Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia
Aggressive systemic mastocytosis (ASM) is characterized by mast cell accumulation in systemic organs. Though ASM may be associated with other hematological disorders, the association with pure red cell aplasia (PRCA) is rare and has not been reported. Pure red cell aplasia (PRCA) is a syndrome, char...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Hematology |
| Online Access: | http://dx.doi.org/10.1155/2018/6928571 |
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| _version_ | 1832545359644065792 |
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| author | Dhauna Karam Sean Swiatkowski Mamata Ravipati Bharat Agrawal |
| author_facet | Dhauna Karam Sean Swiatkowski Mamata Ravipati Bharat Agrawal |
| author_sort | Dhauna Karam |
| collection | DOAJ |
| description | Aggressive systemic mastocytosis (ASM) is characterized by mast cell accumulation in systemic organs. Though ASM may be associated with other hematological disorders, the association with pure red cell aplasia (PRCA) is rare and has not been reported. Pure red cell aplasia (PRCA) is a syndrome, characterized by normochromic normocytic anemia, reticulocytopenia, and severe erythroid hypoplasia. The myeloid and megakaryocytic cell lines usually remain normal. Here, we report an unusual case of ASM, presenting in association with PRCA and the management challenges. |
| format | Article |
| id | doaj-art-3f777680783e4075bb583782aae0c18c |
| institution | Kabale University |
| issn | 2090-6560 2090-6579 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Hematology |
| spelling | doaj-art-3f777680783e4075bb583782aae0c18c2025-02-03T07:25:58ZengWileyCase Reports in Hematology2090-65602090-65792018-01-01201810.1155/2018/69285716928571Aggressive Systemic Mastocytosis in Association with Pure Red Cell AplasiaDhauna Karam0Sean Swiatkowski1Mamata Ravipati2Bharat Agrawal3Rosalind Franklin University, 3333 Green Bay Road, North Chicago, IL 60064, USARosalind Franklin University, 3333 Green Bay Road, North Chicago, IL 60064, USARosalind Franklin University, 3333 Green Bay Road, North Chicago, IL 60064, USARosalind Franklin University, 3333 Green Bay Road, North Chicago, IL 60064, USAAggressive systemic mastocytosis (ASM) is characterized by mast cell accumulation in systemic organs. Though ASM may be associated with other hematological disorders, the association with pure red cell aplasia (PRCA) is rare and has not been reported. Pure red cell aplasia (PRCA) is a syndrome, characterized by normochromic normocytic anemia, reticulocytopenia, and severe erythroid hypoplasia. The myeloid and megakaryocytic cell lines usually remain normal. Here, we report an unusual case of ASM, presenting in association with PRCA and the management challenges.http://dx.doi.org/10.1155/2018/6928571 |
| spellingShingle | Dhauna Karam Sean Swiatkowski Mamata Ravipati Bharat Agrawal Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia Case Reports in Hematology |
| title | Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia |
| title_full | Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia |
| title_fullStr | Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia |
| title_full_unstemmed | Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia |
| title_short | Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia |
| title_sort | aggressive systemic mastocytosis in association with pure red cell aplasia |
| url | http://dx.doi.org/10.1155/2018/6928571 |
| work_keys_str_mv | AT dhaunakaram aggressivesystemicmastocytosisinassociationwithpureredcellaplasia AT seanswiatkowski aggressivesystemicmastocytosisinassociationwithpureredcellaplasia AT mamataravipati aggressivesystemicmastocytosisinassociationwithpureredcellaplasia AT bharatagrawal aggressivesystemicmastocytosisinassociationwithpureredcellaplasia |