A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium

Noncompaction of the ventricular myocardium is a rare cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings are prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular cavity. The clinical manife...

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Main Authors: Julien Bordes, Bertrand Jop, Sandrine Imbert, Sami Hraiech, Frédéric Collard, François Kerbaul
Format: Article
Language:English
Published: Wiley 2009-01-01
Series:Case Reports in Medicine
Online Access:http://dx.doi.org/10.1155/2009/725879
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author Julien Bordes
Bertrand Jop
Sandrine Imbert
Sami Hraiech
Frédéric Collard
François Kerbaul
author_facet Julien Bordes
Bertrand Jop
Sandrine Imbert
Sami Hraiech
Frédéric Collard
François Kerbaul
author_sort Julien Bordes
collection DOAJ
description Noncompaction of the ventricular myocardium is a rare cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings are prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular cavity. The clinical manifestations include heart failure (HF) signs, ventricular arrhythmias, and cardioembolic events. We describe an illustrative case of noncompaction of the ventricular myocardium associated with bicuspid aortic valve, a 42-year-old male presenting a refractory acute heart failure successfully treated by emergency heart transplantation.
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id doaj-art-3fb320a07f914f4a8625d8aa1efa336f
institution Kabale University
issn 1687-9627
1687-9635
language English
publishDate 2009-01-01
publisher Wiley
record_format Article
series Case Reports in Medicine
spelling doaj-art-3fb320a07f914f4a8625d8aa1efa336f2025-02-03T01:07:04ZengWileyCase Reports in Medicine1687-96271687-96352009-01-01200910.1155/2009/725879725879A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular MyocardiumJulien Bordes0Bertrand Jop1Sandrine Imbert2Sami Hraiech3Frédéric Collard4François Kerbaul5Department of Intensive Care, Sainte Anne Hospital, 83800 Toulon, FranceDepartment of Cardiac Surgery, La Timone Hospital, 13000 Marseille, FranceDepartment of Cardiac Surgery, La Timone Hospital, 13000 Marseille, FranceDepartment of Anesthesia and Intensive Care Unit, La Timone Hospital, 13000 Marseille, FranceDepartment of Cardiac Surgery, La Timone Hospital, 13000 Marseille, FranceDepartment of Anesthesia and Intensive Care Unit, La Timone Hospital, 13000 Marseille, FranceNoncompaction of the ventricular myocardium is a rare cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings are prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular cavity. The clinical manifestations include heart failure (HF) signs, ventricular arrhythmias, and cardioembolic events. We describe an illustrative case of noncompaction of the ventricular myocardium associated with bicuspid aortic valve, a 42-year-old male presenting a refractory acute heart failure successfully treated by emergency heart transplantation.http://dx.doi.org/10.1155/2009/725879
spellingShingle Julien Bordes
Bertrand Jop
Sandrine Imbert
Sami Hraiech
Frédéric Collard
François Kerbaul
A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
Case Reports in Medicine
title A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_full A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_fullStr A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_full_unstemmed A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_short A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_sort rare cause of heart failure treated by heart transplantation noncompaction of the ventricular myocardium
url http://dx.doi.org/10.1155/2009/725879
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