Ryan Giordmaina2Duncan Whitwell3Department of Trauma and Orthopaedics, Mater Dei Hospital, Triq Dun Karm, MSD 2090 Msida, MaltaDepartment of General Medicine, Mater Dei Hospital, Triq Dun Karm, MSD 2090 Msida, MaltaDepartment of Trauma and Orthopaedics, Mater Dei Hospital, Triq Dun Karm, MSD 2090 Msida, MaltaConsultant Orthopaedic Tumour and Reconstructive Surgeon, Nuffield Orthopaedic Hospital, Oxford, UKIntestinal epithelial dysplasia (tufting enteropathy) is an uncommon congenital disorder. Furthermore, its association with chronic inflammatory arthropathy is rarely documented in the literature. Low prevalence rates of 1 in 100,000 live births in Western Europe exist, with higher rates in North Africa and Middle Eastern countries. Malta, being a small Mediterranean island at the cusp between Europe and North Africa, has an anecdotal sevenfold prevalence rate. This is the first documented case report of a patient with both intestinal epithelial dysplasia and severe bilateral hip and knee arthropathy that required simultaneous bilateral hip followed by, after a short interval, unilateral knee arthroplasties. Our aim is to highlight the rapid progression of associated arthropathy as well as the successful treatment with joint arthroplasties in such extreme cases. Surgical treatment may be a necessity despite best medical efforts to halt the disease.http://dx.doi.org/10.1155/2018/4630759 |
| spellingShingle | Colin Ng Kurt Magri Ryan Giordmaina Duncan Whitwell Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy) Case Reports in Orthopedics |
| title | Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy) |
| title_full | Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy) |
| title_fullStr | Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy) |
| title_full_unstemmed | Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy) |
| title_short | Bilateral Total Hip and Unilateral Knee Arthroplasties in a Young Adult with Arthropathy-Associated Intestinal Epithelial Dysplasia (Tufting Enteropathy) |
| title_sort | bilateral total hip and unilateral knee arthroplasties in a young adult with arthropathy associated intestinal epithelial dysplasia tufting enteropathy |
| url | http://dx.doi.org/10.1155/2018/4630759 |
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