Significance of autoantibodies in diagnostics of systemic vasculitis

Systemic vasculitis is a heterogeneous group of disorders characterized by inflammation and necrosis in the vessel wall. Patients usually present a quite broad spectrum of manifestations which vary in terms of vessels’ size affected, organs involvement, and the extent of inflammatory process as well...

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Main Authors: Katarzyna Fischer, Marek Brzosko
Format: Article
Language:English
Published: Open Exploration Publishing Inc. 2023-07-01
Series:Exploration of Musculoskeletal Diseases
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Online Access:https://www.explorationpub.com/uploads/Article/A100712/100712.pdf
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author Katarzyna Fischer
Marek Brzosko
author_facet Katarzyna Fischer
Marek Brzosko
author_sort Katarzyna Fischer
collection DOAJ
description Systemic vasculitis is a heterogeneous group of disorders characterized by inflammation and necrosis in the vessel wall. Patients usually present a quite broad spectrum of manifestations which vary in terms of vessels’ size affected, organs involvement, and the extent of inflammatory process as well as an immunological diversity, including autoantibodies profile. Though, the diagnosis is based on clinical features, tissue biopsy, imaging investigations, and serologic tests. The main autoantibodies, important not only in the diagnosis but also in monitoring and prognosis of systemic vasculitides, are anti-neutrophil cytoplasmic antibodies (ANCA), anti-glomerular basement membrane antibodies (anti-GBM), anti-complement component C1q antibodies (anti-C1q), and cryoglobulins. Although other autoantibodies have been analyzed, their clinical utility still needs further investigation. The current work aimed to review the clinical associations of main autoantibodies in systemic vasculitis.
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issn 2836-6468
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publishDate 2023-07-01
publisher Open Exploration Publishing Inc.
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series Exploration of Musculoskeletal Diseases
spelling doaj-art-361efc8d4e734a41b4b2aa80b8ea09ad2025-08-20T02:44:56ZengOpen Exploration Publishing Inc.Exploration of Musculoskeletal Diseases2836-64682023-07-0114778310.37349/emd.2023.00012Significance of autoantibodies in diagnostics of systemic vasculitisKatarzyna Fischer0https://orcid.org/0000-0003-4792-2099Marek Brzosko1https://orcid.org/0000-0001-7681-4367Independent Laboratory for Rheumatologic Diagnostics, Pomeranian Medical University in Szczecin, 71-252 Szczecin, PolandDepartment of Rheumatology, Internal Medicine, Geriatrics and Clinical Immunology, Pomeranian Medical University in Szczecin, 71-252 Szczecin, PolandSystemic vasculitis is a heterogeneous group of disorders characterized by inflammation and necrosis in the vessel wall. Patients usually present a quite broad spectrum of manifestations which vary in terms of vessels’ size affected, organs involvement, and the extent of inflammatory process as well as an immunological diversity, including autoantibodies profile. Though, the diagnosis is based on clinical features, tissue biopsy, imaging investigations, and serologic tests. The main autoantibodies, important not only in the diagnosis but also in monitoring and prognosis of systemic vasculitides, are anti-neutrophil cytoplasmic antibodies (ANCA), anti-glomerular basement membrane antibodies (anti-GBM), anti-complement component C1q antibodies (anti-C1q), and cryoglobulins. Although other autoantibodies have been analyzed, their clinical utility still needs further investigation. The current work aimed to review the clinical associations of main autoantibodies in systemic vasculitis.https://www.explorationpub.com/uploads/Article/A100712/100712.pdfsystemic vasculitisanti-neutrophil cytoplasmic antibodiesanti-glomerular basement membrane antibodiesanti-complement component c1q antibodiescryoglobulins
spellingShingle Katarzyna Fischer
Marek Brzosko
Significance of autoantibodies in diagnostics of systemic vasculitis
Exploration of Musculoskeletal Diseases
systemic vasculitis
anti-neutrophil cytoplasmic antibodies
anti-glomerular basement membrane antibodies
anti-complement component c1q antibodies
cryoglobulins
title Significance of autoantibodies in diagnostics of systemic vasculitis
title_full Significance of autoantibodies in diagnostics of systemic vasculitis
title_fullStr Significance of autoantibodies in diagnostics of systemic vasculitis
title_full_unstemmed Significance of autoantibodies in diagnostics of systemic vasculitis
title_short Significance of autoantibodies in diagnostics of systemic vasculitis
title_sort significance of autoantibodies in diagnostics of systemic vasculitis
topic systemic vasculitis
anti-neutrophil cytoplasmic antibodies
anti-glomerular basement membrane antibodies
anti-complement component c1q antibodies
cryoglobulins
url https://www.explorationpub.com/uploads/Article/A100712/100712.pdf
work_keys_str_mv AT katarzynafischer significanceofautoantibodiesindiagnosticsofsystemicvasculitis
AT marekbrzosko significanceofautoantibodiesindiagnosticsofsystemicvasculitis