Cardiac transplantation as resolution for Uhl's anomaly: A case report

Cardiac transplantation as resolution for Uhl's anomaly: A case report

Uhl's anomaly is an extremely rare congenital cardiac defect characterized by the absence of myocardium in the right ventricle. It has a poor prognosis, typically fatal during the perinatal period, with very few patients reaching adulthood. We present the case of a 28-year-old woman with heart...

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Bibliographic Details
Main Authors: Juan J. Bacigalupe, MD, Natalia Vensentini, MD, Santiago Torroba, MD, Javier A. Mariani, MD, Sandra Defelitto, MD, Norberto Blanco, MD, Fabian Paetz, MD, Julieta Ximena Saenz, MD, Marcelo Nahin, MD, Maximiliano de Abreu, MD
Format: Article
Language:English
Published: Elsevier 2025-08-01
Series:JHLT Open
Subjects:
Uhl anomaly
cardiac transplantation
heart failure
Congenital heart disease
Ventricular arrhythmia
Online Access:http://www.sciencedirect.com/science/article/pii/S2950133425001387
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Summary:Uhl's anomaly is an extremely rare congenital cardiac defect characterized by the absence of myocardium in the right ventricle. It has a poor prognosis, typically fatal during the perinatal period, with very few patients reaching adulthood. We present the case of a 28-year-old woman with heart failure and ventricular arrhythmia associated with Uhl's anomaly, who required cardiac transplantation, with favorable postoperative outcomes. Uhl's anomaly represents an exceedingly rare cause of cardiac transplantation in adults.
ISSN:2950-1334

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