Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the Literature

The dropped head syndrome (DHS) is a disabling condition caused by severe weakness of the neck extensor muscles causing progressive reducible kyphosis of the cervical spine and the inability to hold the head up. Weakness can occur in isolation or in association with a generalized neuromuscular disor...

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Main Authors: Abolfazl Rahimizadeh, Housain F. Soufiani, Saghayegh Rahimizadeh
Format: Article
Language:English
Published: Wiley 2016-01-01
Series:Case Reports in Orthopedics
Online Access:http://dx.doi.org/10.1155/2016/5247102
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author Abolfazl Rahimizadeh
Housain F. Soufiani
Saghayegh Rahimizadeh
author_facet Abolfazl Rahimizadeh
Housain F. Soufiani
Saghayegh Rahimizadeh
author_sort Abolfazl Rahimizadeh
collection DOAJ
description The dropped head syndrome (DHS) is a disabling condition caused by severe weakness of the neck extensor muscles causing progressive reducible kyphosis of the cervical spine and the inability to hold the head up. Weakness can occur in isolation or in association with a generalized neuromuscular disorder. Isolated cases are owed to the late onset of noninflammatory myopathy designated as INEM, where persistent chin to chest deformity may gradually cause or aggravate preexisting degenerative changes of the cervical spine and ultimately result in myelopathy. In review of the literature, we could find only 5 cases, with no unique guidelines to address the management of these two concomitant pathologies. Herein, a 69-year-old man who had developed cervical myelopathy 2 years after being affected by isolated dropped head syndrome is presented. Chin to chest deformity and cervical myelopathy were managed through three-level anterior cervical discectomy and fusion (ACDF) combined with decompressive cervical laminectomy and stabilization with C2 to C7 pedicle screw-rod construct. At 4-month follow-up, despite recovery in patient’s neurological status, flexion deformity reappeared with recurrence of dropped head due to C7 pedicle screws pull-out. However, this was successfully managed with extension of the construct to the upper thoracic levels.
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spelling doaj-art-4101f157574e42228a1955d3adbe61b52025-02-03T05:44:07ZengWileyCase Reports in Orthopedics2090-67492090-67572016-01-01201610.1155/2016/52471025247102Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the LiteratureAbolfazl Rahimizadeh0Housain F. Soufiani1Saghayegh Rahimizadeh2Department of Spinal Surgery, Pars Advanced and Minimally Invasive Manners Research Center (PAMIM), Affiliated to Iran University of Medical Sciences, Pars Hospital, Tehran, IranDepartment of Spinal Surgery, Pars Advanced and Minimally Invasive Manners Research Center (PAMIM), Affiliated to Iran University of Medical Sciences, Pars Hospital, Tehran, IranAtlantic University, School of Medicine, P.O. Box 456, Island Park, NY 11558, USAThe dropped head syndrome (DHS) is a disabling condition caused by severe weakness of the neck extensor muscles causing progressive reducible kyphosis of the cervical spine and the inability to hold the head up. Weakness can occur in isolation or in association with a generalized neuromuscular disorder. Isolated cases are owed to the late onset of noninflammatory myopathy designated as INEM, where persistent chin to chest deformity may gradually cause or aggravate preexisting degenerative changes of the cervical spine and ultimately result in myelopathy. In review of the literature, we could find only 5 cases, with no unique guidelines to address the management of these two concomitant pathologies. Herein, a 69-year-old man who had developed cervical myelopathy 2 years after being affected by isolated dropped head syndrome is presented. Chin to chest deformity and cervical myelopathy were managed through three-level anterior cervical discectomy and fusion (ACDF) combined with decompressive cervical laminectomy and stabilization with C2 to C7 pedicle screw-rod construct. At 4-month follow-up, despite recovery in patient’s neurological status, flexion deformity reappeared with recurrence of dropped head due to C7 pedicle screws pull-out. However, this was successfully managed with extension of the construct to the upper thoracic levels.http://dx.doi.org/10.1155/2016/5247102
spellingShingle Abolfazl Rahimizadeh
Housain F. Soufiani
Saghayegh Rahimizadeh
Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the Literature
Case Reports in Orthopedics
title Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the Literature
title_full Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the Literature
title_fullStr Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the Literature
title_full_unstemmed Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the Literature
title_short Cervical Spondylotic Myelopathy Secondary to Dropped Head Syndrome: Report of a Case and Review of the Literature
title_sort cervical spondylotic myelopathy secondary to dropped head syndrome report of a case and review of the literature
url http://dx.doi.org/10.1155/2016/5247102
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