Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction Obstruction

Aim. Ureteropelvic junction obstruction (UPJO) is rarely associated with a duplex collecting system. We review this unusual anomaly in terms of presentation, diagnostic evaluation, and surgical management. Method. We retrospectively reviewed the medical records of patients diagnosed with a duplex sy...

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Main Authors: Cemile Başdaş, Süleyman Çelebi, Seyithan Özaydın, Birgül Karaaslan, Elmas Reyhan Alim, Ünal Güvenç, Serdar Sander
Format: Article
Language:English
Published: Wiley 2016-01-01
Series:Advances in Urology
Online Access:http://dx.doi.org/10.1155/2016/7960794
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author Cemile Başdaş
Süleyman Çelebi
Seyithan Özaydın
Birgül Karaaslan
Elmas Reyhan Alim
Ünal Güvenç
Serdar Sander
author_facet Cemile Başdaş
Süleyman Çelebi
Seyithan Özaydın
Birgül Karaaslan
Elmas Reyhan Alim
Ünal Güvenç
Serdar Sander
author_sort Cemile Başdaş
collection DOAJ
description Aim. Ureteropelvic junction obstruction (UPJO) is rarely associated with a duplex collecting system. We review this unusual anomaly in terms of presentation, diagnostic evaluation, and surgical management. Method. We retrospectively reviewed the medical records of patients diagnosed with a duplex system with UPJO. Result. Sixteen patients (6 girls, 10 boys) with 18 moieties were treated surgically and four patients were treated conservatively. The median age at surgery was two years (range, 2 months to 7 years). The lower pole and upper moiety were affected in 12 and two kidneys, respectively, and both were affected in two patients. The anomaly was right-sided in 12 moieties and left-sided in six. The duplication was incomplete in seven patients and complete in nine. The mean renal pelvis diameter at the time of surgery was 25.6 (range 11–48 mm) mm by USG. The mean renal function of the involved moiety was 28.3% before surgery. Management included pyelopyelostomy or ureteropyelostomy in six moieties, dismembered pyeloplasty in eight moieties, heminephrectomy in four cases, and simultaneous upper heminephrectomy and lower pole ureteropyelostomy in one patient. Conclusion. There is no standard approach for these patients and treatment should be individualized according to physical presentation, detailed anatomy, and severity of obstruction.
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spelling doaj-art-37b614b18ad842a8ac5ccc47516df3e32025-02-03T01:01:45ZengWileyAdvances in Urology1687-63691687-63772016-01-01201610.1155/2016/79607947960794Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction ObstructionCemile Başdaş0Süleyman Çelebi1Seyithan Özaydın2Birgül Karaaslan3Elmas Reyhan Alim4Ünal Güvenç5Serdar Sander6Department of Pediatric Urology, Kanuni Sultan Suleyman Education and Research Hospital, Istanbul, TurkeyDepartment of Pediatric Urology, Istanbul University, Medicine Faculty, Istanbul, TurkeyDepartment of Pediatric Surgery, Kanuni Sultan Suleyman Education and Research Hospital, Istanbul, TurkeyDepartment of Pediatric Surgery, Kanuni Sultan Suleyman Education and Research Hospital, Istanbul, TurkeyDepartment of Pediatric Surgery, Kanuni Sultan Suleyman Education and Research Hospital, Istanbul, TurkeyDepartment of Pediatric Surgery, Kanuni Sultan Suleyman Education and Research Hospital, Istanbul, TurkeyDepartment of Pediatric Urology, Kanuni Sultan Suleyman Education and Research Hospital, Istanbul, TurkeyAim. Ureteropelvic junction obstruction (UPJO) is rarely associated with a duplex collecting system. We review this unusual anomaly in terms of presentation, diagnostic evaluation, and surgical management. Method. We retrospectively reviewed the medical records of patients diagnosed with a duplex system with UPJO. Result. Sixteen patients (6 girls, 10 boys) with 18 moieties were treated surgically and four patients were treated conservatively. The median age at surgery was two years (range, 2 months to 7 years). The lower pole and upper moiety were affected in 12 and two kidneys, respectively, and both were affected in two patients. The anomaly was right-sided in 12 moieties and left-sided in six. The duplication was incomplete in seven patients and complete in nine. The mean renal pelvis diameter at the time of surgery was 25.6 (range 11–48 mm) mm by USG. The mean renal function of the involved moiety was 28.3% before surgery. Management included pyelopyelostomy or ureteropyelostomy in six moieties, dismembered pyeloplasty in eight moieties, heminephrectomy in four cases, and simultaneous upper heminephrectomy and lower pole ureteropyelostomy in one patient. Conclusion. There is no standard approach for these patients and treatment should be individualized according to physical presentation, detailed anatomy, and severity of obstruction.http://dx.doi.org/10.1155/2016/7960794
spellingShingle Cemile Başdaş
Süleyman Çelebi
Seyithan Özaydın
Birgül Karaaslan
Elmas Reyhan Alim
Ünal Güvenç
Serdar Sander
Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction Obstruction
Advances in Urology
title Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction Obstruction
title_full Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction Obstruction
title_fullStr Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction Obstruction
title_full_unstemmed Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction Obstruction
title_short Unusual Presentation of Duplex Kidneys: Ureteropelvic Junction Obstruction
title_sort unusual presentation of duplex kidneys ureteropelvic junction obstruction
url http://dx.doi.org/10.1155/2016/7960794
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